Elelyso
Injeksiyon ya Taliglucerase alfa ikoreshwa mu kuvura igihe kirekire indwara ya Gaucher yo mu bwoko bwa mbere. Iyi ndwara iterwa no kubura enzyme runaka mu mubiri yitwa glucocerebrosidase. Iyi enzyme ikenewe kugira ngo umubiri ukoreshe amavuta neza, kandi amavuta azajya yiyongera mu bice bimwe na bimwe by'umubiri iyo iyi enzyme itabonetse. Taliglucerase alfa isimbura iyi enzyme ibura kugira ngo ifashe umubiri gutunganya amavuta. Uyu muti ugomba gutangwa gusa na muganga cyangwa munsi y'ubuyobozi bwa muganga. Iyi miti iboneka mu buryo bukurikira bwo kuyikoresha:
Mu gufata icyemezo cyo gukoresha imiti, ibyago byo gufata iyo miti bigomba guhabwa agaciro ugereranyije n'akamaro izagira. Iki ni icyemezo uzatanga hamwe na muganga wawe. Kuri iyi miti, ibi bikurikira bigomba kwitabwaho: Bwira muganga wawe niba warigeze ugira uburwayi butasanzwe cyangwa imitego y'ubuziranenge kuri iyi miti cyangwa izindi miti. Nanone, umenyeshe umuhanga mu by'ubuzima ufite andi moko y'ibintu bitera imitego, nka biribwa, amabara, ibintu birinda kwangirika, cyangwa inyamaswa. Ku bicuruzwa bitagomba kwandikwa, soma witonze ibikubiye kuri etiketi cyangwa ubusobanuro bw'ibintu birimo. Ubushakashatsi bukwiye ntabwo bwakozwe ku isano iri hagati y'imyaka n'ingaruka zo guterwa inshinge ya taliglucerase alfa ku bana bari munsi y'imyaka 4. Ubuziranenge n'ingaruka nziza ntibyarangiye. Nubwo ubushakashatsi bukwiye ku isano iri hagati y'imyaka n'ingaruka zo guterwa inshinge ya taliglucerase alfa ntabwo bwakozwe mu itsinda ry'abakuze, nta kibazo cyihariye cy'abakuze cyanditswe kugeza ubu. Nta bushakashatsi buhagije ku bagore bwo kumenya ibyago by'uruhinja mu gihe ukoresha iyi miti mu gihe cyo konsa. Pima inyungu zishoboka ugereranyije n'ibyago bishoboka mbere yo gufata iyi miti mu gihe cyo konsa. Nubwo imiti imwe n'imwe igomba gukoreshwa hamwe na gato, mu bindi bihe imiti ibiri itandukanye ishobora gukoreshwa hamwe nubwo ishobora kubaho. Muri uru rubanza, muganga wawe ashobora kwifuza guhindura umwanya, cyangwa izindi ngamba zishobora kuba ngombwa. Menyesha umuhanga mu by'ubuzima ufite indi miti yanditswe cyangwa idasabwa (over-the-counter [OTC]). Imiti imwe n'imwe ntigomba gukoreshwa mu gihe cyo kurya cyangwa hafi yacyo cyangwa kurya imirire imwe n'imwe kuko ishobora kubaho. Gukoresha inzoga cyangwa itabi hamwe na imiti imwe nabyo bishobora gutera ishobora kubaho. Gabagana n'umuhanga mu by'ubuzima wawe gukoresha imiti yawe hamwe n'ibiribwa, inzoga cyangwa itabi.
Umuforomokazi cyangwa undi wubatse ubumenyi mu buvuzi azaguha wowe cyangwa umwana wawe imiti muri hopitali cyangwa ku ivuriro. Iyi miti iterwa mu mubiri binyuze mu cyuma gito cyinjizwa mu mubiri (IV catheter) gishyirwa muri imwe mu mitsi yawe. Imiti igomba guterwa buhoro buhoro, ku buryo icyuma gito cyinjizwa mu mubiri (IV) kizakenera kuguma aho kiri iminota 60 kugeza kuri 120. Ibi bisanzwe bikorwa buri cyumweru kimwe. Muganga wawe ashobora kuguha izindi miti mbere y'ubuvuzi (urugero, imiti y'uburwayi bwo kugira allergie, imiti ya steroide) kugira ngo afashe kwirinda ingaruka zidateganijwe.