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Pemphigoid Bullous

Pfupiso

Vanhu vane bullous pemphigoid vanogona kuumba maronda akawanda. Kana maronda acho apwanya, anorasikirwa nemaronda anowanzoporesa pasina kutsvaga.

Bullous pemphigoid (BUL-us PEM-fih-goid) chirwere chisingawanzoitika che ganda rinokonzera maronda makuru akapfava. Kazhinji anowanikwa paganda riri pedyo nemakona, sekunge mapapiro epamusoro nemapapiro. Dzimwe nguva, vanhu vanowana utachiona panzvimbo pemaronda. Nzvimbo dzakabatwa dzinogona kurwadza uye kazhinji dzinonyanya kukwenya. Maronda kana maronda anogonawo kuumbwa mumuromo, asi izvi hazviwanzoitika.

Bullous pemphigoid inoitika kana sisitimu yekudzivirira muviri ikasvika pane imwe rukoko rweganda. Chikonzero chekuita kwesisitimu yekudzivirira muviri iyi hachizivikanwi zvakanaka. Kune vamwe vanhu, mamiriro acho anoitwa nemamwe mishonga.

Bullous pemphigoid kazhinji inoenda yoga mumavhiki mashoma, asi inogona kutora kusvika kumakore mashanu kuti iende zvachose. Kurapa kazhinji kunobatsira kuporesa maronda uye kudzivirira mamwe matsva kuti aungane.

Mamiriro acho akajairika muvanhu vane makore anopfuura makumi matanhatu.

Zviratidzo

'Zviratidzo zvebullous pemphigoid zvinogona kusanganisira: Kutsamwa, kunogona kutanga mavhiki kana mwedzi usati wabuda mabhlister. Mabhlister makuru asingaputsike nyore nyore, kazhinji anowanikwa pakati pemakwinya eganda. Paganda revara rebrown neBlack mabhlister anogona kunge ari rima pink, brown kana dema. Paganda jena anogona kunge ari yero, pink kana tsvuku. Kurwadziwa. Zitsvuku. Mabhlister maduku kana maronda mumuromo kana mamwe mucous membranes. Iri chiratidzo cherudzi rwakasiyana-siyana chirwere chinonzi mucous membrane pemphigoid. Ona nyanzvi yehutano kana uine: Mabhlister asinganzwisisiki. Mabhlister pamaziso ako. Hutachiona. Mabhlister ari kuvhura uye ari kubuda mvura.'

Nguva yekunoona chiremba

Ona mushandi wehutano kana uine:

  • Maronda asinganzwisisiki.
  • Maronda pamaziso ako.
  • Hutachiona.
  • Maronda ari kuvhura uye ari kubuda mvura.
Zvinokonzera

Zviratidzo zvebullous pemphigoid zvinoitika kana immune system ikurwisa rukoko rwenyama mumucheka. Chikonzero chedambudziko iri hachizivikanwi zvakanaka. Muzviitiko zvimwe, mamiriro acho anoitwa ne:

  • Mishonga. Mishonga yakati wandei inozivikanwa kuti inowedzera njodzi ye bullous pemphigoid. Mienzaniso ndeye diuretics senge furosemide; maantibayotiki senge amoxicillin, penicillin ne ciprofloxacin; NSAIDs senge aspirin ne ibuprofen; mishonga yehutachiona senge sitagliptin (Januvia); uye mishonga yekurapa kenza senge nivolumab ne pembrolizumab.
  • Kurapa kwechiedza nekurapa kwemwaranzi. Kurapa kwechiedza che ultraviolet kurapa mamiriro ezve ganda kunogona kuunza bullous pemphigoid. Uyewo, mwaranzi yekurapa kenza inogona kukonzera mamiriro acho.
  • Zvirwere zvepanyama. Psoriasis, lichen planus, dementia, chirwere cheParkinson, stroke uye multiple sclerosis ndezvimwe zvezvirwere zvinogona kusanganiswa ne bullous pemphigoid.

Mamiriro acho haasi hutachiona uye haasi kuzara.

Zvinhu zvinokonzera njodzi

Bullous pemphigoid inowanzoitika kune vanhu vakuru vemakore anopfuura makumi matanhatu, uye njodzi yacho inowedzera nekuwedzera kwezera. Zvirwere izvi zvinogona kuuraya vanhu vakwegura vane zvimwe zvirwere panguva imwe chete.

Matambudziko

Matambudziko anogona kuitika ebullous pemphigoid anosanganisira:

  • Hutachiona.
  • Kushanduka kwevara reganda mushure mekurapa ganda rakabatwa. Kushanduka uku kwevara reganda kunonzi post-inflammatory hyperpigmentation kana ganda racho rakaita rima uye post-inflammatory hypopigmentation kana ganda racho rapera ruvara. Vanhu vane ganda rebrown kana dema vane mukana mukuru wekushanduka kwenguva refu kwevara reganda.
  • Zvinokonzerwa nemishonga inoshandiswa kurapa bullous pemphigoid.
Kuongorora

Munachiremba wenyu achataura nemi nezve zviratidzo zvenyu uye nhoroondo yenyu yezvokurapa, uye aite bvunzo yemuviri. Mungada bvunzo kuti muone kana mune chirwere che bullous pemphigoid. Idzi dzinosanganisira bvunzo yeropa, biopsy yeganda kana zvose zviri zviviri. Biopsy ndiyo nzira yekubvisa sampuli yetsvina kuti iongororwe murabhoritari.

Munachiremba wenyu angakutumirai kune nyanzvi yezvirwere zve ganda. Chiremba we rudzi urwu anonzi dermatologist.

Kurapa

Kurapa bullous pemphigoid kunangisira kupora ganda, kuderedza manyoka nekurwadziwa, uye kudzivirira mavhinga matsva. Munachiremba wenyu angangokupa mushonga mumwe kana musanganiswa wemishonga iyi:

  • Corticosteroids. Kurapa kukuru kwe bullous pemphigoid ndemushonga we corticosteroid unoshandiswa munzvimbo yakabatwa. Kazhinji cream ine steroid ine simba senge clobetasol propionate inoshandiswa. Kushandisa kwenguva refu kwemushonga wemhando iyi kunouya nenjodzi yekunyatsikana kwepande uye kuvhunduka nyore. Munachiremba wenyu angakurudzirawo mushonga we steroid unonwiwa. Steroids dzinonwiwa dzinouya nenjodzi yemhedzisiro inokuvadza, senge mapfupa asina simba, chirwere cheshuga, maronda emudumbu nezvinetso zvemaziso.
  • Antibiotics. Mishonga inonwiwa dapsone nedoxycycline inobatsira kudzora mavhinga.
  • Mishonga inorwisa immune system. Mishonga mimwe inogona kumisa immune system yako kuti isarwi nemasero ane hutano. Mienzaniso ndeye azathioprine (Azasan, Imuran), rituximab (Rituxan), mycophenolate (CellCept) uye methotrexate (Trexall). Mishonga iyi inewo njodzi yemhedzisiro inokuvadza, kusanganisira hutachiona. Vanhu vanotora mishonga iyi vanoda kuongororwa zvakanyanya uye, dzimwe nguva, bvunzo yeropa inoratidzwa kuti vatariswe mhedzisiro.

Corticosteroids. Kurapa kukuru kwe bullous pemphigoid ndemushonga we corticosteroid unoshandiswa munzvimbo yakabatwa. Kazhinji cream ine steroid ine simba senge clobetasol propionate inoshandiswa. Kushandisa kwenguva refu kwemushonga wemhando iyi kunouya nenjodzi yekunyatsikana kwepande uye kuvhunduka nyore. Munachiremba wenyu angakurudzirawo mushonga we steroid unonwiwa. Steroids dzinonwiwa dzinouya nenjodzi yemhedzisiro inokuvadza, senge mapfupa asina simba, chirwere cheshuga, maronda emudumbu nezvinetso zvemaziso.

Zvichienderana nekuti unopindura sei kumishonga yekutanga yaunotora, munachiremba wenyu angakurudzira chimwe chinhu kunze kwe steroids.

Bullous pemphigoid kazhinji inopera nekufamba kwenguva. Maronda anogona kutora mavhiki kuti apone, uye zvakajairika kuti mamwe matsva abude.

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