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Dermatomyositis

Pfupiso

Dermatomyositis (dur-muh-toe-my-uh-SY-tis) chirwere chinhu chisingawanzoitika chinoratidzwa nekushaya simba retsandanyama uye ganda rinoratidza zviratidzo zvakasiyana.

Zvirwere izvi zvinogona kukanganisa vakuru nevana. Muvakuru, dermatomyositis kazhinji inoitika pakati pemakore makumi mana nemana kusvika makumi matanhatu. Muvana, kazhinji inoonekwa pakati pemakore mashanu nemakore gumi nemashanu. Dermatomyositis inokanganisa vakadzi vakawanda kupfuura varume.

Hapana mushonga we dermatomyositis, asi nguva dzekuvandudzwa kwezviratidzo dzinogona kuitika. Kurapa kunogona kubatsira kubvisa ganda rinoratidza zviratidzo uye kukubatsira kudzoreredza simba retsandanyama nebasa rayo.

Zviratidzo

Zviratidzo nezvimwe zvirwere zve dermatomyositis zvinogona kuoneka kamwe kamwe kana kukura zvishoma nezvishoma panguva. Zviratidzo nezvirwere zvakajairika zvinosanganisira:

  • Kuchinja kwe ganda. Kutsvuka kwepurple kana dema kunoumbwa, kazhinji panzvimbo dzakaita se chiso nemaziso uye pamaoko, magaro, mazamu, chipfuva nemutsipa. Kutsvuka uku, kunogona kukwenya uye kurwadza, kazhinji ndicho chiratidzo chekutanga che dermatomyositis.
  • Kushaya simba retsandanyama. Kushaya simba kwemagaro kunobatanidza misumbu iri pedyo nemuviri, senge iri mumabvi, mapapiro, mapendekete, maoko epamusoro nemutsipa. Kushaya simba uku kunokanganisa divi rekuruboshwe nerudyi rwemiviri, uye kunowanzo kuwedzera zvishoma nezvishoma.
Nguva yekunoona chiremba

Tsvaka rubatsiro rwekurapa kana iwe ukakura urombo hwemhasuru kana kuti uropi husina tsananguro.

Zvinokonzera

Chikonzero chedermatomyositis hachizivikanwi, asi chirwere ichi chine zvakawanda zvakafanana nezvirwere zve autoimmune, umo masisitimu ako ekuzvidzivirira anorwisa nyama dzomuviri wako nehurema. Zvinhu zvemagariro ne zvepasi pano zvinogona zvakare kutamba basa. Zvinhu zvepasi pano zvinogona kusanganisira hutachiona hwehutachiona, zuva, mishonga yakati wandei nekutsikira.

Zvinhu zvinokonzera njodzi

Kunyangwe chero munhu anogona kurwara dermatomyositis, inowanzowanikwa muvanhu vakapihwa pabonde rechikadzi pakuumbwa. Zvinhu zvemagwenya nezvakatikomberedza zvinosanganisira hutachiona hwemuviri uye zuva zvinogonawo kuwedzera njodzi yekurwara dermatomyositis.

Matambudziko

Zvinetso zvinogona kuitika zve dermatomyositis zvinosanganisira:

  • Kuomesa kwakaoma kumeza. Kana mhasuru dzemudumbu rako dzakakuvadzwa, unogona kuva nematambudziko ekuruma, izvo zvinogona kukonzera kurasikirwa uremu uye kushomeka kwezvinovaka muviri.
  • Aspiration pneumonia. Kuomesa kumeza kunogona zvakare kukonzera kuti ufemuke chikafu kana zvinwiwa, kusanganisira mate, mumapapu ako.
  • Matambudziko ekufemba. Kana mamiriro acho akakanganisa mhasuru dzako dzepachipfuva, ungava nematambudziko ekufemba, senge kushomeka kwemhepo.
  • Calcium deposits. Idzi dzinogona kuitika mumhasuru dzako, ganda uye tishu dzinobatanidza sezvo chirwere ichi chichienderera mberi. Aya madipoziti akajairika muvana vane dermatomyositis uye anobudirira pakutanga kwechirwere.
Kuongorora

Kana chiremba wenyu achifungidzira kuti mune dermatomyositis, anogona kukurudzira mimwe miedzo inotevera:

  • Kuongororwa kweropa. Kuongororwa kweropa kuchazivisa chiremba wenyu kana mune ma enzymes emuviri akawanda anogona kuratidza kukuvara kwemhasuru. Kuongororwa kweropa kunogona zvakare kuona autoantibodies dzakabatana nezviratidzo zvakasiyana zve dermatomyositis, izvo zvinogona kubatsira pakusarudza mushonga wakanakisa nekurapa.
  • X-ray yepafupa. Iyi bvunzo iri nyore inogona kutarisa zviratidzo zvemarudzi ekukuvara kwemapapu dzimwe nguva kunoitika ne dermatomyositis.
  • Electromyography. Chiremba ane kudzidziswa kwakakosha anopinda electrode yemunwe wakatetepa kuburikidza neganda mumasuru anofanirwa kuongororwa. Simba remagetsi rinoyerwa sezvaunorara kana kusimbisa tsandanyama, uye kuchinja muenzaniso wesimba remagetsi kunogona kusimbisa chirwere chetsandanyama. Chiremba anogona kuona kuti ndeapi masuru akabatwa.
  • MRI. Scanner inogadzira mifananidzo ye cross-sectional yemhasuru dzako kubva kune data yakagadzirwa ne magnetic field ine simba uye ma radio waves. Kusiyana ne biopsy yemhasuru, MRI inogona kuongorora kuzvimba munzvimbo huru yemhasuru.
  • Biopsy yeganda kana mhasuru. Chikamu chidiki cheganda kana mhasuru chinobviswa kuti chiongororwe murabhoritari. Sampuli yeganda inogona kubatsira kusimbisa chirwere che dermatomyositis. Biopsy yemhasuru inogona kuratidza kuzvimba mumasuru ako kana matambudziko mamwe, akadai sekukuvara kana hutachiona. Kana biopsy yeganda ikasimbisa chirwere chacho, biopsy yemhasuru ingasave yakakosha.
Kurapa

Hakuna mushonga wekurapa dermatomyositis, asi kurapwa kunogona kuvandudza ganda rako nesimba remhasuru nemisebenzi yacho.

Mishonga inoshandiswa kurapa dermatomyositis inosanganisira:

Zvichienderana nekuoma kwezviratidzo zvako, chiremba wako angakurudzira:

  • Corticosteroids. Mishonga yakadai se prednisone (Rayos) inogona kudzora zviratidzo zve dermatomyositis nekukurumidza. Asi kushandiswa kwenguva refu kunogona kuva nemigumisiro yakakomba. Saka chiremba wako, mushure mekunyora mushonga wakakura kuti udzivise zviratidzo zvako, angadzikisa zvishoma nezvishoma mushonga sezvo zviratidzo zvako zvichivandudza.

  • Mishonga inodzivirira corticosteroid. Kana yakashandiswa ne corticosteroid, mishonga iyi inogona kudzikisa mushonga nemhedzisiro ye corticosteroid. Mishonga miviri inonyanya kushandiswa ye dermatomyositis ndiyo azathioprine (Azasan, Imuran) ne methotrexate (Trexall). Mycophenolate mofetil (Cellcept) imimwe mishonga inoshandiswa kurapa dermatomyositis, kunyanya kana mapapu akabatwa.

  • Rituximab (Rituxan). Inonyanya kushandiswa kurapa rheumatoid arthritis, rituximab sarudzo kana kurapwa kwekutanga kukundikana kudzora zviratidzo zvako.

  • Mishonga inorwisa malaria. Kune ganda rinoramba riripo, chiremba wako anganyora mushonga unorwisa malaria, sekunge hydroxychloroquine (Plaquenil).

  • Sunscreens. Kuchengetedza ganda rako kubva pakufuridzirwa nezuva nekushandisa sunscreen nekupfeka nguo dzinodzivirira nemagirazi zvakakosha pakugadzirisa ganda re dermatomyositis.

  • Kurapa kwemuviri. Munyanzvi wekurapa kwemuviri anogona kukuratidza maekisesaizi anokubatsira kuchengetedza nekuvandudza simba rako nekugadzikana uye kukupa mazano pamusoro pemazinga ekufamba akakodzera.

  • Kurapa kutaura. Kana mhasuru dzako dzekumera dzakabatwa, kurapa kutaura kunogona kukubatsira kudzidza nzira yekudzikamisa shanduko idzodzo.

  • Kuongororwa kwezvokudya. Gare gare mu dermatomyositis, kukwesha nekumera zvinogona kuva zvakaoma. Munyanzvi wezvokudya anogona kukudzidzisa nzira yekugadzirira zvokudya zviri nyore kudya.

  • Intravenous immunoglobulin (IVIg). IVIg chigadzirwa cheruoko rwakacheneswa rine maantibody ane hutano kubva kuzviuru zvevadonhedzi veropa. Aya maantibody anogona kudzivirira maantibody anokuvadza anorwisa mhasuru neganda mu dermatomyositis. Inopiwa se infusion kuburikidza ne tsinga, kurapwa kwe IVIg kunodhura uye kungada kudzokororwa nguva dzose kuti migumisiro irambe ichifamba.

  • Kuopereta. Kuopereta kungave sarudzo yekubvisa calcium deposits inorwadza uye kudzivirira kuzviratidza kwezvirwere zve ganda.

Kuzvitarisira

Padermatomyositis, nzvimbo dzakabatwa nemaronda ako dzinoita manyoro zvikuru kuzuva. Pfukidza zvipfeko zvinodzivirira kana sunscreen ine dziviriro yakakwirira kana uchienda kunze.

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