Chii Chinonzi Double Outlet Right Ventricle? Zviratidzo, Zvinokonzera, & Kurapa

Double outlet right ventricle (DORV) chirwere chisingawanzoitika chekuberekwa kwechirwere chemwoyo umo ropa rose rinobuda mumoyo rinobatanidzwa nekamuri yekurudyi yemoyo pane rimwe chete rakabatanidzwa nekamuri imwe neimwe yemoyo. Izvi zvinoreva kuti moyo wemwana wako unopomba ropa nenzira isiriyo, izvo zvinogona kukanganisa kuti ropa rakazara oksijeni rinofamba sei mumuviri wavo.

Iyi mamiriro anoitika panguva yekuzvitakura kwemwana wako apo moyo wemwana wako uchiri kuumbwa. Kunyange zvazvo zvinonzwa zvakanyanya, vana vazhinji vane DORV vanogona kurarama hupenyu hunogara, hunoshanda nekuchengetedzwa kwakakodzera kwemishonga nekurapa.

Chii Chinonzi Double Outlet Right Ventricle?

Mumoyo unogara zvakanaka, aorta inobatanidzwa nekamuri yekuruboshwe yemoyo uye pulmonary artery inobatanidzwa nekamuri yekurudyi yemoyo. NeDORV, ropa rose rinobuda mumoyo rinobva mukamuri yekurudyi yemoyo.

Funga nezvemoyo wako seune makamuri maviri makuru ekupomba. Rutivi rwerudyi runotumira ropa kumapfupa kuti awane oksijeni, nepo rutivi rweruboshwe ruchitumira ropa rakazara oksijeni kune dzimwe nhengo dzemuviri wako. Kana ropa rose rinobuda mumoyo richibva mukamuri yekurudyi yemoyo, nzira iyi yekufamba kwakajairwa inokanganiswa.

Iyi mamiriro anoita kuti ropa rakazara oksijeni risvike zvakanaka mumuviri wemwana wako nemuuropi. Kukomba kwacho kunotsamira pane mamwe marwere emwoyo anowanzoitika pamwe chete neDORV, akadai semaholes ari pakati pemakamuri emoyo.

Ndeapi Marudzi eDouble Outlet Right Ventricle?

DORV ine zvimiro zvakasiyana-siyana, uye vanachiremba vanoigovera zvichienderana nekuti gomba rinonzi ventricular septal defect (VSD) riri kupi. Iri gomba rinobatsira ropa kufamba muvana vane DORV.

Marudzi makuru anosanganisira subaortic DORV, kwaari gomba riri pasi pe aorta, uye subpulmonary DORV, kwaari riri pasi pe pulmonary artery. Kunewo doubly committed DORV, kwaari gomba rinobatanidzwa nemapaipi maviri, uye non-committed DORV, kwaari gomba harizobatanidzwi zvakanaka nemapaipi ese.

Marudzi ese anoita kuti ropa rifambe nenzira dzakasiyana uye anoda nzira dzakasiyana dzekurapa. Chiremba wenyu wevana achazviongorora kuti mwana wenyu ane rudzii rweDORV kuburikidza nekuongororwa kwakakwana kwemuviri.

Ndeapi Zviratidzo zveDouble Outlet Right Ventricle?

Zviratidzo zveDORV zvinowanzooneka mumavhiki mashomanana ekutanga kana mwedzi yekutanga yehupenyu, kunyange zvazvo zvinogona kusiyana zvakanyanya zvichienderana nekuti mamiriro acho anokanganisa sei kufamba kweropa. Vamwe vana vanoratidza zviratidzo pakarepo, nepo vamwe vasingave nezviratidzo zvakajeka kusvika gare gare.

Zviratidzo zvakajairwa zvaunogona kuona zvinosanganisira:

• Ruvimbiso rwezvipfeko kana ruvara rwegoridhe, kunyanya kumativi emoyo, misumari, kana rurimi (rinonzi cyanosis)
• Kunetseka kudya kana kunyanya kuneta panguva yekudya
• Kufema kukurumidza kana kuoma, kunyange uri kuzorora
• Kukura kwakaderera kunyange zvazvo uchidyisa zvakakwana
• Kuita shungu, kunyanya panguva yekudya kana mabasa asingakoshi
• Kushatirwa kana kuchema kunoratidzika kusingawanzoitika kumwana wako

Vamwe vana vanogonawo kuona zviratidzo zvakakomba zvakadai sekuzara kwezvirwere zvemapapu kana zviitiko zvinowanzoitika apo vanova neblue uye vanonetseka. Aya maitiro, anonzi hypercyanotic spells, anoda rubatsiro rwekukurumidza rwemishonga.

Muitiko usina kujairika, vana vane marudzi akati wandei eDORV vanogona kutanga kuratidzika vakachena uye vane utano asi gare gare vanoratidza zviratidzo zvekutadza kwemoyo sezvo vakakura. Izvi zvinogona kusanganisira kuzvimba mumitsipa yavo, mudumbu, kana kumativi emaziso avo.

Chii Chinokonzera Double Outlet Right Ventricle?

DORV inoitika mukati memavhiki masere ekutanga ekuzvitakura apo moyo wemwana wako uchiri kuumbwa. Chikonzero chaicho hachizivikanwi zvizere, asi zvinoita sekunge zvinoitika kana ropa rose rinobuda mumoyo risina kutenderera zvakanaka sezvo moyo uchiri kuumbwa.

Kazhinji kazhinji zvinoitika pasina chikonzero chaicho kana chiito chevabereki chakakonzera. Izvi zvinoreva kuti hapana chawakaita kana kusaita panguva yekuzvitakura kwakakonzera mamiriro aya.

Nekudaro, zvinhu zvimwe zvinogona kuwedzera njodzi zvishoma. Izvi zvinosanganisira kuva nedenda panguva yekuzvitakura, kutora mishonga yakati, kana kuva nemhuri ine nhoroondo yemarwere emwoyo ekuberekwa. Zvimwe zvirwere zvemajini zvakadai seDiGeorge syndrome kana Down syndrome zvinobatanidzwawo nehuwandu hwakakwira hweDORV.

Muitiko usina kujairika, kuiswa kune mamwe maronda panguva yekuzvitakura kwemwana kana zvinhu zvakatipoteredza zvinogona kutamba basa. Asi zvakare, kazhinji kazhinji zvinoitika pasina chikonzero chinogona kuzivikanwa, izvo zvinogona kunzwa zvakashata asi zvakajairwa zvachose.

Ndeapi Zvinhu Zvinowedzera Njodzi yeDouble Outlet Right Ventricle?

Kunyangwe kazhinji kazhinji DORV ichiomuka pasina chikonzero, zvinhu zvimwe zvinogona kuita kuti ive nyore kuitika. Kunzwisisa izvi zvinhu zvinowedzera njodzi zvinogona kubatsira, kunyange zvazvo zvakakosha kurangarira kuti kuva nezvinhu zvinowedzera njodzi hazvirevi kuti DORV ichaitika zvirokwazvo.

Zvinhu zveamai zvinogona kuwedzera njodzi zvinosanganisira:

• Kuva nedenda usati kana panguva yekuzvitakura
• Kutora mishonga yakati yakadai semishonga yekudzivirira kuita zvirwere zvepfungwa panguva yekuzvitakura
• Kuva nemakore anopfuura makumi matatu nemashanu panguva yekuzvitakura
• Kuva wakambonzwa uine pamuviri wakakanganiswa nemarwere emwoyo ekuberekwa

Zvinhu zvemajini zvinogonawo kutamba basa mune dzimwe nguva. Vana vane zvirwere zvechromosomal zvakadai seDown syndrome, DiGeorge syndrome, kana 22q11.2 deletion syndrome vane huwandu hwakakwira hweDORV.

Kuonekwa kwezvinhu zvakatipoteredza panguva yekuzvitakura kwemwana, zvakadai semaronda kana kemikari, zvinogona kuita basa mune dzimwe nguva. Nekudaro, vazhinji vevana vane DORV vanoberekwa kuvabereki vasina zvinhu zvinowedzera njodzi zvinogona kuzivikanwa.

Rini Unofanira Kuona Chiremba weDouble Outlet Right Ventricle?

Unofanira kubata nachiremba wenyu wevana pakarepo kana mwana wako akaratidza zviratidzo zvematambudziko emwoyo, kunyanya ruvara rweblue rweganda, miromo, kana misumari. Iri ruvara rweblue, rinonzi cyanosis, rinoratidza kuti mwana wako haana kuwana oksijeni yakakwana.

Zvimwe zviratidzo zvinokurumidza zvinosanganisira kunetseka kukuru kwekufema, kusakwanisa kudya zvakanaka, kana zviitiko apo mwana wako anova neblue uye anonetseka pakarepo. Aya mamiriro anoda rubatsiro rwekukurumidza rwemishonga.

Unofanirawo kubata nachiremba wenyu kana mwana wako achiratidzika kuneta zvakanyanya panguva yekudya, haasi kukura zvakanaka, kana ane zvirwere zvemapapu zvinowanzoitika. Kunyange zvazvo aya maratidzo anogona kuva nezvimwe zvikonzero, anoda kuongororwa kana achiitika pamwe chete.

Kana mwana wako akatoongororwa aine DORV, kuenda kunochirongwa zvakajairwa nemuongorori wemoyo wevana kunokosha. Bata navo pakati pekuenda kana ukaona chero shanduko mune zviratidzo zvemwana wako kana zviratidzo zvitsva zvinotyisa.

Ndeapi Matambudziko Anogona Kuitika eDouble Outlet Right Ventricle?

Pasina kurapwa, DORV inogona kukonzera matambudziko akakomba anokanganisa hutano hwemwana wako nekuvandudzika. Mashoko akanaka ndeawo ekuti nekuchengetedzwa kwakakodzera kwemishonga, matambudziko mazhinji aya anogona kudzivirirwa kana kutarisirwa zvakanaka.

Matambudziko akajairika anosanganisira:

• Kuora kwemoyo, kwaari moyo usingakwanisi kupomba ropa zvakanaka zvakakwana
• Kukura kwakaderera nekuda kwemoyo unoshanda zvakanyanya kupfuura zvakanaka
• Kuwanza kwezvirwere zvemapapu kubva kune nzira dzakachinja dzekufamba kweropa
• Kuderera kwepressure ropa mumapapu (pulmonary hypertension)
• Kufamba kwemoyo kwasingawanzoitika kunogona kuda kuongororwa kana kurapwa
• Njodzi yekurohwa nekuda kwekuwanda kweropa, kunyange zvazvo izvi zvisingawanzoitika

Vamwe vana vanogona kuwana zvinonzi Eisenmenger syndrome, mamiriro asingawanzoitika asi akakomba kwaari kuwanda kwepressure ropa mumapapu kunokonzera shanduko dzisingaperi. Izvi zvinowanzoitika mune zviitiko zvisina kurapwa kana izvo zvakawanikwa zvakare gare gare.

Matambudziko chaiwo anomuka kumwana wako anotsamira zvakanyanya pane rudzi rweDORV rwavane uye chero marwere emwoyo anobatanidzwa. Chiremba wenyu wemoyo achazviongorora aya matambudziko uye achaita kuti adzivirirwe nekupa kurapwa kwakakodzera panguva yakakodzera.

Double Outlet Right Ventricle Inooongororwa Sei?

DORV inowanzoonekwa pakutanga kana chiremba akanzwa ruzha rwemoyo pakuongororwa kwakajairwa kana akaona zviratidzo zvakadai seruvara rweblue rweganda. Kuongororwa kunozobva kwaongororwa nekuongororwa kwakawanda kwemoyo.

Echocardiogram kazhinji ndiyo bvunzo yekutanga yakakwana inoitirwa. Iri ultrasound yemoyo inoratidza chimiro nebasa panguva chaiyo, ichibvumira vanachiremba kuona kuti ropa rinofamba sei mumakamuri emoyo wemwana wako nemapaipi.

Dzimwe nguva bvunzo dzakawanda dzinoda kuwana mufananidzo wakakwana. Izvi zvinogona kusanganisira cardiac catheterization, kwaari chubhu duku inoiswa muropa kuti iyere pressure ropa uye mazinga eoksijeni zvakananga, kana kuongororwa kwakakwana kwakadai se cardiac MRI.

Muitiko usina kujairika, DORV inogona kuonekwa usati waberekwa panguva yekuzvitakura kwakajairwa. Kana zvikafungidzirwa usati waberekwa, iwe uchaenda kune nyanzvi yezvokurapa zveamai nevana uye chiremba wemoyo wevana kuti uongororwe zvakakwana uye urongedze kuberekwa.

Kurapa kweDouble Outlet Right Ventricle Ndeapi?

Kurapa kweDORV kazhinji kunosanganisira kuvhiya kuti utungamirire kufamba kweropa uye kubatsira moyo kushanda zvakanaka. Nzira chaiyo yekuvhiya inotsamira pane zvakakosha zvemwana wako uye marwere emwoyo anobatanidzwa.

Vana vazhinji vanoda kuvhiya kwakawanda pane kuvhiya kumwe chete. Kuvhiya kwekutanga kazhinji kunoitika muhucheche kuti kuvandudze zviratidzo zvepakarepo nekufamba kweropa. Izvi zvinogona kusanganisira kuita kubatanidzwa pakati pemapaipi eropa kana kuisa shunts yenguva pfupi.

Chinangwa chekupedzisira kazhinji ndechekuwana zvinonzi vanachiremba "two-ventricle repair," kwaari makamuri ese emoyo anogona kushanda zvakanaka. Izvi zvinogona kusanganisira nzira dzakadai se arterial switch operations kana kugadziriswa kwakaoma kuti utungamirire kufamba kweropa zvakanaka.

Muitiko usina kujairika kwaari two-ventricle repair isingakwanisi, vanachirongwa vanogona kukurudzira nzira ye single-ventricle. Izvi zvinosanganisira kuvhiya kwakawanda kwetatu kunobvumira kamuri imwe yemoyo kuita basa rose rekupomba kwemoyo.

Pakati pekuvhiya, mwana wako anogona kuda mishonga yekubatsira moyo wavo kushanda zvakanaka kana kudzivirira matambudziko. Izvi zvinogona kusanganisira diuretics kuderedza kuwanda kwemvura kana mishonga yekutsigira basa remwoyo.

Maitiro Ekutarisira Mwana Pamba Panguva Yekurapwa kweDouble Outlet Right Ventricle?

Kutarisira mwana ane DORV pamba kunosanganisira zvinhu zvakakosha zvekumuchengetedza aine hutano uye akasununguka pakati pekuenda kuchipatara. Timu yako yekuchengetedza hutano ichapa mirairo yakakosha yakagadzirirwa zvinodiwa nemwana wako.

Kudya kazhinji kunoda kutarisirwa kwakakosha sezvo vana vane DORV vanogona kuneta nyore. Ungada kupa kudya kudiki, kazhinji kazhinji kana kushandisa mabhodhoro chaiwo anokurumidza kudya. Vamwe vana vanobatsirwa nemafomula ane macalorie akawanda kuti vabatsirwe kukura zvakanaka.

Tarisa zviratidzo zvinoda rubatsiro rwekukurumidza rwemishonga, zvakadai sekuwedzera kweblue coloring, kunetseka kukuru kwekufema, kana shanduko huru mumaitiro ekudya kana mabasa. Chengetera nhamba dzekukurumidza kubata nadzo dziri nyore kuwana.

Mwana wako anogona kuda kudzivirirwa kubva kune mamwe maronda, kunyanya maronda emuviri. Izvi zvinogona kureva kuderedza kuiswa kune vanhu vazhinji panguva yechando nechirwere chemafuru kana kuve nechokwadi chekuti nhengo dzese dzemhuri dzakazara nejekiseni.

Mishonga yakajairwa ndeyokosha kana mwana wako achitora mishonga yemoyo. Usambofa wakasiya dose pasina kubvunza chiremba wemoyo, uye chengeta zvekutsiva zviripo kana zvikaitika zvisingatarisirwi kana kufamba.

Unofanira Kugadzirira Sei Kune Chiremba Wako?

Kugadzirira kuenda kuchipatara kunogona kubatsira kuve nechokwadi chekuti unowana zvakawanda kubva kune imwe neimwe yekushanya uye usakanganwa mibvunzo yakakosha kana zvinhu zvinokunetsa. Chengeta rondedzero yezviratidzo kana shanduko dzawakaona pakati pekuenda kuchipatara.

Uya nerondedzero yakakwana yemishonga yose inotorwa nemwana wako, kusanganisira zviyero chaizvo uye nguva. Uyaiwo nechero rekodhi yekukura, maitiro ekudya, kana mazinga ebasa kana wakanga uchizvitarisa pamba.

Nyora mibvunzo usati watanga sezvo kuenda kuchipatara kunogona kunzwa kwakanyanya. Mibvunzo yakajairwa inogona kusanganisira kubvunza nezvemiganho yebasa, zviratidzo zvekuona, kana kuti kuvhiya kunotevera kunogona kudikanwa.

Kana zvichibvira, uya nemumwe munhu mukuru newe kuenda kuchipatara. Kuva nemumwe munhu kunogona kukubatsira kurangarira ruzivo rwakataurwa uye kupa rutsigiro rwemanzwiro panguva yekukurukura inogona kunetsa.

Usambofa wakashamisika kukumbira kuti ujekeswe kana mazwi emishonga kana marapirwo achiratidzika kunge asinganzwisisike. Timu yako yekuchengetedza hutano inoda kuti unzwisise mamiriro emwana wako uye unzwe wakavimbika mukuchengetedzwa kwavo.

Double Outlet Right Ventricle Inogona Kudzivirirwa Sei?

Nekudaro, hapana nzira inozivikanwa yekudzivirira DORV sezvo inoitika pasina chikonzero panguva yekuzvitakura kwemwana mune kazhinji kazhinji. Izvi zvinogona kunzwa zvakashata, asi zvakakosha kunzwisisa kuti hapana chawakaita chakakonzera mamiriro aya.

Nekudaro, mamwe matanho ekutanga panguva yekuzvitakura anogona kutsigira kukura kwemoyo wemwana. Izvi zvinosanganisira kutora mavhitamini ekutanga nefolic acid, kutarisira shuga zvakanaka kana uine, uye kudzivisa doro nekusvuta fodya.

Kana uri kuronga kuzvitakura kwenguva yemberi uye une nhoroondo yemhuri yemarwere emwoyo ekuberekwa, mazano emajini anogona kubatsira. Munyori anogona kukurukura njodzi dzako dzakakosha uye nzira dzekuongorora dziripo.

Kuongororwa kwakajairwa kwekuzvitakura kunobvumira kuonekwa pakutanga kana marwere emwoyo akaitika. Kunyange zvazvo izvi zvisingadziviriri DORV, zvinobvumira kugadzirira kwakanaka uye kuronga kuchengetedzwa kwemwana wako mushure mekuberekwa.

Chii Chinonyanya Kukosha Nezve Double Outlet Right Ventricle?

DORV chirwere chakakomba asi chinorapika chekuberekwa kwechirwere chemwoyo chinoita kuti ropa rifambe sei mumoyo wemwana wako. Kunyange zvazvo kuongororwa kunogona kunzwa kwakanyanya, vana vazhinji vane DORV vanorarama hupenyu huzere, hunoshanda nekuchengetedzwa kwakakodzera kwemishonga.

Kiyi yemigumisiro yakanaka ndeyekushanda pedyo nechikwata chakakwanisa chevana vechikoro chevana vanogona kukutungamirira mune zvisarudzo zvekurapa uye nguva. Mamiriro emwana mumwe nemumwe akasiyana, uye marapirwo anogadzirirwa zvinodiwa nemwana mumwe nemumwe.

Rangarira kuti kunzwa kutya, kusanzwisisika, kana kunetseka kwakajairwa kana uchitarisana nekuongororwa kwakadai seDORV. Usambofa wakashamisika kubvunza mibvunzo, kutsvaga mamwe mazano kana zvichidikanwa, uye kubatanidza nemagungano ekutsigira kana mhuri dzakafamba nzira iyi.

Nezviitiko zvakakosha mukuvhiya kwemoyo wevana nekutarisirwa kwenguva refu, tarisiro yevana vane DORV inoramba ichivandudzika. Tarisa pakutora zvinhu nhanho nhanho uye kufarira kukunda duku munzira.

Mibvunzo InowanzoBvunzwa Nezve Double Outlet Right Ventricle

Q1. Mwana wangu achakwanisa here kuita mitambo nemabasa emuviri?

Vana vazhinji vane DORV yakarapwa zvakanaka vanogona kuita mabasa emuviri, kunyange zvazvo miganho yakakosha inotsamira pane basa ravo remwoyo uye nhoroondo yekuvhiya. Chiremba wenyu wemoyo wevana achazviongorora basa remwoyo remwana wako uye achapa mirairo yebasa yakagadzirirwa iye.

Vamwe vana vangave vasina miganho zvachose, nepo vamwe vangada kudzivisa mitambo ine simba kwazvo. Chinangwa ndechekuwana chiyero chakakodzera chinobvumira mwana wako kuramba achishanda uye aine hutano nepo achichengetedza moyo wavo.

Q2. Mwana wangu achada kuvhiya kangani?

Huwandu hwekuvhiya hunosiyana zvakanyanya zvichienderana nerudzi rwemwana wako rweDORV uye marwere emwoyo anobatanidzwa. Vamwe vana vanoda kuvhiya kumwe kana maviri chete, nepo vamwe vangada kuvhiya kutatu kana kupfuura kwemakore mazhinji.

Timu yako yekuvhiya ichagadzira chirongwa chakakwana pakutanga, kunyange zvazvo izvi zvingada kugadziriswa sezvo mwana wako achikura. Vachaedza kugara vachideredza huwandu hwekuvhiya nepo vachiwana basa rakanaka remwoyo.

Q3. Tarisiro yenguva refu yevana vane DORV ndeyei?

Tarisiro yenguva refu yakavandudzika zvikuru mumakore achangopfuura nekuvandudzika mukuvhiya kwemoyo wevana. Vana vazhinji vane DORV vanokura kuti vararame hupenyu hunowanzoitika, vachienda kuchikoro, vachitsvaga mabasa, uye kunyange kuva nemhuri dzavo.

Nekudaro, vazhinji vachada kuongororwa kwenguva refu kwemoyo kuti vatarisire basa ravo remwoyo uye vatarisire chero matambudziko gare gare. Tarisiro chaiyo inotsamira pane zvinhu zvakadai serudzi rweDORV, marwere anobatanidzwa, uye kuti kugadziriswa kwakaita sei basa kwenguva refu.

Q4. Vakadzi vane DORV vanogona here kuva nevana zvakanaka?

Vakadzi vazhinji vane DORV yakagadziriswa zvakanaka vanogona kuva nekuzvitakura kwakachengeteka, kunyange zvazvo izvi zvinoda kuronga zvakanaka nekutarisirwa kwakakosha. Sarudzo inotsamira pane zvinhu zvakadai sebasa remwoyo ikozvino, chero marwere asara, uye hutano hwese.

Vakadzi vanofunga nezvekuzvitakura vanofanira kushanda nechikwata chavo chekare chevanachiremba nemunyori wezvokurapa zveamai nevana kuti vaongorore njodzi uye vagadzire chirongwa chakakwana chekuchengetedza. Nekutarisa kwakakodzera, vakadzi vazhinji vane DORV vane kuzvitakura kwakabudirira nevana vane hutano.

Q5. Mwana wangu achada here kutora mishonga yemoyo kwenguva refu?

Havasi vana vose vane DORV vanoda mishonga yenguva refu, asi vamwe vangada kurapwa kwenguva refu zvichienderana nebasa ravo remwoyo mushure mekuvhiya. Mishonga yakajairwa inogona kusanganisira blood thinners, mishonga yekufamba kwemoyo, kana mishonga yekutsigira basa remwoyo.

Zvinodikanwa zvemwana wako zve mishonga zvichaongororwa zvakare sezvo vakakura uye basa ravo remwoyo richiongororwa. Vamwe vana vanogona kurega kutora mishonga yakati, nepo vamwe vangada kuenderera nayo kwenguva refu kuti vave nehutano hwakanaka hwemoyo.