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Fivha Yemediterranean Yemhuri

Pfupiso

Fivha yeMediterranean yemhuri (FMF) chirwere chinokonzerwa nemafuro ekuzvara chinokonzera fivha dzinopera uye kuzvimba kunorwadza kwemudumbu, chipfuva nemapfundo. Fivha yeMediterranean yemhuri (FMF) chirwere chinogara chiripo chinowanzoitika kune vanhu vekuMediterranean — kusanganisira avo vechiJudha, vechiArabhu, vechiArmenia, vechiTurkey, vekuNorth Africa, vechiGiriki kana vechiItari. Asi inogona kukanganisa vanhu chero rudzi. Fivha yeFMF inowanzoonekwa panguva yehudiki. Kunyangwe pasina mushonga wechirwere ichi, unogona kudzikamisa kana kutoita kuti zviratidzo zveFMF zvisavepo nekutevera chirongwa chako chekurapa.

Zviratidzo

Zviratidzo nezvimwe zvirwere zvefamilial Mediterranean fever kazhinji zvinovamba muhudiki. Zvinoitika mumapoka anonzi kurwisa anogara kwemazuva 1-3. Kurwisa kweArthritis kunogona kugara kwemavhiki kana mwedzi.

Zviratidzo nezvimwe zvirwere zveFmf zvinosiyana, asi zvinogona kusanganisira:

*Fivha *Kurwadziwa kwemudumbu *Kurwadziwa kwepfupa, kunogona kuita kuti zviome kufema zvakadzika *Joints dzine kurwadziwa, dzakazvimba, kazhinji mumabvi, makwati nemabvi *Tsvuku pamatete ako, kunyanya pasi pemabvi ako *Marwadzo emhasuru *Scrotum yakazvimba, ine kurwadziwa

Kurwisa kazhinji kunozvigadzirisa mushure memazuva mashoma. Pakati pekurwisa, iwe uchazonzwa wakadzokera kuhutano hwako hwenguva dzose. Nguva dzisina zviratidzo zvinogona kunge pfupi semamazuva mashoma kana kureba kwemakore mazhinji.

Pavanhu vamwe, chiratidzo chekutanga cheFMF ndeye amyloidosis. Pamwe chete neamyloidosis, puroteni amyloid A, isingawanzoonekwa mumuviri, inoungana mune zvikamu zvemuviri - kunyanya itsvo - ichikonzera kuzvimba uye kukanganisa basa rayo.

Nguva yekunoona chiremba

Ona chiremba wako kana iwe kana mwana wako akaita fivha kamwe kamwe ine kurwadziwa mudumbu, muchidya nemidziyo.

Zvinokonzera

Fivha yeMediterranean inobva kumhuri inokonzerwa nechinja chejini (mutation) chinopfuudzwa kubva kuvabereki kuenda kuvana. Kuchinja kwejeni kunokanganisa basa repuroteni yesimba remuviri rinonzi pyrin, zvichikonzera matambudziko mukudzora kuzvimba mumuviri.

Muvanhu vane FMF, kuchinja kunoitika mujini inonzi MEFV. Kuchinja kwakasiyana-siyana muMEFV kunobatanidzwa neFMF. Kuchinja kwakati kungaite kuti zviitike zvakanyanya, nepo zvimwe zvingaite kuti zviratidzo nezviratidzo zvive zvishoma.

Hazvina kujeka kuti chii chaizvo chinokonzera kurwisa, asi zvinogona kuitika nekushushikana kwepfungwa, kumwedzi, kuiswa mukutonhora, uye kushushikana kwemuviri sekurwara kana kukuvara.

Zvinhu zvinokonzera njodzi

Zvinhu zvinogona kuwedzera njodzi yekukuvara kwemhuri yeMediterranean zvinosanganisira:

  • Nhoroondo yemhuri yerudzi urwu. Kana uine nhoroondo yemhuri yeFMF, une njodzi yakakwira yerudzi urwu.
  • Madzitateguru eMediterranean. Kana mhuri yako ikakwanisa kutevera nhoroondo yayo kuenda kunzvimbo yeMediterranean, njodzi yako yerudzi urwu inogona kuwedzera. FMF inogona kukanganisa vanhu veboka ripi neripi, asi inogona kunge iri yakawanda muvanhu vechiJudha, veArabhu, veArmenia, veTurkey, veNorth Africa, veGreece kana veItaly.
Matambudziko

Zvinetso zvinogona kuitika kana chirwere cheMediterranean chemhuri chisingarapwi. Kutsvuka kunogona kukonzera zvinetso senge:

  • Amyloidosis. Panguva yekurwisa kweFMF, muviri wako unogona kugadzira puroteni inonzi amyloid A, isingawanzoonekwa mumuviri. Kuwanda kwepuroteni iyi kunokonzera kutsvuka, izvo zvinogona kukonzera kukuvara kwezvikamu zvemuviri.
  • Kukuvara kweitsvo. Amyloidosis inogona kukuvadza itsvo, ichikonzera nephrotic syndrome. Nephrotic syndrome inoitika kana masisitimu ekusefa etsvo (glomeruli) akakuvadzwa. Vanhu vane nephrotic syndrome vanogona kurasikirwa nehuwandu hwakawanda hwepuroteni mumukaka wavo. Nephrotic syndrome inogona kukonzera ropa kuvhara muitsvo (renal vein thrombosis) kana kutadza kweitsvo.
  • Kurwadziwa kwemashure. Arthritis inowanzoitika kune vanhu vane FMF. Zvikamu zvemuviri zvinowanzokanganiswa ndemakumbo, makwati nemabvi.
  • Kushaya simba rekubereka. Kutsvuka kusina kurapwa kunokonzerwa neFMF kunogona kukanganisa nhengo dzekubereka, zvichikonzera kushaya simba rekubereka.
  • Zvimwe zvinetso. Izvi zvinogona kusanganisira kutsvuka mumoyo, mapapu, spleen, uropi uye tsinga dzakadzika.
Kuongorora

Kuongororwa nekuedzwa kunoshandiswa pakuzivisa fivha yeMediterranean yemhuri kunosanganisira:

Kuongororwa kwemajini kweFMF kunogona kukurudzirwa kune hama dzako dzepedyo, dzakadai sevabereki, vanin'ina kana vana, kana kune dzimwe hama dzine njodzi. Kurudziro yemajini inogona kukubatsira kunzwisisa kuchinja kwemajini nemigumisiro yacho.

  • Kuongororwa kwemuviri. Mupi wehutano hwako anogona kukubvunza nezvezviratidzo zvako uye kuita kuongororwa kwemuviri kuti awane rumwe ruzivo.
  • Kuongororwa kwezvehutano hwemhuri yako. Nhoroondo yemhuri yeFamilial Mediterranean fever (FMF) inowedzera mukana wako wekuwana chirwere ichi nekuti kuchinja uku kwemajini kunopfuudzwa kubva kuvabereki kuenda kuvana vavo.
  • Kuongororwa kwerabhoritari. Panguva yekurwisa, bvunzo yeropa neyeweti inogona kuratidza mazinga akakwira emamwe mamakisi anoratidza mamiriro ekutsamwa mumuviri wako. Kuwanda kwema cell machena eropa, anorwisa hutachiona, chimwe chezviratidzo izvozvo. Puroteni iri muweti inogona kuratidza amyloidosis chimwewo.
  • Kuongororwa kwemajini. Kuongororwa kwemajini kunogona kuona kana jini rako reMEFV rine kuchinja kwejeni rine chekuita neFMF. Kuongororwa kwemajini hakufambire mberi zvakakwana kuti kuongorore kuchinja kwejeni kwese kunobatanidzwa neFMF, saka mukana wezvibvumikiso zvenhema uripo. Nechikonzero ichi, vanachiremba kazhinji havashandisi bvunzo dzemajini sedanho rekutanga rekuzivisa FMF.
Kurapa

Hapana mushonga wechirwere che familial Mediterranean fever. Zvisinei, kurapwa kunogona kubatsira kuderedza zviratidzo, kudzivirira kurwisa uye kudzivirira matambudziko anokonzerwa nekuzvimba.

Mishonga inoshandiswa kuderedza zviratidzo uye kudzivirira kurwisa kwe FMF inosanganisira:

Colchicine inoshanda pakudzivirira kurwisa kwevanhu vakawanda. Kuti uderedze kukomba kwezviratidzo panguva yekurwisa, mutariri wehutano wako anogona kukurudzira mvura inoiswa mutsinga nemishonga yekuderedza fivha nekuzvimba uye kudzora marwadzo.

Zvikamu zvemazuva ese nemupi wehutano hwako zvinokosha pakutarisa mishonga yako nehutano hwako.

  • Colchicine. Colchicine (Colcrys), inotorwa muchimiro chepiritsi, inoderedza kuzvimba mumuviri wako uye inobatsira kudzivirira kurwisa nekukura kwe amyloidosis. Shanda nachiremba wako kuti uone nzira yakanakisa yekupa mishonga kwauri. Vamwe vanhu vanotora dose imwe chete pazuva, nepo vamwe vachida zviduku, zvakawanda-kazhinji doses. Zvinokonzeresa zvakajairika zvinosanganisira kurwadziwa kwemudumbu, kusvotwa uye manyoka. Kurapwa kazhinji kwehupenyu hwese.
  • Mishonga yakasiyana yekudzivirira kuzvimba. Kune vanhu vane zviratidzo nezviratidzo zvisingadzorwi ne colchicine, mishonga inodzivirira puroteni inonzi interleukin-1, iyo inobatanidzwa mukuzvimba, inogona kunyorwa. Canakinumab (Ilaris) inobvumirwa neU.S. Food and Drug Administration (FDA) ye FMF. Kunyangwe isingabvumirwi neFood and Drug Administration (FDA) chaiyo ye FMF, mamwe ma options anosanganisira rilonacept (Arcalyst) uye anakinra (Kineret).

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