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Focal Segmental Glomerulosclerosis (Fsgs)

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Pfupiso

Focal segmental glomerulosclerosis (FSGS) inokonzerwa nemaronda anokura mu glomeruli. Glomeruli ndidzo nhengo duku dziri mumatombo dzinoyerera zvinhu zvisina basa kubva muropa kuti dzigadzire weewee. Glomerulus ine hutano inoratidzwa kuruboshwe. Kana maronda akakura mu glomerulus, basa reitsvo rinoipisisa (inoratidzwa kurudyi).

Focal segmental glomerulosclerosis (FSGS) chirwere chinoitika apo maronda anokura paglomeruli, zvikamu zvidiki zveitsvo zvinoyerera zvinhu zvisina basa kubva muropa. FSGS inogona kukonzerwa nezvinhu zvakasiyana-siyana.

FSGS chirwere chakakomba chinogona kukonzera kutadza kweitsvo, izvo zvinogona kurapwa chete nedialysis kana kupanwa kweitsvo. Nzira dzekurapa FSGS dzinoenderana nerudzi rwaunaro.

Marudzi eFSGS anosanganisira:

  • Primary FSGS. Vanhu vazhinji vanorwara neFSGS havazivi chikonzero chechirwere chavo. Izvi zvinonzi primary (idiopathic) FSGS.
  • Secondary FSGS. Zvinhu zvakawanda, zvakadai sehutachiona, chepfu yemishonga, zvirwere zvinosanganisira chirwere cheshuga kana chirwere che sickle cell, kuzara, uye kunyange mamwe marwere eitsvo zvinogona kukonzera secondary FSGS. Kudzora kana kurapa chikonzero chikuru kazhinji kunodzikisa kukuvara kweitsvo kuri kuenderera mberi uye kungaita kuti basa reitsvo rive nani nekufamba kwenguva.
  • Genetic FSGS. Iri rudzi rwakasiyana-siyana rweFSGS rwakakonzerwa nekushanduka kwemajini. Inonziwo familial FSGS. Inofungidzirwa kana nhengo dzakawanda dzemhuri dzicharatidza zviratidzo zveFSGS. Familial FSGS inogonawo kuitika kana vabereki vasina chirwere asi mumwe nemumwe wavo aine kopi yejini yakachinja inogona kupfuudzwa kuzvizvarwa zvinotevera.
  • FSGS isingazivikanwe. Muzviitiko zvimwe, chikonzero cheFSGS hachigone kuzivikanwa kunyangwe mushure mekuongororwa kwezviratidzo zvekiriniki nekuongororwa kwakawanda.
Zviratidzo

Zviratidzo zve focal segmental glomerulosclerosis (FSGS) zvinogona kusanganisira:

  • Kuruwisa, kunonzi edema, mumitsipa nemakumbo, kumativi emaziso nemumaviriro emuviri.
  • Kuwedzera uremu kubva pakukura kwemvura.
  • Mvura ine mhangura kubva pakukura kwe protein, inonzi proteinuria.
Nguva yekunoona chiremba

Kana uine chero zviratidzo zveFSGS, enda kuna chiremba.

Zvinokonzera

Focal segmental glomerulosclerosis (FSGS) inogona kukonzerwa nezvikonzero zvakasiyana-siyana, zvakadai sedhiyabhotesi, chirwere che sickle cell, zvimwe zvirwere zveitsvo uye kuzara kwemuviri. Kunetseka uye kukuvara kunokonzerwa nezvinodhaka zvisiri pamutemo, mishonga kana chepfu zvinogona zvakare kukonzera. Kushanduka kwemajini kunopfuudzwa kuburikidza nemhuri, kunonzi inherited gene changes, kunogona kukonzera rudzi rwakasiyana rweFSGS. Dzimwe nguva hapana chikonzero chinozivikanwa.

Zvinhu zvinokonzera njodzi

Zvinhu zvinogona kukwidziridza njodzi ye focal segmental glomerulosclerosis (FSGS) zvinosanganisira:

  • Zvirwere zvinogona kukuvadza itsvo. Zvirwere zvimwe nezvimwe zvinosimudzira njodzi yekuwana FSGS. Izvi zvinosanganisira chirwere cheshuga, lupus, kuzara kwemuviri nezvimwe zvirwere zveitsvo.
  • Utachiona hwakati. Utachiona hunowedzera njodzi yeFSGS hunosanganisira HIV nehepatitis C.
  • Kushanduka kwemajini. Majini akati akafambiswa kuburikidza nemhuri anogona kukwidziridza njodzi yeFSGS.
Matambudziko

Focal segmental glomerulosclerosis (FSGS) inogona kukonzera matambudziko mamwe ehutano, anozivikanwawo sekuoma, anosanganisira:

  • Kukundikana kweitsvo. Kukuvadzwa kweitsvo kunogona kuregererwa kunokonzera kuti itsvo dzirege kushanda. Mishonga chete yekukundikana kweitsvo ndeye dialysis kana kupanwa kweitsvo.
Kuongorora

Kana zvichiita kunge uri ne focal segmental glomerulosclerosis (FSGS), mushandi wako wehutano anotarisa nhoroondo yako yezvokurapa uye anorayira bvunzo dzemabhora kuti aone kuti itsvo dzako dziri kushanda zvakanaka sei. Kuongororwa kunogona kusanganisira:

  • Kuongororwa kwemukaka. Izvi zvinosanganisira kuunganidzwa kwemukaka kwemaawa makumi maviri nemana kunoyeresa huwandu hwemapuroteni nezvimwe zvinhu zviri mumukaka.
  • Kuongororwa kweropa. Kuongororwa kweropa kunonzi glomerular filtration rate kunoyeresa kuti itsvo dziri kubvisa marara mumuviri zvakanaka sei.
  • Kuonekwa kweitsvo. Aya maekisi anoshandiswa kuratidza chimiro nehukuru hweitsvo. Anogona kusanganisira ultrasound uye CT kana MRI scans. Zvidzidzo zveNuclear medicine zvinogona kushandiswawo.
  • Biopsy yeitsvo. Biopsy kazhinji inosanganisira kuisa tsono kuburikidza neganda kuti utarise sampuli diki kubva kuitsvo. Mhedzisiro ye biopsy inogona kusimbisa chirwere cheFSGS.
Kurapa

Kurapa kwe focal segmental glomerulosclerosis (FSGS) kunoenderana nerudzi uye chikonzero chacho. Zvichienderana nezviratidzo, mishonga yekurapa FSGS inogona kusanganisira:

  • Mishonga inoderedza mazinga echolesterol. Vanhu vane FSGS kazhinji vane cholesterol yakakwira.
  • Mishonga inoderedza kudzora kwemuviri. Kune FSGS huru, mishonga iyi inogona kumisa sisitimu yekudzivirira muviri pakukuvadza itsvo. Mishonga iyi inosanganisira corticosteroids. Inogona kuva nemigumisiro yakakomba, saka inoshandiswa nekuchenjerera.

FSGS chirwere chinogona kudzoka. Nekuti kukuvara kwe glomeruli kungave kwenguva refu, unofanirwa kutevera nechikwata chehutano hwako kuti uone kuti itsvo dzako dzinoshanda zvakanaka sei.

Kune vanhu vane kutadza kweitsvo, kurapwa kunosanganisira dialysis nekusimudzirwa kweitsvo.

Kuzvitarisira

Kushandura mararamiro anotevera kunogona kubatsira kuchengetedza itsvo dzakagwinya:

  • Usashandise mishonga inogona kukuvadza itsvo dzako. Izvi zvinosanganisira zvimwe zvinorwisa marwadzo senge zvinodzora kupisa kwemajoini (NSAIDs). NSAIDs aunogona kuwana usina chinyorwa chechiremba anosanganisira ibuprofen (Advil, Motrin IB, nezvimwewo) uye naproxen sodium (Aleve).
  • Usafume. Kana uchida rubatsiro pakusiya, taura nemumwe wechikwata cheutano hwako.
  • Ramba uine uremu hwakakodzera. Deredza uremu kana uri wakakura kupfuura zvakafanira.
  • Iva ane simba mazuva mazhinji. Kuva nesimba kwakanaka kune hutano hwako. Bvunza chikwata chako cheutano marudzi ekuita zvemuviri uye kuti ungaita sei zvemuviri.
Kugadzirira musangano wako

Unogona kutanga nokuona nyanzvi yako huru yekutarisira utano. Kana kuti ungatumirwa kunyanzvi yezvirwere zveitsvo, anonzi nephrologist.\n\nHeano mamwe mashoko anokubatsira kugadzirira musangano wako.\n\nPaunenge uchiita musangano, bvunza kana paine chimwe chinhu chaunofanira kuita usati wasangana nachiremba, sekusadya kana kunwa usati waita bvunzo dzakati. Izvi zvinonzi kuve nenzara.\n\nGadzira rondedzero ye:\n\n- Zviratidzo zvako, kusanganisira chero zvisingatarisirwi kuti zvine chekuita nechivikonzero chemusangano wako, uye nguva zvakatanga.\n- Mashoko akakosha emuviri wako, kusanganisira kushushikana kukuru, kuchinja kwoupenyu munguva pfupi yapfuura uye nhoroondo yemhuri yezveutano.\n- Mishonga yose, mavitamini kana zvimwe zvinowedzerwa zvaunotora, kusanganisira zviyero.\n- Mibvunzo yekubvunza timu yako yekutarisira utano.\n\nTora nhengo yemhuri kana shamwari pamwe chete, kana zvichibvira, kukubatsira kuyeuka ruzivo rwaunopiwa.\n\nKune focal segmental glomerulosclerosis (FSGS), mimwe mibvunzo yekubvunza nyanzvi yako yekutarisira utano inosanganisira:\n\n- Chii chinokonzera zviratidzo zvangu?\n- Ndeapi mamwe makondisheni anogona kukonzera zviratidzo zvangu?\n- Ndeapi bvunzo dzandinoda?\n- Zvirwere zvangu zvinogona kupera here kana kuti zvichagara kwenguva refu?\n- Ndeapi sarudzo dzangu dzekurapa?\n- Ndine mamwe mamiriro ezveutano. Ndingazvitarisira sei zviri nani pamwe chete?\n- Kune zvipingamupinyi zvandofanira kutevera?\n- Ndinofanira kuona nyanzvi here?\n- Kune mabhurocha kana mamwe mapepa andinogona kuwana here? Ndezvipi mawebsite aunofunga kuti angabatsira?"\n\nIva nechokwadi chekubvunza mibvunzo yose yaunayo.\n\nNyanzvi yako yekutarisira utano inogona kukubvunza mibvunzo, yakadai se:\n\n- Zviratidzo zvako zvinouya nekuenda here kana kuti une nguva dzose?\n- Zviratidzo zvako zvakakomba sei?\n- Chii, kana chiripo, chinoita kuti zviratidzo zvako zvive nani?\n- Chii, kana chiripo, chinoita kuti zviratidzo zvako zviwedzere?

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