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Hemophilia

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Pfupiso

Hemophilia chirwere chisingawanzoitika umo ropa risinganyanyi kuomarara sezvazvinoita nekuti harina maproteni akakwana anokonzera kuomarara kweropa (zvinhu zvinoita kuti ropa riomere). Kana uine hemophilia, ungabuda ropa kwenguva yakareba mushure mekukuvadzwa kupfuura kwaizova kana ropa rako rakaomarara zvakanaka.

Kutemwa duku kazhinji hakusi dambudziko rakakura. Kana uine chirwere chakakomba, chinonyanya kunetseka kubuda ropa mumuviri mako, kunyanya mumabvi, mumabvi nemumagaro. Kubuda ropa mukati kunogona kukuvadza nhengo dzako netsitisi uye kunotyisa upenyu.

Hemophilia kazhinji chirwere chinowanikwa kubva kumagwenya. Kurapa kunosanganisira kutsiva nguva dzose kwechinhu chinokonzera kuomarara kweropa icho chakadzikira. Mishonga mitsva isina zvinhu zvinoita kuti ropa riomere iri kushandiswawo.

Zviratidzo

Zviratidzo nezvimwe zvirwere zvehemophilia zvinosiyana, zvichienderana nehuwandu hwako hwezvinhu zvinobatsira kuvhara ropa. Kana huwandu hwako hwezvinhu zvinobatsira kuvhara ropa hwakaderera zvishoma, unogona kubuda ropa chete mushure mekuvhiyiwa kana kukuvara. Kana kushomeka kwako kuri kukuru, unogona kubuda ropa nyore nyore pasina chikonzero chakajeka. Zviratidzo nezvimwe zvirwere zvekuyerera ropa zvinosanganisira: Kuyerera ropa kunoshamisa uye kwakawanda kubva pakachekwa kana kukuvara, kana mushure mekuvhiyiwa kana basa rezino Maronda mazhinji makuru kana akadzika Kuyerera ropa kusina kujairika mushure mekuiswa kwemishonga Kurwadziwa, kuzvimba kana kuoma mumapfundo ako Ropa mumukaka wako kana matumbu Kuyerera ropa mumhuno pasina chikonzero chinozivikanwa Muvana vacheche, kusagadzikana kusina kujekeswa Kurova kwakapusa pamusoro pemusoro kunogona kukonzera kuyerera ropa mubongo renyu kune vamwe vanhu vane hemophilia yakakomba. Izvi hazviiti kazhinji, asi chimwe chezvinhu zvakakomba zvinogona kuitika. Zviratidzo nezvimwe zvirwere zvinosanganisira: Kurwadziwa, musoro unorebesa Kurutsa kazhinji Kurara kana kushaya simba Kuona zvinhu zviviri Kushaya simba kamwe kamwe kana kusakwanisa kufamba zvakanaka Kuita zvinhu zvisina kujairika kana kuita zvinhu zvisina kujairika Tsvaga rubatsiro rwekukurumidzira kana iwe kana mwana wako ane: Zviratidzo kana zvimwe zvirwere zvekuyerera ropa mubongo renyu Kukuvara umo ropa harisi kupera Mapfundo akafuta anopisa kana kubata uye anorwadza kana kukotama

Nguva yekunoona chiremba

Tsvaga kurapwa kwekukurumidza kana iwe kana mwana wako ane:

  • Zviratidzo kana zviratidzo zvekuyerera ropa muuropi
  • Kuhuvara umo ropa risingamiri
  • Zvibatanidzwa zvakazvimba zvinopisa pakubata uye zvinorwadza pakukotama
Zvinokonzera

Kana munhu abuda ropa, kazhinji muviri unosanganisa masero eropa kuti uite ropa rakaoma kuti umise kubuda ropa. Zvinhu zvinoita kuti ropa riome mapuroteni ari muropa anoshanda nemasero anozivikanwa seplatelets kuti uite ropa rakaoma. Hemophilia inoitika kana chikamu chinoita kuti ropa riome chisingawanikwi kana mazinga echiito chinoita kuti ropa riome ari pasi.

Hemophilia kazhinji inowanikwa kubva kuna madzitateguru, zvinoreva kuti munhu anoberekwa ane chirwere ichi (congenital). Hemophilia inoberekwa nayo inoratidzirwa nerudzi rwechiito chinoita kuti ropa riome chiri pasi.

Rudzi runowanzoitika ndiro hemophilia A, rine hukama nemazinga ari pasi e factor 8. Rudzi runotevera rinozivikanwa ndiro hemophilia B, rine hukama nemazinga ari pasi e factor 9.

Vamwe vanhu vanowana hemophilia pasina nhoroondo yemhuri yechirwere ichi. Izvi zvinonzi hemophilia yakawanikwa.

Hemophilia yakawanikwa rudzi rwechirwere ichi runoitika kana sisitimu yemuviri wemunhu ikarwisa chiito chinoita kuti ropa riome 8 kana 9 muropa. Inogona kuwirirana ne:

  • Pamuviri
  • Zvirwere zve autoimmune
  • Cancer
  • Multiple sclerosis
  • Mishonga inokonzeresa

Mumarudzi akajairika e hemophilia, jini rakaipa riri pachromosome ye-X. Munhu wese ane ma chromosomes maviri esex, rimwe kubva kuna mai nerimwe kubva kuna baba. Vakadzi vanowana chromosome ye-X kubva kuna mai ne chromosome ye-X kubva kuna baba. Varume vanowana chromosome ye-X kubva kuna mai ne chromosome ye-Y kubva kuna baba.

Izvi zvinoreva kuti hemophilia inowanzoitika muvakomana uye inopfuudzwa kubva kuna mai kuenda kumwanakomana kuburikidza neimwe yemajini amai. Vakadzi vazhinji vane jini rakaipa vanova vatakuri vasina zviratidzo kana zviratidzo zve hemophilia. Asi vamwe vatakuri vanogona kuva nezviratidzo zve kubuda ropa kana zvinhu zvinoita kuti ropa riome zvadzikira zvishoma.

Zvinhu zvinokonzera njodzi

Chikonzero chikuru chinokonzera hemophilia ndechekuva nemhuri inotamburawo nedambudziko iri. Varume vane mukana wakakura wekuve nehemophilia kupfuura vakadzi.

Matambudziko

Zvinetso zvehemophilia zvinogona kusanganisira:

  • Kubuda kweropa mumhino kana mutsipa. Izvi zvinogona kukanganisa kugona kwemunhu kubata mweya.
  • Hutachiona. Kana zvinhu zvinobatsira ropa kugwamba zvinoshandiswa kurapa hemophilia zvichibva muropa remunhu, pane njodzi yakawedzera yehutachiona hwemuvirusi senge hepatitis C. Nekuda kwemaitiro ekutarisa vanopa ropa, njodzi iyi yakaderera.
  • Kuita kwakaipa kumishonga inobatsira ropa kugwamba. Kune vamwe vanhu vane hemophilia yakakomba, masimba emuviri anorwisa zvirwere ane kuita kwakaipa kumishonga inobatsira ropa kugwamba inoshandiswa kurapa kubuda kweropa. Kana izvi zvikaitika, masimba emuviri anorwisa zvirwere anoita mapuroteni anodzivirira mishonga inobatsira ropa kugwamba kuti isashande, zvichiita kuti kurapwa kusave kwakanaka.
Kuongorora

Matambudziko akaoma e hemophilia kazhinji anowanikwa mukati megore rekutanga rehupenyu. Zvimiro zvinyoro zvingasave pachena kusvika pakuva mukuru. Vamwe vanhu vanoziva kuti vane hemophilia mushure mekunge varasa ropa zvakanyanya panguva yekuvhiya.

Kuongororwa kwezvinhu zvinobatsira pakugwamba ropa kunogona kuratidza kushomeka kwezvinhu zvinobatsira pakugwamba ropa uye kuona kuti hemophilia yakakomba sei.

Kune vanhu vane nhoroondo yemhuri yehemophilia, bvunzo dzemajini dzinogona kushandiswa kuziva vanotakura kuti vaite sarudzo dzakakodzera pamusoro pekuita mimba.

Zvinokwanisikawo kuona panguva yekuzvitakura kana fetus yakabatwa nehemophilia. Zvisinei, bvunzo iyi ine njodzi kune fetus. Kurukurai zvakanakira nezvayakaipira bvunzo iyi nachiremba wenyu.

Kurapa

Kurapa kukuru kwehemophilia yakakomba kunosanganisira kutsiva chikamu chekuvharisa ropa chaunoda kuburikidza nehwamanda iri muchikamu.

Kurapa uku kwekutsiva kunogona kupiwa kurapa kuyerera kweropa kuri kuitika. Kunogonawo kupiwa nguva dzose pamba kubatsira kudzivirira kuyerera kweropa. Vamwe vanhu vanowana kurapa kwekutsiva nguva dzose.

Chikamu chekuvharisa ropa chinogona kugadzirwa kubva muropa rakapa. Zvigadzirwa zvakafanana, zvinonzi recombinant clotting factors, zvinogadzirwa mulaboratori, kwete kubva muropa remunhu.

Kurapa kwakasiyana-siyana kunosanganisira:

  • Emicizumab (Hemlibra). Uyu mushonga mutsva usingasanganisiri zvikamu zvekuvharisa ropa. Mushonga uyu unogona kubatsira kudzivirira kuyerera kweropa kune vanhu vane hemophilia A.
  • Mishonga inodzivirira kuparara kwema clots. Inonyanya kuzivikanwa se anti-fibrinolytics, mishonga iyi inobatsira kudzivirira ma clots kuti arege kupatsanuka.
  • Fibrin sealants. Idzi dzinogona kuiswa zvakananga panzvimbo dzekuvava kuti dziwedzere kuvharisa ropa nekurapa. Fibrin sealants inobatsira zvikuru pakurapa mazino.
  • Kurapa kwemuviri. Kunogona kuderedza zviratidzo kana kuyerera kweropa mukati memuviri kwakakuvadza majoini ako. Kukuvadzwa kukuru kunogona kuda kuvhiya.

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