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Cardiomyopathy Hypertrophic

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Pfupiso

Mukushaya kwekuwedzera kwemhasuru yemoyo, madziro emhasuru yemoyo anonzi septum kazhinji anowedzera kupfuura zvakajairwa. Asi kuwedzera uku kunogona kuitika chero kupi munzvimbo yepasi pemoyo kuruboshwe, inonziwo left ventricle.

Hypertrophic cardiomyopathy (HCM) chirwere umo mhasuru yemoyo inowedzera, inonziwo hypertrophied. Mhasuru yemoyo yakakura inogona kuita kuti zviome kumotokari yemoyo kuburitsa ropa.

Vanhu vazhinji vane hypertrophic cardiomyopathy havazivi kuti vane. Izvozvo ndizvo nekuti vane zviratidzo zvishoma, kana zvisina. Asi muhuwandu duku hwevanhu vane HCM, mhasuru yemoyo yakakura inogona kukonzera zviratidzo zvakakomba. Izvi zvinosanganisira kushomeka kwekufema uye kurwadziwa pabvudzi. Vamwe vanhu vane HCM vane shanduko muchikamu chemagetsi yemoyo. Shanduko idzi dzinogona kukonzera kurova kwemoyo kusina kujairika kunouraya kana rufu rwakatonyanya kukurumidza.

Zviratidzo

Zviratidzo zve hypertrophic cardiomyopathy zvinogona kusanganisira chimwe kana kupfuura zvinotevera: Kurwadziwa kwepfupa, kunyanya panguva yekurovedza muviri. Kuenda mumarwadzo, kunyanya panguva kana mushure mekurovedza muviri kana mamwe mabasa emuviri. Kunzwa kwekurova kwemoyo nekukurumidza, kuzunguza kana kurova kwakasimba kunonzi palpitations. Kushaya mweya, kunyanya panguva yekurovedza muviri. Zvirwere zvakawanda zvinogona kukonzera kushaya mweya nekurova kwemoyo nekukurumidza, kwakasimba. Zvakakosha kuongororwa nekukurumidza kuti uwane chikonzero uye uwane kurapwa kwakakodzera. Ona chiremba wako kana uine nhoroondo yemhuri yeHCM kana chero zviratidzo zvine chekuita ne hypertrophic cardiomyopathy. Fonera 911 kana nhamba yako yekukurumidzira yemuno kana uine chero chezviratidzo zvinotevera kwemaminitsi mashoma kupfuura: Kurova kwemoyo nekukurumidza kana kusina kururama. Kushaya mweya. Kurwadziwa kwepfupa.

Nguva yekunoona chiremba

Zvirwere zvizhinji zvinogona kukonzera kushaya mweya nemwoyo unokurumidza kurova. Zvakakosha kuongororwa nekukurumidza kuti uwane chikonzero uye uwane kurapwa kwakakodzera. Ona chiremba wako kana uine nhoroondo yemhuri yeHCM kana chero zviratidzo zvine chekuita ne hypertrophic cardiomyopathy.

Fona 911 kana nhamba yako yekukurumidzira kana uine chero chezviratidzo zvinotevera kwemaminitsi anopfuura mashomanana:

  • Kurova kwemwoyo kukurumidza kana kusina kururama.
  • Kushaya mweya.
  • Kurwadziwa pabvudzi.
Zvinokonzera

Hypertrophic cardiomyopathy kazhinji inokonzerwa nekuchinja kwemajini anokonzera kuti tsandanyama yemoyo ikurumidze kukora.

Hypertrophic cardiomyopathy kazhinji inokanganisa rusvingo ruri pakati pekamuri mbiri dziri pasi pemoyo. Rusvingo urwu runonzi septum. Makamuri anonzi ventricles. Rusvingo rwakakura runogona kudzivirira kuyerera kweropa kubva pamoyo. Izvi zvinonzi obstructive hypertrophic cardiomyopathy.

Kana pasina kudzivirirwa kukuru kwekuyerera kweropa, mamiriro acho anonzi nonobstructive hypertrophic cardiomyopathy. Asi kamuri huru yekupomba yemoyo, inonzi left ventricle, inogona kuoma. Izvi zvinoita kuti zviome kuti moyo uzorore. Kuomarara uku kunoderedzawo huwandu hweropa rinochengetwa ne ventricle uye rinotumira mumuviri nekumhanya kwemoyo kwega kwega.

Masero etsandanyama yemoyo anorongeka zvakasiyanawo muvanhu vane hypertrophic cardiomyopathy. Izvi zvinonzi myofiber disarray. Zvinogona kutanga kumhanya kwemoyo kusina kururama kune vamwe vanhu.

Zvinhu zvinokonzera njodzi

Hypertrophic cardiomyopathy kazhinji inopfuudzwa kuburikidza nemhuri. Izvo zvinoreva kuti inogara ichipfuudzwa. Vanhu vane mubereki mumwe chete ane hypertrophic cardiomyopathy vane mukana we50% wekuva nechinja chejini chinokonzera chirwere ichi.

Vabereki, vana, kana hanzvadzi dzemunhu ane hypertrophic cardiomyopathy vanofanira kubvunza timu yavo yekuchengetedza utano nezve bvunzo dzekuongorora chirwere ichi.

Matambudziko

Zvinetso zve hypertrophic cardiomyopathy zvinogona kusanganisira:

  • Atrial fibrillation (AFib). Tsandanyama yemoyo yakakura uye kuchinja muumboo ma cell emoyo zvinogona kutungamirira kune kurova kwemoyo kusina kururama uye kazhinji kunokurumidza kunonzi AFib. AFib inowedzerawo njodzi yekukora kweropa, iyo inogona kufamba kuenda kuuropi uye kukonzera stroke.
  • Kuumbwa kweropa. Muvanhu vazhinji, tsandanyama yemoyo yakakura inodzivirira kuyerera kweropa kubva pamoyo. Izvi zvinogona kukonzera kushomeka kwemhepo nemabasa, kurwadziwa pachipfuva, kuzvinzwa musoro uye kupera simba.
  • Mitral valve disease. Kana tsandanyama yemoyo yakakura ichidzivirira kuyerera kweropa kubva pamoyo, valve iri pakati pekamuri dzemoyo dzekuruboshwe ingasavharwa zvakanaka. Iyo valve inonzi mitral valve. Kana isingavharwe zvakanaka, ropa rinogona kudzokera kumashure mukamuri yepamusoro yekuruboshwe. Iyi mamiriro anonzi mitral valve regurgitation. Inogona kuita kuti zviratidzo zve hypertrophic cardiomyopathy zviwedzere kuipa.
  • Dilated cardiomyopathy. Muhuwandu duku hwevanhu vane HCM, tsandanyama yemoyo yakakura inoshaya simba uye haishande zvakanaka. Iyo mamiriro anoita sekutanga mukamuri yepasi yemoyo yekuruboshwe. Iyo kamuri inokura. Moyo unopomba nesimba shoma.
  • Kukundikana kwemoyo. Nekufamba kwenguva, tsandanyama yemoyo yakakura inogona kuoma zvakanyanya kuzadza moyo neropa. Somugumisiro, moyo haugone kupomba ropa rakakwana kuti usangane nezvinodiwa nemuviri.
  • Kupera simba, kunonziwo syncope. Kurova kwemoyo kusina kururama kana kuumbwa kweropa dzimwe nguva kunogona kukonzera kupera simba. Kupera simba kusina tsananguro kunogona kuenderana nerufu rwemoto kamwe kamwe, kunyanya kana zvikaitika munguva pfupi yapfuura uye mumunhu mudiki.
  • Rufu rwemoto kamwe kamwe. Zvisingawanzoitika, hypertrophic cardiomyopathy inogona kukonzera rufu rwemoto kamwe kamwe muvanhu vezera rose. Vanhu vazhinji vane hypertrophic cardiomyopathy havazivi kuti vane iyo. Somugumisiro, rufu rwemoto kamwe kamwe rungave chiratidzo chekutanga chemamiriro acho. Inogona kuitika muvechidiki vanoita sekutendeuka, kusanganisira vatambi vechikoro chesekondari nevamwe vechidiki, vakuru vanoshanda.
Kudzivirira

Hapana nzira inozivikanwa yekudzivirira hypertrophic cardiomyopathy (HCM). Zvakakosha kuwana mamiriro acho nemiedzo pakutanga sezvinobvira kuitira kuti kurapwa kuitwe uye kudzivirira matambudziko. Hypertrophic cardiomyopathy kazhinji inopfuudzwa mumhuri. Kana uine mubereki, hanzvadzi, hanzvadzi kana mwana ane hypertrophic cardiomyopathy, bvunza timu yako yekuchengetedza utano kana kuongororwa kwemajini kuri kwauri. Asi kwete munhu wese ane HCM ane shanduko yegene iyo miedzo inogona kuwana. Uyewo, makambani emishuwarenzi mamwe angasave nechokwadi chekuongororwa kwemajini. Kana kuongororwa kwemajini kuchinge kusina kuitwa, kana mhedzisiro yacho isina kubatsira, kuongororwa kunogona kuitwa ne echocardiograms dzakawanda. Echocardiograms inoshandisa mafungu ekuita mifananidzo yemoyo. Kune vanhu vane nhengo yemhuri ine hypertrophic cardiomyopathy: - Kuongororwa kweEchocardiogram kunokurudzirwa kutanga pazera remakore anenge 12. - Kuongororwa ne echocardiograms kunofanira kuenderera mberi gore rega rega kusvika ku3 kuburikidza nemakore e18 kusvika ku21. - Mushure maizvozvo, kuongororwa kunogona kuitwa makore mashanu ese kuburikidza nehupenyu hwemunhu mukuru. Ungada kuita echocardiogram kazhinji zvichienderana nehutano hwako hwese uye sarudzo yetimu yako yekuchengetedza utano.

Kuongorora

Munachirebvu anoongorora uye anoteerera mwoyo wako uchishandisa chishandiso chinonzi stethoscope. Kunzwika kwemwoyo kunogona kunzwika pakuiteerera mwoyo.

Mumwe wechikwata chehutano hwako kazhinji anobvunza mibvunzo nezve zviratidzo zvako uye nhoroondo yako yehutano nemhuri. Kuongororwa kwemajini kana mazano kunogona kukurudzirwa kana uine nhoroondo yemhuri yeiyi mamiriro.

Kuongororwa kunoitirwa kuongorora mwoyo uye kutsvaga zvinokonzera chero zviratidzo.

  • Echocardiogram. Echocardiogram kazhinji inoshandiswa kuona hypertrophic cardiomyopathy. Mafungu ezwi anoshandiswa kugadzira mifananidzo yemwoyo unorova. Kuongororwa uku kunoratidza kuti mapapu nemichinjikwa yemwoyo inoshanda sei pakupomba ropa. Echocardiogram inogonawo kuona kana tsandanyama yemwoyo yakakura kupfuura zvaifanira.
  • Electrocardiogram (ECG kana EKG). Kuongororwa uku kukurumidza uye kusina marwadzo kunoyera basa remagetsi remwoyo. Mapatches anobatanidza anonzi electrodes anoiswa pachipfuva uye dzimwe nguva pamaoko nemakumbo. Waya inobatanidza ma electrodes ku komputa, iyo inodhinda kana kuratidza mhinduro dzekuongorora. ECG inogona kuratidza kurova kwemwoyo kusina kururama uye zviratidzo zvekukora kwemwoyo.
  • Holter monitor. Chishandiso ichi chidiki, chinofambisika cheECG chinotora basa remwoyo. Chinopfekwa kwezuva kana maviri uchitoita mabasa ako emazuva ese.
  • Cardiac MRI. Kuongororwa uku kunoshandisa ma magnets ane simba nema radio waves kugadzira mifananidzo yemwoyo. Inopa ruzivo nezve tsandanyama yemwoyo uye kuti mwoyo ne michinjikwa yemwoyo inoshanda sei. Kuongororwa uku kazhinji kunoitirwa ne echocardiogram.
  • Stress test. Stress test kazhinji inosanganisira kufamba pane treadmill kana kukwira bhasikoro risingafambi uchiteerera mwoyo. Kuongororwa kwe stress test kunobatsira kuratidza kuti mwoyo unopindura sei kune zvemuviri.
  • Cardiac CT scan. Zvisingawanzoitika, kuongororwa uku kunoitirwa kuona hypertrophic cardiomyopathy. Asi kunogona kukurudzirwa kana MRI isingakwanisi kushandiswa. Cardiac CT scan inoshandisa X-rays kugadzira mifananidzo yemwoyo nechipfuva. Inogona kuratidza saizi yemwoyo.
Kurapa

Zvinangwa zvechirwere che hypertrophic cardiomyopathy ndechekudzikisa zviratidzo uye kudzivirira rufu rwenguva pfupi rwemoyo kune vanhu vane njodzi yakakura. Kurapwa kunotsamira pakukura kwezviratidzo. Kana uine cardiomyopathy uye uri nepamuviri kana uchifunga nezvekuva nepamuviri, taura nachiremba wako. Ungatumirwa kuna chiremba ane ruzivo mukuita nepamuviri ine njodzi yakakura. Uyu chiremba angave perinatologist kana nyanzvi yezvehutano hwamai nembereko. Mishonga Mishonga inogona kubatsira kuderedza simba remhasuru yemoyo inosvina uye kunonoka kumhanya kwemoyo. Nenzira iyoyo, moyo unogona kuburitsa ropa zviri nani. Mishonga yekurapa hypertrophic cardiomyopathy nezviratidzo zvaro inogona kusanganisira: Beta blockers senge metoprolol (Lopressor, Toprol-XL), propranolol (Inderal LA, Innopran XL) kana atenolol (Tenormin). Calcium channel blockers senge verapamil (Verelan) kana diltiazem (Cardizem, Tiazac, nezvimwewo). Mushonga unonzi mavacamten (Camzyos) unoderedza kumanikidzwa kwemoyo. Inogona kurapa obstructive HCM muvakuru vane zviratidzo. Timu yako yekuchengetedza utano inogona kukurudzira mushonga uyu kana usingakwanisi kutora kana usingaoneke uchifambira mberi ne beta blockers kana verapamil. Mishonga yekumhanya kwemoyo senge amiodarone (Pacerone) kana disopyramide (Norpace). Mishonga inononotsa ropa senge warfarin (Jantoven), dabigatran (Pradaxa), rivaroxaban (Xarelto) kana apixaban (Eliquis). Mishonga inononotsa ropa inogona kubatsira kudzivirira kuumbwa kweropa kana uine atrial fibrillation kana rudzi rwe apical hypertrophic cardiomyopathy. Apical HCM inogona kuwedzera njodzi yerufu rwenguva pfupi rwemoyo. Kuongororwa kana mamwe maitiro Septal myectomy Wedzera mufananidzo Vhara Septal myectomy Septal myectomy Septal myectomy ndiro kuongororwa kwemoyo wakavhurwa. Chiremba anobvisa chikamu che septum yakakura, yakakura pakati pekamuri dzemoyo dziri pasi anonzi ventricles, sezvakaratidzwa pamoyo uri kurudyi. Apical myectomy Wedzera mufananidzo Vhara Apical myectomy Apical myectomy Apical myectomy ndiro kuongororwa kwemoyo wakavhurwa kurapa hypertrophic cardiomyopathy. Chiremba anobvisa mhasuru yemoyo yakakura pedyo nekumucheto kwemoyo. Kuongororwa kwakawanda kana maitiro aripo ekurapa cardiomyopathy kana zviratidzo zvaro. Zvinosanganisira: Septal myectomy. Iyi kuongororwa kwemoyo wakavhurwa kunogona kukurudzirwa kana mishonga isina kuvandudza zviratidzo. Zvinosanganisira kubvisa chikamu chemadziro akakura, akakura pakati pekamuri dzemoyo. Uyu madziro anonzi septum. Septal myectomy inobatsira kuvandudza kuyerera kweropa kubva mumoto. Inoderedzawo kuyerera kwepamusoro kweropa kuburikidza ne mitral valve. Kuongororwa kunogona kuitwa uchishandisa nzira dzakasiyana, zvichienderana nekwakagara mhasuru yemoyo yakakura. Mumhando imwe, inonzi apical myectomy, vanachiremba vanobvisa mhasuru yemoyo yakakura pedyo nekumucheto kwemoyo. Dzimwe nguva mitral valve inogadziriswa panguva imwe chete. Septal ablation. Iyi nzira inoshandisa doro kudzikisa mhasuru yemoyo yakakura. Tube refu, yakatetepa inonzi catheter inoisirwa mu artery inopa ropa kunzvimbo yakabatwa. Doro rinoyerera kuburikidza ne tube. Kushanduka mumagetsi emagetsi emoyo, anonziwo heart block, ndiro rimwe dambudziko. Heart block inofanira kurapwa ne pacemaker. Chishandiso chidiki chinoiswa muchidzitiro kubatsira kudzora kumhanya kwemoyo. Implantable cardioverter-defibrillator (ICD). Ichi chishandiso chinoiswa pasi peganda pedyo ne collarbone. Inoramba ichiongorora kumhanya kwemoyo. Kana chishandiso chacho chawana kumhanya kwemoyo kwasinganzwisisiki, chinopa magetsi mashoma kana ane simba kuti gadzirise kumhanya kwemoyo. Kushandiswa kwe ICD kwakaratidzwa kubatsira kudzivirira rufu rwenguva pfupi rwemoyo, runowanikwa muhuwandu hudiki hwevanhu vane hypertrophic cardiomyopathy. Cardiac resynchronization therapy (CRT) device. Zvisingawanzoitika, ichi chishandiso chakaiswa chinoshandiswa kurapa hypertrophic cardiomyopathy. Inogona kubatsira makamuri emoyo kusvina nenzira yakarongeka uye inoshanda. Ventricular assist device (VAD). Ichi chishandiso chakaiswa hachishandiswi kazhinji kurapa hypertrophic cardiomyopathy. Inobatsira kuyerera kweropa kuburikidza nemoyo. Heart transplant. Iri kuongororwa kwekuchinja moyo une chirwere nemoyo une hutano wemupi. Inogona kuva sarudzo yekurapa kupera kwemoyo kana mishonga nemamwe kurapwa zvisingashandi. Hypertrophic cardiomyopathy nezvisarudzo zvekurapa Tambanudza Tambanudza Kudzoka kune vhidhiyo 00:00 Tambanudza Tsvaga masekondi gumi kumashure Tsvaga masekondi gumi mberi 00:00 / 00:00 Mute Settings Mufananidzo mumufananidzo Screen yakazara Ratidza kopi yevhidhiyo Hypertrophic cardiomyopathy nezvisarudzo zvekurapa Steve R. Ommen, M.D., Zvirwere zveCardiovascular, Mayo Clinic: Hypertrophic cardiomyopathy ndiro mamiriro akave asingazivikanwe uye anotyisa kwazvo pasi rese. MuUnited States chete, kune vanhu vanopfuura hafu yemamirioni vane hypertrophic cardiomyopathy, vazhinji vavo vasina zviratidzo uye vasina kuziva nezvechirwere chavo. Vamwe vanhu vanogona kufa kamwe kamwe. Rufu rwenguva pfupi rwemoyo runowanzoitika pasina chiziviso. Hartzell V. Schaff, M.D., Kuongororwa Kwemoyo, Mayo Clinic: Anopfuura 2/3 evagari vemo vachava nekuvhara. Uye kuvhara kwechigadziko chekuyerera kwepamusoro kwepamusoro ndicho chiratidzo chekuongororwa muvarwere vane zviratidzo. Saka tinoziva zvino kuti 2/3 yevagari vemo vane hypertrophic cardiomyopathy uye kuvhara ndivo vanokodzera kuongororwa. Dr. Ommen: Hypertrophic cardiomyopathy ndiyo yakajairika cardiomyopathy yakagara nhaka kana chirwere chemhasuru yemoyo. Vanhu vanoberekwa nemagadzirirwo ayo, asi hypertrophy haioneke kutanga kukura kusvika pakuchembera, kukura kwemhasuru, kana kupfuura. Zvinogoneka kuti vacheche vaberekwe nemhasuru dzemoyo dzakakura, asi izvozvo zvisingawanzoitika uye kazhinji zviratidzo zvakakomba zvemushonga. Uye zvakare zvakarondedzerwa sekusauya kusvika vanhu vakasvika mumakore avo mashanu kana matanhatu ehupenyu. Saka zvechokwadi, kutanga kunogona kuva chero nguva yehupenyu. Uye zvechokwadi zviratidzo zvinogona kuitika muhupenyu hwese. Dr. Schaff: Zviratidzo zvakajairika izvo varwere vane kana vane obstructive hypertrophic cardiomyopathy ndeyekufema, kurwadziwa kwepfupa kwakafanana ne angina uye syncope. Uye zvinosuwisa, zvimwe zvezviratidzo izvi zvinoitika zvishoma nezvishoma uye kwenguva yakareba zvekuti varwere havazonyatsonzwisisi kuti vakaganhurirwa sei. Dr. Ommen: Kune varwere vane zviratidzo nekuda kwe hypertrophic cardiomyopathy, mutsetse wekutanga wekurapa ndeyekushandisa kurapwa kwemishonga, mishonga. Kazhinji, izvozvo ndekuwedzera mishonga chaiyo, asi dzimwe nguva varwere vari pamishonga inogona kuita kuti mamiriro avo aipisire. Saka imwe yekurapa inonyanya kushanda ndeyekubvisa zvinhu zvisina kunaka, uye zvichida kuwedzera zvinhu zvakakodzera kuvatsigira nezviratidzo zvavo pasi. Kune varwere vasina kupindura kune izvo shanduko dzemishonga, kana kuti avo mishonga yakakonzeresa zvinokonzeresa zvisingagumiri, ipapo ndapoka tinofamba kuenda kune zvinhu senge kuongororwa kwemasikirwo, izvo zvinogona kubvisa zviratidzo zvavo zvakajeka. Dr. Schaff: Varwere vanotumirwa kuongororwa vanowanzova vakakundikana kurapwa kwemishonga kana vane zvinokonzeresa kubva mumishonga inovaganhurira sezvakaita zviratidzo kubva ku hypertrophic cardiomyopathy. Saka kuongororwa kwekuvhara kwepamusoro kwepamusoro ndekubvisa zviratidzo. Uye muvamwe varwere, kuvarambidza kutora mishonga ine zvinokonzeresa zvisingadiwi. Dr. Ommen: Kuongororwa kwemasikirwo kwave kuri kuongororwa kwakabudirira kwazvo kune vazhinji vevarwere vedu. Nekudaro, haishandiswe sezvakaita zvingave zvichikonzerwa nepfungwa dzekare pamusoro penjodzi yakawedzera nekuongororwa, kushayikwa kwekuwanikwa kwese kwevanachiremba vanogona kuzviita. Asi mumaoko emakiriniki ane ruzivo, mitengo yekukanganisa yakaderera uye mitengo yedu yekubudirira yakakwira. Dr. Schaff: Iye zvino tinoita septal myectomy yakakura inosvika pakukura kwemoyo. Uye takadzidza nemakore kuti chikamu ichi chekupedzisira chemyectomy ndicho chinonyanya kukosha maererano nekubvisa zviratidzo. Varwere vashoma vakaita kuongororwa kwechipiri, vakatumirwa kwatiri mushure mekuita kuongororwa kwakakundikana, takawana kuti myectomy yakanga isina kuitwa zvakakwana mumoyo. Hazvisi kukura kwemhasuru. Iri kungoita kuongororwa kwakakwana kwepakutanga. Dr. Ommen: Ne septal myectomy, chiremba anobvisa chikamu che septum yakakura, iyo iri kunyanyisa nzira yeropa, kubva mumoto. Nekuita izvi, inochinja nzira yeropa rinoyerera kuburikidza ne ventricle. Inobvumira mitral valve kushanda zvakanaka. Uye inobvumira ropa kubva mumoto pasina kuwedzera kumanikidzwa kana kuwedzera simba. Iyi mhasuru haikuri zvakare nekufamba kwenguva. Iri kugadziriswa kwenguva refu. Dr. Schaff: Takawana kuti zvisingawanzoitika kuita chimwe chinhu ku mitral valve. Uye njodzi yekuita chimwe chinhu ku mitral valve, apo zvinoratidzika kuti hazvina kukosha, ndeyekuti mukana wekukuvadzwa uripo. Saka tinoda kuita septal myectomy, kubva kubaya, kuongorora mitral valve ne echocardiogram panguva yekuongororwa, usati watarisana ne mitral valve kana paine regurgitation yakasara. Tinogona kuziva kana mitral regurgitation yakabviswa pakarepo mushure memyectomy kana aorta yakavharwa uye moyo watangazve. Echocardiogram inoitirwa mukamuri yekuongororwa uye tinoziva pakarepo kana mitral regurgitation yakabviswa. Kuongororwa kuripo kune vamwe varwere vane non-obstructive hypertrophic cardiomyopathy. Uye ava varwere vane kupararira kwe apical hypertrophy. Vamwe vevarwere ava vane diastolic heart failure nekuda kwemakomba maduku emoyo. Uye muvarwere ava, kuita transapical myectomy kuwedzera ventricle kunogona kuvandudza zviratidzo zvavo zve heart failure. Dr. Ommen: Patinoona mhedzisiro huru kubva ku septal myectomy sezvinoitwa iye zvino, ichi chinhu chinofanira kuitwa chete kumakiriniki ane ruzivo. Data yazvino yakabuda yakaratidza kuti kumakiriniki ane huwandu hudiki, hwakati hwakati, uye kunyange "huwandu hukuru", kune gradient yekufa, zvinoreva kuti yakakwira kumakiriniki ane huwandu hudiki uye yakaderera kumakiriniki ane huwandu hukuru. Asi kunyange izvo zvinonzi makiriniki ane huwandu hukuru ane mitengo yekufa yakakwira zvakanyanya pane zvinoratidzwa kubva kumakiriniki ane ruzivo. Uye iyi nzira inofanira kuitwa neavo vanoziva zvakanyanya nezve iyi nzira, uye vanoita zvakawanda. Dr. Schaff: PaMayo Clinic, takaita kuongororwa kunopfuura 3,000 kwe hypertrophic cardiomyopathy. Tinoita kuongororwa kwe200 kusvika ku250 gore rega rega. Kufa kwekuongororwa uku kuri pasi pe1%, kunyanya kune varwere vane hutano. Dr. Ommen: Chimwe chezvinhu zvikuru zvechero kutaurirana kwandinacho nevarwere ndechekuvabatsira kunzwisisa kuti njodzi yavo yekufa kwenguva pfupi rwemoyo ingave yakakura sei, uye kana vangafunga kuve ne implantable defibrillator. Varwere vedu vakaita kuongororwa vane huwandu hudiki hwerufu rwenguva pfupi rwemoyo uye huwandu hudiki hwe defibrillators dzavo kudzima pakati pe avo vakadaro. Dr. Schaff: Chimwe chezvinhu zvatakadzidza mushure mekuita septal myectomy ndechekuti chaizvoizvo kuitika kwe ventricular arrhythmia zvinoita sekuderera. Uye izvi zvinoratidzwa mune zvidzidzo zvinotarisa defibrillator discharges uye mitengo yerufu rwenguva pfupi. Dr. Ommen: Nzira yekagara nhaka ye hypertrophic cardiomyopathy ndeye autosomal dominant, zvinoreva kuti mumwe nemumwe wevana vemurwere ane HCM ane mukana we50/50 wekugara nhaka iyi chirwere. Tinokurudzira kuongororwa kwehama dzepedyo, izvo zviri bvunzo yemagadzirirwo kana kuongororwa kwakavakirwa pa echocardiography. Kana mhuri yasarudza kushandisa echocardiography seshumiro yavo yekuongorora, tinokurudzira kuti hama dzepedyo dzakura dziongororwe makore mashanu ese. Hama dzepedyo dziri kuyaruka kana vatambi, tinowanzoongorora mwedzi yega yega ye12 kusvika ku18. Dr. Schaff: Septal myectomy inorapisa zviratidzo zve hypertrophic cardiomyopathy kana ichibvisa kuvhara. Asi zvechokwadi, varwere vachiri kuve ne hypertrophic cardiomyopathy, vachiri kuda kuteverwa nachiremba wavo nezvimwe zvinetso zvine chekuita ne hypertrophic cardiomyopathy. Asi ndinotarisira, vanobviswa kufema, kurwadziwa kwepfupa, kana kushaya simba kunotungamira kuongororwa. Rumwe Ruzivo Hypertrophic cardiomyopathy care paMayo Clinic Ablation therapy Implantable cardioverter-defibrillators (ICDs) Pacemaker Vhidhiyo: Septal myectomy ne apical myectomy Ratidza rumwe ruzivo rwakabatana Kumbira musangano

Kuzvitarisira

Taura neshamwari nemhuri kana boka rekutsigira. Ungawana kuti kutaura nezve hypertrophic cardiomyopathy nevamwe vari munzvimbo dzakafanana kunogona kubatsira. Zvakakoshawo kudzora kushushikana kwemanzwiro. Kuwedzera kurovedza muviri uye kuita fungisisa inzira dzekuzorodza kushushikana. Kana uine kunetseka kana kuora mwoyo, taura nechikwata chehutano hwako nezano ekubatsira.

Kugadzirira musangano wako

Unogona kutumirwa kuna chiremba akarovedzwa pamusoro pezvirwere zvemoyo. Murwere uyu anozivikanwa sa cardiologist. Heano mamwe mashoko anokubatsira kugadzirira musangano wako. Zvaunogona kuita Kana uchiita musangano, bvunza kana uchifanira kutevera chero zvipingamupinyi usati waita check-up. Semuenzaniso, ungada kuchinja nhanho yako yekushanda kana kudya kwako. Gadzira runyorwa rwe: Zviratidzo zvako uye pavakatanga. Mishonga yose, mavhitaminzi uye zvinowedzerwa zvaunotora, kusanganisira zvikamu. Ruzivo rwakakosha rwezvokurapa, kusanganisira mamwe mamiriro aunova nawo uye nhoroondo yeumhuri yezvirwere zvemoyo. Mibvunzo yekubvunza nyanzvi yako yehutano. Mibvunzo yekubvunza nyanzvi yako yehutano ingasanganisira: Chii chinonyanya kukonzera zviratidzo zvangu? Ndeapi miedzo yandinoda? Ndeapi kurapwa anogona kubatsira? Njodzi dzipi dzinokonzerwa nechirwere chemoyo changu? Ndingazova nemisangano yekutevera kazhinji sei? Ndinofanira kudzora mabasa angu here? Vana vangu kana vamwe hama dzepedyo vanofanira kuongororwa nezve mamiriro aya here, uye ndinofanira kusangana nechiremba we genetic here? Mamwe mamiriro andinawo kana mishonga yandinotora achakanganisa sei mamiriro emoyo wangu? Usazengese kubvunza mimwe mibvunzo yaunayo. Zvaunofanira kutarisira kubva kuchiremba wako Nyanzvi yako yehutano inogona kukubvunza mibvunzo yakadai se: Zviratidzo zvako zvakakomba sei? Zviratidzo zvako zvakachinja sei nekufamba kwenguva? Kana zvakadaro, sei? Kuita zvemuviri kana kushanda kwemuviri kunowedzera zviratidzo zvako here? Wakambotsvaira here? Zvaunogona kuita pakati pezviitiko Zvisati zvasvika musangano wako, bvunza nhengo dzemhuri yako kana paine hama dzakamboonekwa ne hypertrophic cardiomyopathy kana dzakambova nerufu rwakasangoonekwa, rwakatangira kamwe kamwe. Kana kuita zvemuviri kuchideredza zviratidzo zvako, usaita zvemuviri zvakaoma kusvika waona nyanzvi yako yehutano. Kumbira mazano chaiwo ekurovedza muviri. Na Mayo Clinic Staff

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