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Nephrogenic systemic fibrosis (NSF) chirwere chisingawanzoitika asi chine ngozi chinoita kuti ganda rive guruu, rakaoma, uye chinogona kukanganisa nhengo dzemukati. Inowanzoitika kune vanhu vane chirwere cheitsvo chakakomba vakatarisana nemamwe makemikari anoshandiswa mukuongororwa kwezvifananidzo zvemuviri.
Chirwere ichi chakatanga kuzivikanwa kuma1990s ekupedzisira, uye kunyange zvazvo chinonzwa chichitya, kunzwisisa NSF kunogona kukubatsira kuita sarudzo dzakanaka pamusoro pekurapwa kwako. Mashoko akanaka ndeakuti nekuvandudzwa kwezviyero zvekuchengetedza, NSF yave isingawanzoitika kupfuura kare.
NSF chirwere umo muviri wako unogadzira collagen yakawanda, puroteni inopa chimiro kweganda rako nenhengo. Iyi collagen yakawanda inogadzira mapachi akakura, akafanana neganda reguruu paganda rako uye inogona kukonzera kukuvara kwemoyo, mapapu, nenhengo dzakakosha.
Chirwere ichi chinowana zita rayo nekuti pakutanga chaifungidzirwa kuti chinoita paganda chete (systemic fibrosis) uye chinoitika kazhinji kune vanhu vane matambudziko etsvo (nephrogenic). Zvisinei, vanachiremba iye zvino vanoziva kuti chinogona kukanganisa masisitimu akawanda emumuviri wako.
NSF kazhinji inoitika mavhiki kusvika kumwedzi mushure mekutarisana nemagadolinium-based contrast agents. Aya ndiwo marangi chaiwo anoshandiswa pakuongororwa kweMRI nenhanho dzakasiyana dzekuongorora kuti abatsire vanachiremba kuona nhengo dzako zviri nyore.
Zviratidzo zveNSF kazhinji zvinoita zvishoma nezvishoma uye zvinogona kuva nyore kukanganisa nemamwe marwere pakutanga. Kushanduka kweganda rako kazhinji ndiwo maratidziro ekutanga anoyevedza, kunyange zvazvo chirwere ichi chinogona kukanganisa muviri wako wese.
Zviratidzo zvakajairika zvine chekuita neganda zvinosanganisira:
Kushanduka kwe ganda uku kunowanzoonekwa pamaoko nemakumbo ako, asi kunogona kupararira kumucheto wako, chiso, nedzimwe nzvimbo. Ganda rakabatwa rinogona kuita kuti zviome kubendera majoini ako kana kufamba zvakanaka.
Kunze kwezviratidzo zve ganda, NSF inogona kukonzera matambudziko makuru mukati:
Mune zviitiko zvisingawanzoitika, NSF inogona kukurumidza kuitika uye kuva ngozi yehupenyu. Vamwe vanhu vanowana kuipisisa kwakapfupi kwezviratidzo, nepo vamwe vachiwana matambudziko anokanganisa mwoyo yavo, mapapu, kana midziyo yeropa.
NSF inokonzerwa nekuonekwa kune gadolinium-based contrast agents muvanhu vane itsvo dzisingakwanisi kuchenesa zvinhu izvi kubva muropa ravo. Kana gadolinium ikagara mumuviri mako kwenguva yakareba, inogona kutanga kupindura kwemuviri kwakashata kunotungamira pakugadzirwa kwe collagen yakawanda.
Gadolinium ndiyo simbi yakakura inova yakachengeteka kana yakabatana nemamwe makemikari mune contrast agents. Zvisinei, muvanhu vane chirwere chakakomba cheitsvo, mabhondi aya anogona kuputsika, achiburitsa gadolinium yakasununguka mune tishu dzako. Iyi gadolinium yakasununguka inoita kunge inoshanda masero emuviri anokurudzira kukuvara uye fibrosis.
Zvinhu zvakati wandei zvinoona njodzi yako yekuwana NSF mushure mekuonekwa kwe gadolinium:
Hazvisi zvese gadolinium-based contrast agents zvine njodzi imwe chete. Mamwe ekare, linear agents ane mukana mukuru wekuburitsa gadolinium yakasununguka kupfuura mamwe matsva, ane fomula dzakasimba. Ndizvo zvinoita kuti nzvimbo dzakawanda dzekurapa dzashandura kuzvimwe zvakachengeteka pakuongorora varwere vane chirwere cheitsvo.
Unofanira kubata nehutano hwako pakarepo kana ukawana chero shanduko yeganda mushure mekuita MRI kana imwe ongororo yemifananidzo ine contrast, kunyanya kana uine chirwere cheitsvo. Kuziva nekurapa pakutanga kunogona kubatsira kudzivirira mamiriro acho kuti asanyanya kuipa.
Tsvaga rubatsiro rwekurapa nekukurumidza kana ukaona:
Kunyangwe zviratidzo zvako zvichitaridzika zvisina kuoma, zvakakosha kuti uzviongorore nekukurumidza. NSF inogona kukurumidza kuwedzera kune vamwe vanhu, uye kuita zvekurapa pakutanga kunogona kubatsira kudzikisira kana kudzivirira matambudziko akawanda.
Kana uine chirwere cheitsvo uye wakarongedzerwa kuongororwa kwemifananidzo, kurukurai njodzi nemabhenefiti nachiremba wako usati watanga. Vanogona kubatsira kuona kana scan ichifanira kuitwa zvechokwadi uye kuti zviyero zvipi zvingave zvakakodzera.
Njodzi yako yekuwana NSF inonyanya kuenderana nehutano hweitsvo dzako uye kuonana kwako ne gadolinium-based contrast agents. Kunzwisisa izvi zvinokonzera njodzi kunogona kukubatsira iwe nechikwata chako chehutano kuita sarudzo dzakachenjera pamifananidzo yekurapa.
Zvinokonzera ngozi zvakanyanya zvinosanganisira:
Itsvo dzako kazhinji dzinoyerera gadolinium kubva muropa rako mukati memaawa mashoma ekuratidzwa. Kana dzisingashande zvakanaka, gadolinium inogona kuramba iri mumuviri wako kwemavhiki kana mwedzi, ichikwidziridza mukana wekuti ichakonzera matambudziko.
Zvinhu zvimwe zvinogona kuwedzera ngozi yako zvinosanganisira:
Zvinokosha kucherechedza kuti NSF yakasiyana kwazvo kune vanhu vane basa reitsvo rakanaka. Vakawanda vevanhu vanorwara vane kukuvara kwakakomba kweitsvo, ndosaka mazano aripo ikozvino achinyanya kufunga nezvekuchengetedza vanhu ava vanotambura.
NSF inogona kukonzera matambudziko akakomba anokanganisa hupenyu hwako uye hutano hwese. Kunyangwe kuchinja kwe ganda kazhinji kuve dambudziko rinonyanya kuoneka, zviito zvemukati zvinogona kunge zvine ngozi uye zvinotyisa hupenyu.
Matambudziko akajairika anosanganisira kufamba kwako uye kushanda zuva nezuva:
Zvipingamupinyi izvi zvemuviri zvinogona kukanganisa zvikuru kuzvimiririra kwako nekugara zvakanaka kwepfungwa. Vanhu vakawanda vane NSF vanoda rubatsiro mumabasa ezuva nezuva senge kupfeka, kugeza, kana kugadzirira zvokudya.
Zvinetso zvakakomba zvemukati zvinogona kusanganisira:
Mumazuva akaoma zvikuru, NSF inogona kuuraya. Kufa kazhinji kunobva pakukundikana kwemoyo, mvere dzeropa, kana kukundikana kwekufema nekuda kwekuvadzwa kwemapapu. Zvisinei, mugumisiro uyu hauna kujairika, kunyanya nemabatiro ekudzivirira aripo iye zvino uye kuzivikanwa kwakakwana kwechirwere ichi.
Kukura kweNSF kunosiyana zvikuru pakati pevanhu. Vamwe vanhu vanosangana nekuipisisa kwakanyanya, kwakanyanya kwemwedzi kana makore, nepo vamwe vangave nekukura nekukurumidza mukati memavhiki ekutanga kwezviratidzo.
Kuziva NSF kunoda kuongororwa kwakanyatsojeka kwezviratidzo zvako, nhoroondo yekurapa, uye kazhinji biopsy yeskin kuti ubvumikisise chirwere ichi. Chiremba wako acharamba achitsvaga muenzaniso wakajairika wekuchinja kwe ganda ne tishu pamwe nenhoroondo yekuratidzwa kwe gadolinium mumamiriro ezvirwere zveitsvo.
Mupi wako wehutano anotanga nekubvunza mibvunzo yakadzama nezvezviratidzo zvako nenhoroondo yekurapa. Vanoda kuziva nezve chero ongororo dzemafambiro dzakaitwa munguva pfupi yapfuura, basa reitsvo rako, uye kana zviratidzo zvako zvakabuda. Ruzivo urwu runobatsira kuona kana NSF iri chirwere chinogona kunge chiripo.
Kuongororwa kwemuviri kunotarisa paganda rako nemapfundo:
Kazhinji biopsy yeganda inodiwa kuti uone chirwere chacho. Izvi zvinosanganisira kutora sampuli diki ye tishu yeganda rakarwara kuti iongororwe pasi pe microscope. Biopsy ichaona maitiro akafanana ekuwedzera kwe collagen nekuchinja kwekuzvimba kunotsanangura NSF.
Kuongororwa kwakawedzerwa kunogona kusanganisira kuongororwa kweropa kuti uone basa reitsvo dzako uye kuongororwa kwemuviri kuti uongorore mwoyo wako nemapapu. Zvisinei, vanachiremba vanochenjera kwazvo pakushandisa gadolinium-based contrast mumamiriro ezvinhu anofungidzirwa eNSF, kazhinji vachisarudza nzira dzakasiyana dzekuongorora kana zvichibvira.
Zvinosuruvarisa, hapana bvunzo yeropa kana kuongororwa kwemuviri kunogona kuona NSF zvakajeka. Kuona chirwere kunobva pakubatanidza uchapupu hwakawanda, ndosaka kushanda nevanachiremba vane ruzivo kwakakosha kwazvo.
Parizvino, hapana mushonga weNSF, asi kurapwa kwakawanda kunogona kubatsira kudzora zviratidzo uye zvichida kudzikisa kufambira mberi kwechirwere. Danho rinokosha ndekuvandudza basa reitsvo dzako kana zvichibvira, sezvo izvi zvinogona kubatsira muviri wako kubvisa gadolinium yakasara.
Kana usati uri kurapwa nedialysis, kutanga kurapwa nedialysis kunogona kubatsira kubvisa gadolinium mumuviri wako. Kune vamwe vanhu, izvi zvinogona kuita kuti zviratidzo zvavo zveNSF zvidzikire, kunyange zvazvo mhinduro inosiyana zvikuru pakati pevanhu.
Kusimudzirwa kweitsvo kunopa tariro yakanakisa yekuvandudzika kwezviratidzo zveNSF. Vanhu vazhinji vanowana kusimudzirwa kweitsvo kwakabudirira vanoona ganda ravo richinyorovedzwa zvishoma nezvishoma uye kuvandudzika kwekuenda kwenguva. Zvisinei, kusimudzirwa hakugoneki kune munhu wese, uye kuvandudzika kunogona kutora mwedzi kana makore kuti kuitike.
Kurapa kunotsigira kunotarisa pakutonga zviratidzo nekutsigira hupenyu hwako hwakanaka:
Vamwe vanachiremba vakashandisa mishonga yakasiyana-siyana kurapa NSF, kusanganisira mishonga inodzora immune system, asi mhinduro dzakasiyana-siyana. Aya kurapa achiri kufungwa sekuedzwa uye anogona kuuya nemigumisiro yavo.
Phototherapy (kurapa kwechiedza che ultraviolet) yakaratidza tariro mune zvidzidzo zviduku, asi kunodiwa kutsvakurudza kuwedzera kusimbisa kushanda kwayo nekudzivirira. Kurapa kwakasiyana-siyana kuri kufungwa kunosanganisira mamwe marudzi eantibiotic nemishonga inodzora kuzvimba.
Kiyi yekutonga NSF ndeyekushanda nesangano revanachiremba vanonzwisisa mamiriro acho ezvinhu. Izvi zvinogona kusanganisira nephrologists, dermatologists, rheumatologists, uye nyanzvi dzekurapa.
Kutonga NSF kumba kunosanganisira kutarisisa pakutarisira ganda, kuchengetedza kufamba, uye kudzivirira matambudziko. Paunenge uchida kutarisirwa kwakajairwa kwemishonga, kune zvinhu zvakawanda zvaunogona kuita kubatsira kutonga zviratidzo zvako nekutsigira hupenyu hwako hwakanaka.
Kutarisirwa kwepande remuviri kunokosha zvikuru kune vanhu vane NSF. Chengeterai ganda renyu rakanyorova nemafuta kana makirisiri akapfava, asina kunhuhwirira. Isai mafuta panguva iyo ganda renyu richiri mvura mushure mekushambira kuti muchengetedze hunyoro. Dzivirai masobho akaomarara kana zvinhu zvingakonzera ganda renyu rakaoma kukuvadzwa.
Kuramba muri vakasununguka mukati memiganho yenyu kunokosha pakuchengetedza kufamba kwezvibatanidzwa:
Kudzorera marwadzo pamba kunogona kusanganisira mushonga wekurwadziwa unowanikwa pasina chinyorwa chechiremba, pamwe chete nezvinhu zvisiri mishonga senge kupisa kana kutonhora, kuveza zvinyoro nyoro, uye nzira dzekudzikamisa.
Kuvhara ganda renyu pakukuvara kunokosha sezvo ganda rakakuvadzwa neNSF ringapore zvishoma:
Kuchengetedza chikafu chakanaka uye kuramba muri vakanyorova kunogona kutsigira hutano hwenyu hwese uye zvinogona kubatsira mukuporesa kwenyu. Kana muri pakurapa kwekudirisa ropa, tevedzerai zvokudya zvenyu zvakanyatsonaka.
Funga nezvekubatanidzwa nemapoka ekutsigira kana kutaurirana nevamwe vane NSF. Kugovana zviitiko nezano rekutambura kunogona kubatsira zvikuru pakugadzirisa zvinhu zvepfungwa zvekurarama nechirwere ichi.
Kuagadzirira misangano yenyu yezvokurapa kunogona kubatsira kuve nechokwadi chekuti munowana zvakanakisa kubva panguva yenyu nevanachiremba. Kuva nemashoko akarongeka nemibvunzo yakajeka yakagadzirira kuchabatsira chiremba wenyu kupa hanya yakanakisa inogona kune NSF yenyu.
Usati kuenda kukurapa,unganidza mashoko akakosha ezvokurapa:
Chengeta dhayari yezviratidzo pakati pekuongororwa. Nyora chero kuchinja kweganda rako, matanho eruzha, kufamba, kana zvimwe zviratidzo. Ruzivo urwu runobatsira chiremba wako kutevera kufambira mberi kwechirwere chako uye kugadzirisa kurapwa zvakakodzera.
Gadzira rondedzero yemibvunzo yekubvunza timu yako yekurapa:
Funga nezvekutora nhengo yemhuri kana shamwari pakushanya kwakakosha. Vanogona kukubatsira kurangarira ruzivo rwakakurukurwa uye kupa rutsigiro rwemanzwiro panguva yekushanya kwakaoma kwemishonga.
Usanetseka kubvunza kuti ucheneswe kana usinganzwisisi chimwe chinhu chakatsanangurwa nachiremba wako. NSF chirwere chakaoma, uye zvakakosha kuti unzwe wakasununguka neruzivo nezano raunowana.
Nzira yakanakisa yekudzivirira NSF ndeyekudzivirira kuiswa kwakawanda kwezvinhu zvinonzi gadolinium-based contrast agents, kunyanya kana uine chirwere cheitsvo. Mirayiridzo yemazuva ano yezvokurapa yakaderedza zvikuru njodzi yeNSF kuburikidza nekutarisa kwakanyatsojeka uye tsika dzakachengeteka.
Kana uine chirwere cheitsvo, ita shuwa kuti vanachiremba vako vose vanoziva nezvemamiriro ako ezvinhu. Izvi zvinosanganisira chiremba wako mukuru, nyanzvi, uye chero chirongwa chaungave uine ongororo dze mifananidzo. Gara uchitaura nezvematambudziko ako eitsvo paunenge uchitarisa MRI kana mamwe maitiro anowedzera contrast.
Vanachiremba iye zvino vanotevera mirairo yakasimba yekushandisa gadolinium:
Kana uchida MRI uye uine chirwere cheitsvo, kurukura mamwe maitiro nechikurama chako. Dzimwe nguva non-contrast MRI inogona kupa ruzivo rwakakwana, kana mamwe maitiro ekufananidza senge ultrasound kana CT isina contrast inogona kukodzera.
Apo gadolinium exposure inodikanwa chaizvo kune munhu ane chirwere cheitsvo, mamwe ma centers ekurapa anopa mamwe ma dialysis sessions mushure mekubatsira kubvisa contrast nekukurumidza. Zvisinei, nzira iyi haina kuratidzwa kuti inodzivirira NSF zvachose.
kuchengetedza hutano hwakanaka hweitsvo kunogona kuderedza njodzi yako. Izvi zvinosanganisira kutonga mamiriro ezvinhu akadai sedayabetisi uye kuwedzera kweropa kunogona kuipa kushanda kweitsvo, kuramba wakanyorova, uye kudzivisa mishonga inogona kukuvadza itsvo dzako kana zvichibvira.
Kuita kweizvi zviyero zvekudzivirira kwakaderedza zvikuru nhamba yezviitiko zvitsva zveNSF mumakore achangopfuura. Kunyange mamiriro acho aiwanzoitika pakutanga kwa2000s, kuwedzera kwekuziva uye zvirongwa zvekutonga zvakaita kuti zvive zvisingawanzoitiki nhasi.
NSF chirwere chakakomba asi chisingawanzoitika chinotapura vanhu vane chirwere cheitsvo chakakomba avo vakatarisana nemamwe mishonga inoshandiswa mukuongororwa kwemuviri. Kunyange hazvo pasina mushonga iye zvino, kunzwisisa NSF kunogona kukubatsira kuita sarudzo dzakanaka pamusoro pekurapwa kwako uye kutonga chirwere ichi kana chakaitika.
Chinhu chakakosha chokurangarira ndechekuti NSF inogona kudzivirirwa zvikuru kuburikidza nekutarisa kwakanyatsojeka uye tsika dzakachengeteka dzekurapa. Mirayiridzo iripo ikozvino yakaderedza njodzi kune vanhu vane chirwere cheitsvo, uye vanachiremba vanoziva zvakanyanya nezvechirwere ichi kupfuura zvavaiziva kare.
Kana uine chirwere cheitsvo, gara uchizivisa vanachiremba vako usati waita chero ongororo dzekuongorora. Usarega kutya NSF kukuvadza kubva pakuwana kurapwa kwakakosha, asi ita shuwa kuti timu yako yekurapa inoziva nezvebasa reitsvo rako kuitira kuti vagone kuita sarudzo dzakachengeteka kwauri.
Kune avo vanorarama neNSF, tarisa pakushanda nevanachiremba vane ruzivo uye kuchengetedza hupenyu hwakanaka kuburikidza nekurapwa kwakakodzera uye kutarisira kwako pachako. Kunyange zvazvo chirwere ichi chinopa matambudziko makuru, vanhu vakawanda vane NSF vanowana nzira dzekugadzirisa uye kuramba vachirarama hupenyu hunoreva chimwe chinhu.
Ramba uchiziva nezvekuvandudzika kwitsva mune tsvakurudzo yeNSF uye kurapwa. Sezvo kunzwisisa kwedu kwechirwere ichi kuchiramba kuchikura, mikana mitsva yekurapa inogona kuwanika inogona kubatsira kuvandudza zvibereko zvevanhu vanotapurwa neNSF.
Kwete, NSF haitapuriri. Haugoni kuibata kubva kune mumwe munhu kana kuipamhidza kune vamwe vanhu. NSF inoitika semhedzisiro yemishonga inoshandiswa pakuongorora vanhu vane chirwere cheitsvo, kwete kubva kune chero chirwere chinopinda semhuka duku kana hutachiona.
NSF inogona kuitika kuvana, asi zvisingawanzoitika. Zviitiko zvakanyorwa zvakawanda zvaive kuvana vane chirwere chakakomba cheitsvo vakagamuchira gadolinium contrast yezvifananidzo zvemuviri. Kufungisisa kwakafanana kwakashandiswa kuvabereki kunoshandawo kuvana vane matambudziko etsvo.
Zviratidzo zveNSF kazhinji zvinoonekwa mukati memazuva kusvika kumwedzi mushure mekubatwa ne gadolinium, nezviitiko zvakawanda zvichiitika mukati memavhiki maviri kusvika matatu. Zvisinei, vamwe vanhu vakaratidza zviratidzo mavhiki kana kunyange kusvika gore mushure mekubatwa kwavo ne contrast. Nguva inogona kuchinja zvichienderana nebasa reitsvo rako nezvimwe zvinhu zvemunhu.
Kunyangwe vamwe vanhu vangave vakasangana nekuvandudzika kwezviratidzo zvavo, NSF haina kukura zvakanyanya pasina kurapwa. Mikana yakanakisa yekuvandudzika inobva pakudzosa basa reitsvo kuburikidza nekudyara kwetsvo kwakabudirira, kunyangwe ipapo, kupora kunogona kuva kwakanyanya uye kusakwana.
Kwete, mishonga yakasiyana-siyana yegadolinium-based contrast ine nhanho dzakasiyana dze njodzi. Mishonga ye linear, isinganyanyi kugadzikana, ine njodzi yakakura kupfuura mishonga ye macrocyclic, iyo yakagadzikana uye isingawanzo bvisa gadolinium yakasununguka. Nzvimbo zhinji dzekurapa ikozvino dzinoshandisa mishonga yakachengeteka, kunyanya muvarwere vane chirwere cheitsvo.