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Pemphigus

Pfupiso

Pemphigus chirwere che ganda rinonzwika zvishoma chinoita kuti ganda nemafomu emuromo zviome. Rudzi runowanzoitika ndiro pemphigus vulgaris, rine maronda anorwadza nemavanga paganda mumuromo.

Pemphigus foliaceus kazhinji haibati mafomu emuromo. Mavanga angatanga pachiso nepakati peganda, ozobuda pachipfuva nekumashure. Angave akasviba, achikwenya uye achirwadza.

Pemphigus boka remachirwere eganda anowanzoitika zvishoma anokonzera mavanga nemaronda paganda kana mafomu emuromo, akadai semumuromo kana pabonde. Inowanzoitika kune vanhu vakakwegura kana vakura.

Pemphigus iri nyore kudzora kana yakawanikwa ichirapwa pakutanga. Kazhinji inorapwa ne mishonga yaunotora kwenguva refu. Maronda angapora zvishoma nezvishoma kana kuti asina kupora. Iyo mamiriro ezvinhu anogona kuva ngozi kana maronda akazozara.

Zviratidzo

Pemphigus inokonzera makomba paganda nepanzvimbo dzakanyorova. Makomba anopwanya nyore nyore, achisiya maronda akavhurika. Maronda anogona kuzara utachiona uye kubuda mvura. Zviratidzo zvemarudzi maviri akakurumbira epemphigus zvinotevera: Pemphigus vulgaris. Rudzi urwu runowanzo tanga nemakomba mumuromo wozopinda paganda kana panzvimbo dzakanyorova dzepabonde. Kazhinji anorwadza asi haakwenyi. Makomba ari mumuromo kana muhuro anogona kuita kuti zviome kutaura, kunwa uye kudya. Pemphigus foliaceus. Rudzi urwu runokonzera makomba pachipfuva, kumusana nepamafudzi. Makomba anogona kukwenya kana kurwadza. Pemphigus foliaceus haikonzere makomba mumuromo. Pemphigus yakasiyana nebullous pemphigoid, iyo imhando imwe yekukomba kwe ganda inokanganisa vakuru vakwegura. Ona nyanzvi yehutano kana uine makomba asingarapiki mumuromo kana paganda kana panzvimbo dzakanyorova dzepabonde.

Nguva yekunoona chiremba

Ona chiremba kana uine maronda asingarapiki mumuromo kana paganda kana pamahwanda emuviri.

Zvinokonzera

Pemphigus chirwere chinokonzerwa nekuzvidzivirira kwemuviri, zvinoreva kuti masimba emuviri anorwisa masero ane hutano emuviri wako. Nepemphigus, masimba emuviri anorwisa masero ari muganda nemumamembranes emukati. Pemphigus haapfuudzirwe kubva kumunhu kuenda kune mumwe. Muzviitiko zvizhinji, hazvizivikanwe kuti chii chinokonzera chirwere ichi. Zvisingawanzoitika, chirwere ichi chinogona kuitika semhedzisiro yemishonga, senge penicillamine nemamwe mishonga yekudzikisa BP. Rudzi urwu rwechirwere runowanzopopera kana mushonga wacho wamira.

Zvinhu zvinokonzera njodzi

Ngozi yekubatwa nepemfhigus inowedzera kana uri pakati pemakore kana kupfuura. Zvirwere izvi zvakajairikawo kune vanhu vechitendero chechiJudha, vekuIndia, vekuEurope kumaodzanyemba kwakadziva kumabvazuva kana vekuMiddle East.

Matambudziko

Zvinogona kukonzerwa nepemphigus zvinosanganisira:

  • Kunetseka kweganda.
  • Hutachiona hunopararira muropa rako, hunonziwo sepsis. Rudzi urwu rwehutachiona runogona kuuraya.
  • Kutsvaga uye kuchinja kwemavara eganda mushure mekunge ganda rakabatwa rapora. Izvi zvinonzi postinflammatory hyperpigmentation kana ganda racho rakaita rima uye postinflammatory hypopigmentation kana ganda racho rapera ruvara. Vanhu vane ganda rebhuruu kana dema vane njodzi yakakura yekuchinja kwenguva refu kwemavara eganda.
  • Kushomeka kwezvokudya, nekuti maronda anorwadza mumuromo anoita kuti zviome kudya.
  • Kufa, zvishoma, kana marudzi akati wandei epemphigus asiri kurapwa.
Kuongorora

Munachiremba wenyu angatanga nekutaura nemi nezvematongerwo enyu emuviri nezviratidzo uye kuongorora nzvimbo yakabatwa. Kuwedzera, mungave nemiedzo, kusanganisira:

  • Biopsy. Biopsy ndiyo nzira yekubvisa sampuli yetsvina kuti iongororwe murabhoritari. Kuti uongorore pemphigus, chikamu chebhisita chinoshandiswa.
  • Kuongororwa kweropa. Chinangwa chimwe chezviyedzo izvi ndechekuwana uye kuziva maantibody ari muropa rwenyu anozivikanwa kuti aripo nepemphigus.

Munachiremba wenyu angakutumai kune nyanzvi yezvirwere zve ganda. Rudzi urwu rwenyanzvi inyanzvi yezvirwere zve ganda.

Kurapa

Kurapa pemphigus kunowanzo tanga ne mishonga inoderedza zviratidzo uye kudzivirira mavhisi matsva. Izvi zvinogona kusanganisira steroids nemishonga inorwisa sisitimu yemuviri. Kana zviratidzo zvako zvakakonzerwa nekushandisa mishonga chaiyo, kumisa mushonga iwoyo kungakwana kubvisa zviratidzo zvako.

Vanhu vamwe vangada kurapwa muchipatara kuti vagamuchire mvura, zvokudya kana kurapwa kwakasiyana.

Munachiremba wako angakurudzira mushonga mumwe kana kupfuura unotevera. Kusarudzwa kwemishonga kunotsamira pane rudzi rwepemphigus raunaro, kuti zviratidzo zvako zvakakomba sei uye kana uine zvimwe zvirwere.

  • Corticosteroids. Kune vanhu vane chirwere chinenge chisinganyanyi kukomba, kirimu ye corticosteroid kana jekiseni zvinogona kukwana kudzora. Kune vamwe, kurapwa kukuru mushonga we corticosteroid unotorwa nemuromo, sekupisa mapiritsi e prednisone.

Kushandisa corticosteroids kwenguva yakareba kana muhuwandu hukuru kunogona kukonzera matambudziko akakomba. Izvi zvinosanganisira chirwere cheshuga, kurasikirwa nemapfupa, njodzi yakawedzera yekutapukirwa, maronda emudumbu uye kuchinja kwemafuta emuviri. Kuchinja uku kwemafuta kunogona kutungamira kumeso akapoteredzwa, anonziwo moon face. Kuti udzivise matambudziko aya, steroids inogona kushandiswa chete kwenguva pfupi kudzora kuzvimba. Uye mishonga yakasiyana inorwisa sisitimu yemuviri inogona kushandiswa kwenguva refu kudzora chirwere.

  • Mishonga inorwisa sisitimu yemuviri. Mishonga yakati wandei inogona kumisa sisitimu yako yemuviri kuti isarwisa tishu dzakakodzera. Mienzaniso ndeye azathioprine (Imuran, Azasan), mycophenolate (Cellcept) uye cyclophosphamide. Izvi zvinogonawo kuva nematambudziko akakomba, kusanganisira njodzi yakawedzera yekutapukirwa.
  • Mishonga yakasiyana. Kana mishonga yekutanga isingakubatsiri, munachiremba wako angakurudzira mushonga mumwe, sekudapone, intravenous immunoglobulin kana rituximab-pvvr (Ruxience). Ungadawo maantibayotiki ekurapa hutachiona.

Corticosteroids. Kune vanhu vane chirwere chinenge chisinganyanyi kukomba, kirimu ye corticosteroid kana jekiseni zvinogona kukwana kudzora. Kune vamwe, kurapwa kukuru mushonga we corticosteroid unotorwa nemuromo, sekupisa mapiritsi e prednisone.

Kushandisa corticosteroids kwenguva yakareba kana muhuwandu hukuru kunogona kukonzera matambudziko akakomba. Izvi zvinosanganisira chirwere cheshuga, kurasikirwa nemapfupa, njodzi yakawedzera yekutapukirwa, maronda emudumbu uye kuchinja kwemafuta emuviri. Kuchinja uku kwemafuta kunogona kutungamira kumeso akapoteredzwa, anonziwo moon face. Kuti udzivise matambudziko aya, steroids inogona kushandiswa chete kwenguva pfupi kudzora kuzvimba. Uye mishonga yakasiyana inorwisa sisitimu yemuviri inogona kushandiswa kwenguva refu kudzora chirwere.

Vanhu vakawanda vane pemphigus vanorapa, kunyanya kana kurapwa kuchitangwa pakutanga. Asi zvinogona kutora makore uye zvinoda kutora mushonga kwenguva yakareba.

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