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Gomarara Rewilms

Pfupiso

Kenza yeWilms rudzi rwakanyanya kuwanda rekenza yeitsvo muvana. Itsvo chikamu chetsvina yekubuda kwemvura mumuviri, inobvisa tsvina mumuviri kuburikidza newee. Tsina yekubuda kwemvura inosanganisirawo ureters, bhara, neurethra.\n\nKenza yeWilms kenza isingawanzoitika yeitsvo inonyanya kukanganisa vana. Inozivikanwawo se nephroblastoma, ndiyo kenza inonyanya kuwanda yeitsvo muvana. Kenza yeWilms inonyanya kukanganisa vana vane makore matatu kusvika mana. Inova shoma zvikuru mushure memakore mashanu, asi inogona kukanganisa vana vakura kunyange vakuru.\n\nKenza yeWilms inonyanya kuitika muitsvo rimwe chete. Asi dzimwe nguva inogona kunge iri muitsvo ese panguva imwe chete.\n\nKufamba kwenguva, kufambira mberi mukuongororwa nekurapwa kwekenza yeWilms kwakavandudza zvikuru mamiriro evana vane chirwere ichi. Nerapwo, tarisiro yevanakomana vakawanda vane kenza yeWilms yakanaka.

Zviratidzo

Zviratidzo zveWilms tumor zvakasiyana-siyana. Vamwe vana havaoneki kuva nezviratidzo. Asi vamwe vane Wilms tumor vane chimwe chezviratidzo izvi kana kupfuura chimwe: Boka mudumbu rinogona kunzwika. Kuwedzera mudumbu. Kurwadziwa mudumbu. Zvimwe zviratidzo zvinogona kusanganisira: Fivha. Ropa mumukaka. Huwandu hwakaderera hwemasero matsvuku eropa, anozivikanwawo se anemia. Kufuta kweropa. Rongai musangano nehutano hwemwana wenyu kana mukaona zviratidzo zvinokunetsa. Wilms tumor yakawanda. Saka zvinogona kunge chimwe chinhu chiri kukonzera zviratidzo. Asi zvakakosha kuongorora chero zvinokunetsa.

Nguva yekunoona chiremba

Enda kuona chiremba wehutano hwemwana wako kana ukaona zviratidzo zvinokunetsa. Utachiona hweWilms hunyanya kushayikwa. Saka zvinogoneka kuti chimwe chinhu chiri kukonzera zviratidzo. Asi zvakakosha kuongorora chero hanya.

Zvinokonzera

Hazvina kujeka kuti chii chinokonzera Wilms tumor.

Kenza inotanga kana masero akaita shanduko muDNA rawo. DNA remasero rine mirairo inoudza masero kuti aite sei. Shanduko idzodzo dzinoudza masero kuti akure nekukura nekukurumidza. Masero ekenza anorarama nepo masero ane hutano afa sezvikamu zvehupenyu hwavo hwakajairwa. NeWilms tumor, shanduko dzinokonzera masero akawanda muchiuno anoumba tumor.

Zvisingawanzoitiki, shanduko dzeDNA dzakapfuudzwa kubva kuvabereki kuvana dzinogona kuwedzera njodzi yeWilms tumor.

Zvinhu zvinokonzera njodzi

Zvinhu zvinogona kuwedzera njodzi yeWilms tumor zvinosanganisira:

  • Kuva mutema. KuNorth America neEurope, vana vatema vane njodzi yakakwirira zvishoma yekuwana Wilms tumor kupfuura vana vemimwe mitambo. Vana vekuAsia-America vanoita sekunge vane njodzi yakaderera kupfuura vana vemimwe mitambo.
  • Kuva ne nhoroondo yemhuri yeWilms tumor. Kuva nemumwe munhu mumhuri ane Wilms tumor kuwedzera njodzi yekuwana chirwere.

Wilms tumor inoitika kazhinji muvana vane mamiriro ezvinhu akati akaberekwa, anosanganisira:

  • Aniridia. Mu aniridia (an-ih-RID-e-uh), chikamu chine ruvara retsoka, chinozivikanwa se iris, chinoumbwa zvishoma kana kuti zvachose.
  • Hemihypertrophy. Hemihypertrophy (hem-e-hi-PUR-truh-fee) zvinoreva kuti divi rimwe remuviri kana chikamu chemuviri chikuru kupfuura divi rimwe.

Wilms tumor inogona kuitika sechikamu chema syndromes asingawanzoitika, anosanganisira:

  • WAGR syndrome. Iyi syndrome inosanganisira Wilms tumor, aniridia, matambudziko emuviri wepabonde neye urinary system, uye kusakwanisa kufunga.
  • Denys-Drash syndrome. Iyi syndrome inosanganisira Wilms tumor, chirwere cheitsvo uye pseudohermaphroditism yevakadzi (soo-do-her-MAF-roe-dit-iz-um). Mu pseudohermaphroditism yevakadzi, zviberekero zvemucheche hazvina kujeka kuti zvemurume.
  • Beckwith-Wiedemann syndrome. Vana vane iyi syndrome vanowanzova vakakura kupfuura zvakajairwa, zvinozivikanwa se macrosomia. Iyi syndrome inogona kukonzera kuti nhengo dziri mudumbu dzipinde muchikamu che umbilical cord, rurimi rukuru, nhengo huru dzemukati uye nzeve dzakagadzirwa zvisina kujairika.
Kudzivirira

Kenza reWilms harigone kudzivirirwa. Kana mwana akaita chero chimwe chezvipatadzo zvinoita kuti njodzi yekenza reWilms iwedzere, mushandi wehutano angakurudzira kuita ultrasound yeitsvo dzimwe nguva kuti aone kana paine chinhu chisingawanzoitika muitsvo. Kunyange zvazvo kuongororwa uku kusina kukwanisa kudzivirira kenza reWilms, kunogona kubatsira kuwana chirwere ichi pakutanga.

Kuongorora

Dzimwe nguva muchina we3D unoshandiswa kugadzira modheli chaiyo yemuviri wemurwere kuti ubatsire kuronga mabasa akaoma eWilms tumor.

Kuti aone chirwere cheWilms tumor, chiremba angatora nhoroondo yemhuri oita zvinotevera:

  • Kuongororwa kwemuviri. Chiremba acharamba achitsvaga zviratidzo zvinogona kuva zveWilms tumor.
  • Kuongororwa kweropa nemukaka. Aya maekisi emurayiridzo anoratidza kuti itsvo dziri kushanda zvakanaka sei.
  • Kuongororwa kwemafirimu. Kuongororwa kunogadzira mifananidzo yetsvo kunobatsira kuwana kana mwana ane tumor yetsvo. Kuongororwa kwemafirimu kunogona kusanganisira ultrasound, CT scans kana MRI uye X-rays yechipfuva.

Pashure pokuwana Wilms tumor, timu yekurapa inogona kukurudzira kuongororwa kwakawanda kuti ione kana kenza yakapararira. Izvi zvinonzi nhanho yekenza. X-ray yechipfuva kana CT scan yechipfuva uye bone scan inogona kuratidza kana kenza yakapararira kubva kutsvo.

Nhanho yekenza inobatsira pakusarudza kurapwa. MuUnited States, nhanho dzeWilms tumor ndidzo:

  • Nhanho 1. Kenza inowanikwa chete mumutsvo mumwe. Kuvhiya kunogona kubvisa zvese.
  • Nhanho 2. Kenza yakapararira kunze kwemutsvo, sekufamba kune mafuta ari pedyo kana midziyero yeropa. Asi kuvhiya kunogona kubvisa zvese.
  • Nhanho 3. Kenza yakapararira kunze kwemitsvo kuenda kune zvikamu zvidiki zviri pedyo zvinorwisa hutachiona, zvinozivikanwawo se lymph nodes. Inogonawo kupararira kune dzimwe nzvimbo dziri mudumbu. Masero ekenza anogona kupararira mudumbu usati wavhiyiwa kana panguva yekuvhiya, kana kuvhiya kungakwanisi kubvisa kenza yese.
  • Nhanho 4. Kenza yakapararira kunze kwemutsvo kuenda kune dzimwe nzvimbo mumuviri, dzakadai semapapu, chiropa, mapfupa kana uropi.
  • Nhanho 5. Masero ekenza anowanikwa mutsvo yese. Tumor mumutsvo wega wega inoratidzwa pachayo.
Kurapa

Kurapa chirwere cheWilms kunowanzo sanganisira kuvhiya ne chemotherapy. Dzimwe nguva kunosanganisira kurapwa kwemwaranzi. Kurapa kunotsamira pane nhanho yekenza. Nekuti rudzi urwu rwekenza rwakasiyana, nzvimbo yekenza ye vana yakarapira rudzi urwu rwekenza ingave sarudzo yakanaka.

Kurapa kweWilms tumor kunogona kutanga nekushanda kuvhiya kubvisa chikamu chose kana chikamu cheitsvo. Kuvhiya kunosimbisawo chirwere. Tishu inobviswa panguva yekuvhiya inotumirwa ku laboratori kuti inzwisise kana iri kenza uye rudzi rwekensa ruri mumusoro.

Kuvhiya kweWilms tumor kunogona kusanganisira:

  • Kubvisa chikamu cheitsvo. Zvinozivikanwa se partial nephrectomy, izvi zvinosanganisira kubvisa tumor nechikamu chidiki cheitsvo chakakomberedza. Izvi zvinogona kuitwa kana kenza iri diki kwazvo kana mwana ane itsvo imwe chete inoshanda.
  • Kubvisa itsvo netishu yakakomberedza. Zvinozivikanwa se radical nephrectomy, rudzi urwu rwekushanda kuvhiya kunosanganisirawo kubvisa lymph nodes iri pedyo, chikamu che ureter uye dzimwe nguva adrenal gland. Itsvo yakasara inogona kutora basa reitsvo mbiri.
  • Kubvisa zvese kana chikamu cheitsvo mbiri. Kana kenza ichikanganisa itsvo mbiri, kuvhiya kunosanganisira kubvisa kenza yakawanda sezvinobvira kubva kuzviviri. Dzimwe nguva, izvi zvinoreva kubvisa itsvo mbiri. Mwana aizoda dialysis yeitsvo kana kupanwa kwetsvo.

Chemotherapy inoshandisa mishonga ine simba kuuraya masero ekenza mumuviri wose. Kurapa kweWilms tumor kunowanzo sanganisira kushandisa mishonga yakawanda kuuraya masero ekenza. Mushonga unopiwa kuburikidza ne tsinga.

Migumisiro ye chemotherapy inotsamira pamishonga inoshandiswa. Migumisiro yakajairika inosanganisira kusvotwa, kurutsa, kurasikirwa nechido chekudya, kurasikirwa nevhudzi uye njodzi yakakwira yekusangana nehutachiona. Bvunza timu yehutano hwemwana wako kuti migumisiro ipi inogona kuitika panguva yekurapa. Bvunza kana paine matambudziko emangwana anogona kuitika semugumisiro wekurapa.

Kana ikapiwa usati wavhiyiwa, chemotherapy inogona kudzikisa tumors uye kuita kuti zvive nyore kubvisa. Mushure mekuvhiya, inogona kuuraya masero ekensa ari mumuviri. Chemotherapy inogona kunge iri sarudzo ye vana vane kenza yakareba kwazvo kuti ibviswe zvizere nekushanda kuvhiya.

Kune vana vane kenza muitsvo mbiri, chemotherapy inopiwa usati wavhiyiwa. Izvi zvinogona kuita kuti zvive nyore kuti itsvo imwe igone kuponeswa.

Vana vamwe vangave nerapira remwaranzi. Kurapwa kwemwaranzi kunoshandisa ma beam ane simba rakakura kuuraya masero ekensa. Simba rinogona kubva ku X-rays, protons nezvimwe zvinhu.

Panguva yekurapa kwemwaranzi, mwana anoiswa patafura. Muchina mukuru unofamba-famba pamwana, uchitarisa ma beam esimba pakenza. Migumisiro inogona kuitika inosanganisira kusvotwa, manyoka, kuneta uye kutsamwa kwe ganda senge sunburn.

Vana vamwe vachava nerapira remwaranzi mushure mekuvhiya kuuraya masero ekensa ese aripo. Inogona kushandiswawo kudzora kenza yakapararira kune dzimwe nzvimbo dzemuviri. Bvunza kana paine matambudziko emangwana anogona kuitika semugumisiro wekurapa kwemwaranzi.

Heano mamwe mazano ekukubatsira iwe kutungamira mhuri yako mukurapa kenza.

Kana mwana wako ane magwaro emuviri kana kugara muchipatara:

  • Garai nemwana wenyu panguva yekuedzwa kana kurapwa, kana zvichibvira. Rondedzera zvichaitika uchishandisa mazwi anomuzivana.
  • Sanganisira nguva yekutamba mune purogiramu yemwana wako. Zvipatara zvikuru kazhinji zvine kamuri yekutambira vana vari kurapwa. Kazhinji vashandi vekamuri yekutambira vane kudzidziswa mukukura kwemwana, zororo, psychology kana basa rezvemagariro. Kune vana vanofanirwa kugara mumakamuri avo, nyanzvi yehupenyu hwemwana kana therapist wezororo inogona kushanyira.
  • Kumbira rubatsiro kubva kuvanhu vekiriniki kana vechipatara. Tsvaga masangano evabereki vevana vane kenza. Vabereki vakapfuura izvi vanogona kupa rutsigiro, tariro uye mazano akanaka. Bvunza timu yehutano hwemwana wako nezvemapoka ekutsigira munzvimbo.

Mushure mekubva muchipatara:

  • Tarisa nhanho yesimba remwana wako kunze kwechipatara. Kana mwana wako achinzwa zvakanaka zvakakwana, kurudzira zvinyoro nyoro kutora chikamu mumabasa akajairika. Uyewo ita nguva yekuzorora, kunyanya mushure me chemotherapy kana mwaranzi.
  • Chengeta rekodhi yezuva nezuva yemwana wako tembiricha yemuviri, nhanho yesimba, hope, mishonga inoshandiswa uye migumisiro. Govera ruzivo urwu nemupi wehutano hwemwana wako.
  • Ronga kudya kwakajairika kunze kwekunge mupi wemwana wako akurudzira zvimwe. Ita zvokudya zvaunofarira. Chemotherapy inogona kukanganisa kuda kudya. Wedzera mvura.
  • Kurudzira kuchengetedza muromo. Kuchadzika muromo kunogona kubatsira pakukuvadzwa kana nzvimbo dzakabuda ropa. Shandisa lip balm kunyaradza miromo yakapwanya. Zvakanaka, mwana wako anofanira kunge aida kurapwa kwemeno usati watanga kurapwa. Zvadaro tarisa nemupi wemwana wako usati waronga kushanya kudentist.
  • Tarisa nemupi usati wawana jekiseni. Kurapa kenza kunokanganisa sisitimu yekudzivirira muviri.
  • Taura nevamwe vana vako nezvechirwere. Vaudza nezvechinja zvavanogona kuona mumwana ane kenza, senge kurasikirwa nevhudzi uye simba shoma. Teerera kuzvinetso zvavo.
Kuzvitarisira

'Heano mamwe mazano anogona kukubatsira kutungamira mhuri yako pakuporeswa kenza. Muchipatara Kana mwana wako aine magwaro emuviri kana kugara muchipatara: Uyai netoy kana bhuku raanofarira kuenda kunzvimbo yekurapa kana kuchipatara, kuti mwana wako agare akabatikana achimirira. Garai nemwana wenyu panguva yekuongororwa kana kurapwa, kana zvichibvira. Rondedzerai zvichaitika uchishandisa mazwi anoziva mwana. Ita kuti pave nenguva yekutamba muhurongwa hwemwana wako. Zvipatara zvikuru kazhinji zvine kamuri yekutambira vana vari kurapwa. Kazhinji vashandi vekamuri yekutambira vanodzidziswa mukukura kwemwana, zvekuvaraidza, zvepfungwa kana basa rezvemagariro. Kune vana vanofanirwa kugara mumakamuri avo, nyanzvi yehupenyu hwemwana kana munyanzvi wekurapa vanogona kushanyira. Kumbirai rubatsiro kubva kuvanoshanda muchipatara kana mukiriniki. Tsvakai masangano evabereki vane vana vane kenza. Vabereki vakapfuura izvi vanogona kupa rutsigiro, tariro uye mazano akanaka. Bvunzai timu yekuchengetedza utano yemwana wenyu nezvemapoka ekutsigira munzvimbo. Pamba Mushure mekubva kuchipatara: Tarisa simba remwana wako kunze kwechipatara. Kana mwana wako achinzwa zvakanaka, kurudzirai zvinyoro nyoro kutora chikamu mumabasa emazuva ose. Uyewo ita nguva yekuzorora, kunyanya mushure me chemotherapy kana kurapwa nerangi. Chengetedza rekodhi yezuva nezuva yemwana wako tembiricha yemuviri, simba, hope, mishonga inoshandiswa uye zvinokonzerwa. Govera ruzivo urwu neanopereka utano hwemwana wako. Rongai kudya kwakajairwa kunze kwekunge anopereka utano hwemwana wako akurudzira zvimwe. Gadzirai zvokudya zvaanofarira. Chemotherapy inogona kukanganisa kuda kudya. Wedzerai mvura. Kurudzirai kuchengetedza muromo. Kusuka muromo kunogona kubatsira pakukuvara kana nzvimbo dzinovera ropa. Shandisa lip balm kunyaradza miromo yakapwanya. Zvakanaka, mwana wako anofanira kunge aine kurapwa kwemeno kunodiwa usati watanga kurapwa. Zvadaro tarisa neanopereka utano hwemwana wako usati waronga kushanya kudentist. Tarisa neanopereka utano usati waita jekiseni. Kurapwa kenza kunokanganisa sisitimu yekudzivirira muviri. Taura nevamwe vana vako nezvechirwere ichi. Vaudza nezvechinja zvavanogona kuona mumwana ane kenza, sekurasikirwa nevhudzi uye simba shoma. Teerera kuzvinetso zvavo.'

Kugadzirira musangano wako

'Kana mwana wenyu akaonekwa aine Wilms tumor, munogona kutumirwa kune vanachiremba vane hunyanzvi. Uyu angava chiremba anorapira kenza, anonzi oncologist, kana kuti chiremba anoita mabasa okuvhiya echiropa, anonzi urologist. Zvamunogona kuita Kuti mugadzirire musangano: Gadzirai rondedzero yemishonga yose, mavhitaminzi, zvinomera, mafuta nezvimwe zvinowedzerwa zviri kudyiwa nemwana wenyu, kusanganisira zviyero. Kumbirai hama kana shamwari kuti iuyewo nemi kuti ikubatsire kurangarira mashoko aunowana panguva yemusangano. Nyora rondedzero yemibvunzo yekubvunza mutariri wehutano hwemwana wenyu. Kune Wilms tumor, mimwe mibvunzo yekubvunza inosanganisira: Mwana wangu anoda bvunzo dzipi? Mwana wangu ari padanho ripi rekukura kwenzara? Kurapwa kwei kupi kuripo, uye ndechipi raunokurudzira? Mhando dzipi dzemaitiro ekukanganisa aya kurapwa anogona kuita? Ndichada here kudzora mabasa emwana wangu kana kuchinja kudya panguva yekurapwa? Tarisiro yemwana wangu ndeyei? Iko mukana wei wekuti kenza idzokere? Kune mabhurocha kana mamwe mapepa andinogona kuwana here? Websites dzipi dzaunokurudzira? Usanetseka kubvunza mimwe mibvunzo yaunayo. Zvinotarisirwa kubva kuchiremba wako Mutariri wehutano hwemwana wenyu angakubvunza mibvunzo yakadai se: Wakaziva rini zviratidzo zvemwana wako? Pane nhoroondo yekenza, kusanganisira kenza yehudiki, mumhuri yenyu here? Mwana wenyu ane nhoroondo yemhuri yezvikanganiso zvekuzvarwa, kunyanya zvepabonde kana turakiti yekumisa mvura here?'

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