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Galsulfase (inowaniswa muchipatara)

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Mhando dzinowanikwa

Naglazyme

Nezve mushonga uyu

Jekiseni yeGalsulfase inoshandiswa kubata zviratidzo zvechirwere chinogara kuri nhaka chinonzi mucopolysaccharidosis (MPS VI) chirwere kana kuti Maroteaux-Lamy syndrome. Mushonga uyu unovandudza kugona kufamba nekukwira matanho muvarwere vasina enzyme chaiyo inonzi N-acetylgalactosamine 4-sulfatase mumuviri. Mushonga uyu unofanirwa kupiwa chete kana uri pasi pekutarisirwa kwakananga kwemudokotera. Chigadzirwa ichi chinowanikwa mumhando dzinotevera dzekuyerwa:

Usati washandisa mushonga uyu

Pakusarudza kushandisa mushonga, njodzi dzekutorwa kwemushonga dzinofanira kuyerwa nemabhenefiti awo. Iyi sarudzo ichaitwa newe nechikamu chako. Kune mushonga uyu, zvinotevera zvinofanira kufungwa: Udza chiremba wako kana wakambonzwa chero mhinduro isingawanzoitika kana chirwere cheallergy kumushonga uyu kana mimwe mishonga. Udzawo nyanzvi yako yehutano kana uine mamwe marudzi eallergies, akadai sekudya, dyes, preservatives, kana mhuka. Kune zvigadzirwa zvisingadi kuraira kwechiremba, verenga zvinyorwa zvepakiti kana zvinosanganiswa zvakanaka. Kudzidza kwakakodzera kwakaitwa kusvika pari zvino hakuisimbise matambudziko chaiwo ekuvana aizoita kuti kushandiswa kwe galsulfase injection kuvana vane makore mashanu ekuberekwa nekupfuura kuve kwakaoma. Kwakasimbiswa kuchengetedzeka nekushanda kwakanaka. Kudzidza kwakakodzera hakuisimbisi hukama hwezera nemigumisiro ye galsulfase injection muvanhu vakwegura. Kuchengetedzeka nekushanda kwakanaka hazvina kusimbiswa. Hapana zvidzidzo zvakakwana zvevakadzi zvekutsvaga njodzi yemwana pakuishandisa mushonga uyu panguva yekuyamwisa. Yera mabhenefiti anogona kuitika pamwe nenjodzi dzinogona kuitika usati watora mushonga uyu panguva yekuyamwisa. Kunyangwe mimwe mishonga isingafanirwe kushandiswa pamwe chete, mune mamwe mamiriro mishonga miviri yakasiyana inogona kushandiswa pamwe chete kunyangwe paine kuwirirana kunogona kuitika. Mune izvi, chiremba wako angada kuchinja huwandu, kana kuti dzimwe nhau dzinogona kudiwa. Udza nyanzvi yako yehutano kana uri kutora chero mushonga wekuraira kana usina kuraira (over-the-counter [OTC]). Mimwe mishonga haifanirwe kushandiswa panguva yekudya kana pedyo nenguva yekudya kana kudya marudzi akati e chikafu sezvo kuwirirana kunogona kuitika. Kushandisa doro kana fodya nemamwe mishonga kunogona zvakare kukonzera kuwirirana. Kurukura nenyanzvi yako yehutano kushandiswa kwemushonga wako nechikafu, doro, kana fodya. Kuvapo kwemamwe matambudziko ehutano kunogona kukanganisa kushandiswa kwemushonga uyu. Ita shuwa kuti unoudza chiremba wako kana uine mamwe matambudziko ehutano, kunyanya:

Mashandisirwo aungaita mushonga uyu

Mufambiri kana mumwe munyanzvi wehutano akarovedzwa achakupa iwe kana mwana wako mushonga uyu muchipatara. Mushonga uyu unoiswa ne catheter ye IV inoiswa mumutsinga yako. Mushonga uyu unofanirwa kuiswa zvishoma nezvishoma, saka IV icharamba iripo kwemaawa anopfuura 4. Kazhinji unoiswa kamwe chete pavhiki. Iwe kana mwana wako munogonawo kugamuchira mishonga (semuenzaniso, mushonga wehosha, mushonga wefivha) maminetsi makumi matatu kusvika makumi matanhatu usati watanga kurapwa nemushonga uyu.

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