Livmarli
Maralixibat inoshandiswa kurapa manyoka anokonzerwa necholestatic (kutsamwa kwe ganda) muvarwere vane Alagille syndrome (ALGS) uye progressive familial intrahepatic cholestasis (PFIC). Mushonga uyu unowanikwa chete kana uine chinyorwa chekubvumidzwa nachiremba. Chigadzirwa ichi chinowanikwa mumhando dzinotevera dzekuyerwa:
Pakusarudza kushandisa mushonga, njodzi dzekutora mushonga unofanirwa kuyerwa nemabhenefiti awo. Iyi sarudzo iwe nechikamu chako muchaita. Kune mushonga uyu, zvinotevera zvinofanirwa kufungwa: Udza chiremba wako kana wakambonzwa chero mhinduro isingawanzoitika kana chirwere cheallergy kumushonga uyu kana mimwe mishonga. Uyewo udza nyanzvi yako yehutano kana uine mamwe marudzi eallergies, akadai sekudya, dyes, preservatives, kana mhuka. Kune zvigadzirwa zvisingadi kuraira, verenga zvinyorwa zvepakeji kana zvinosanganiswa zvakanaka. Ongororo dzakakodzera hadzina kuitwa pane hukama hwezera nemigumisiro yemaralixibat ekurapa kukwenya kwepande neAlagille syndrome (ALGS) muvana vane makore asingasviki mwedzi mitatu uye kurapa kukwenya kwepande neprogressive familial intrahepatic cholestasis (PFIC) muvana vane makore asingasviki mwedzi gumi nembiri. Kwakachengeteka uye kushanda kwakanaka hazvina kusimbiswa. Ongororo dzakakodzera hadzina kuitwa pane hukama hwezera nemigumisiro yemaralixibat muvarwere vakwegura. Kwakachengeteka uye kushanda kwakanaka hazvina kusimbiswa. Hapana ongororo dzakakwana muvakadzi dzekuona njodzi yemwana panguva yekupa amai mukaka. Yengetera mabhenefiti anogona kuitika pamwe nenjodzi dzinogona kuitika usati watora mushonga uyu panguva yekupa amai mukaka. Kunyangwe mimwe mishonga isingafanirwe kushandiswa pamwe chete, mune mamwe mamiriro mishonga miviri yakasiyana inogona kushandiswa pamwe chete kunyangwe paine kuwirirana kunogona kuitika. Mumativi aya, chiremba wako angada kuchinja dose, kana mamwe matanho angave akakosha. Udza nyanzvi yako yehutano kana uri kutora chero mushonga wekuraira kana usingadi kuraira (over-the-counter [OTC]). Mimwe mishonga haifaniri kushandiswa panguva kana pedyo nenguva yekudya kana kudya marudzi akati wandei ezvokudya sezvo kuwirirana kunogona kuitika. Kushandisa doro kana fodya nemamwe mishonga kunogona zvakare kukonzera kuwirirana kuitika. Kurukura nehutano hwako hwenyanzvi kushandiswa kwemushonga wako nezvokudya, doro, kana fodya. Kuvapo kwemamwe matambudziko ehutano kunogona kukanganisa kushandiswa kwemushonga uyu. Ita shuwa kuti unoudza chiremba wako kana uine mamwe matambudziko ehutano, kunyanya:
Tora mushonga uyu chaizvoizvo sezvakarayirwa nachiremba wako. Usatore zvakawanda, usatore kazhinji, uye usatore kwenguva yakareba kupfuura zvakarayirwa nachiremba wako. Mushonga uyu unouya neGwara reMishonga nemirayiridzo yevagoni. Verenga utevedzere mirayiridzo iyi zvakanyatsonaka. Bvunza chiremba wako kana uine mibvunzo ipi neipi. Tora mushonga uyu kwemaminitsi anopfuura makumi matatu usati watanga kudya kwemangwanani. Tarisa mvura iri mubhodhoro. Inofanira kunge yakajeka kusvika pakunge yakajeka uye isina ruvara kusvika kune yero yakapfava. Usashandise mushonga kana mvura yakachinja ruvara, kana iine zvinhu zviri mukati. Kushandisa: Tora mushonga uyu kwemaawa anopfuura mana usati washandisa kana maawa mana mushure mekushandisa bile acid sequestrants (semuenzaniso, cholestyramine, colesevelam, colestipol). Doses yemushonga uyu ichava yakasiyana kune varwere vakasiyana. Tevedzera mirairo yechiremba wako kana mirairo iri parinenge. Ruzivo runotevera rinosanganisira chete avhareji doses yemushonga uyu. Kana dose yako yakasiyana, usachinje kunze kwekunge chiremba wako akakuudza kudaro. Huwandu hwemushonga waunotora hunotsamira pakusimba kwemushonga. Uyewo, nhamba ye doses yaunotora zuva rega rega, nguva inobvumirwa pakati pe doses, uye nguva yaunotora mushonga zvinoenderana nedambudziko rehutano rauri kushandisa mushonga. Kana ukasapotsa dose yemushonga uyu, itora nekukurumidza sezvinobvira. Zvisinei, kana iri nguva yekutora dose yako inotevera, siya dose yakarasika uye dzokera kune yako dosing schedule. Usatore doses kaviri. Kamwe chete pazuva dosing: Kana dose ikarasika nemaawa gumi nemaviri kana zvishoma, itora nekukurumidza sezvinobvira, wobva wadzoka kune yako schedule. Kana dose ikarasika kwemaawa anopfuura gumi nemaviri, usatore dose yakawedzerwa. Tora dose inotevera panguva yakarongwa. Kaviri pazuva dosing: Kana dose ikarasika nemaawa matanhatu kana zvishoma, itora nekukurumidza sezvinobvira, wobva wadzoka kune yako schedule. Kana dose ikarasika kwemaawa anopfuura matanhatu, usatore dose yakawedzerwa. Tora dose inotevera panguva yakarongwa. Chengetedza kure nevana. Usachengetse mushonga wakapfuura nguva kana mushonga usingachadiwi. Bvunza nyanzvi yehutano maitiro aunofanira kubvisa mishonga ipi neipi yausashandisi. Chengetedza mushonga mubhodhoro rakavharwa pane tembiricha yekamuri, kure nekupisa, hunyoro, uye chiedza chakananga. Chengetedza kuti urege kuomarara. Chengetedza mushonga uyu necap iri pabhodhoro. Rasa mishonga ipi neipi isina kushandiswa mazuva zana mushure mekuvhura bhodhoro.