Elelyso
Jekiseni yeTaliglucerase alfa inoshandiswa kurapa kwenguva refu chirwere cheGaucher chemarudzi 1. Chirwere ichi chinokonzerwa nekushaikwa kwe enzyme chaiyo mumuviri inonzi glucocerebrosidase. Enzyme iyi inodiwa kuti muviri ushandise mafuta zvakanaka, uye mafuta achaunganidzwa munzvimbo dzakati dzomuviri kana enzyme iyi isinapo. Taliglucerase alfa inotsiva enzyme isingawanikwe kubatsira muviri kushandisa mafuta. Mushonga uyu unofanirwa kupihwa chete kana uri pasi pekutarisirwa kwemuchiremba. Chigadzirwa ichi chinowanikwa mumafomu anotevera ekurapa:
Pakusarudza kushandisa mushonga, ngozi dzokutora mushonga iyeye dzinofanira kuyeranidzwa nezvakanaka zvichaita. Iyi sarudzo iwe nesachiremba wenyu muchaita. Kune mushonga uyu, zvinotevera zvinofanira kufungwa: Udza chiremba wako kana wakambonzwa chero mhinduro isingawanzoitika kana chirwere cheallergy kumushonga uyu kana mimwe mishonga. Uyewo udza nyanzvi yako yehutano kana uine mamwe marudzi eallergies, akadai sekudya, dyes, preservatives, kana mhuka. Kune zvigadzirwa zvisingadi kuraira, verenga zvinyorwa zvepakeji kana zvinosanganiswa zvakanaka. Ongororo dzakakodzera hadzina kuitwa pane hukama hwezera nemigumisiro yekuisa taliglucerase alfa muvana vane makore asingasviki 4. Kwakachengeteka uye kushanda hazvina kusimbiswa. Kunyange zvazvo ongororo dzakakodzera pane hukama hwezera nemigumisiro yekuisa taliglucerase alfa hazvina kuitwa muvanhu vakwegura, hapana matambudziko chaiwo evakwegura akanyorwa kusvika pari zvino. Hapana ongororo dzakakwana muvakadzi dzekuona ngozi yemwana pakuita mushonga uyu panguva yekuyamwisa. Yera mabhenefiti anogona kuitika pamwe nengozi dzinogona kuitika usati watora mushonga uyu panguva yekuyamwisa. Kunyange zvazvo mimwe mishonga isingafaniri kushandiswa pamwe chete, mune mamwe mamiriro mishonga miviri yakasiyana inogona kushandiswa pamwe chete kunyange kana kuwirirana kungavepo. Mumamiriro ezvinhu aya, chiremba wako angada kuchinja chiyero, kana mamwe matanho angave achidiwa. Udza nyanzvi yako yehutano kana uri kutora chero mushonga wekuraira kana usingadi kuraira (over-the-counter [OTC]). Mimwe mishonga haifaniri kushandiswa panguva kana pedyo nenguva yekudya kana kudya marudzi akati wandei ezvokudya sezvo kuwirirana kungavepo. Kushandisa doro kana fodya nemamwe mishonga kunogona zvakare kukonzera kuwirirana kuitika. Kurukura nehutano hwako hwenyanzvi kushandiswa kwemushonga wako nezvokudya, doro, kana fodya.
Mufambiri kana mumwe munyanzvi wehutano akarovedzwa achakupa iwe kana mwana wako mushonga uyu muchipatara kana mukiriniki. Mushonga uyu unopihwa kuburikidza ne catheter ye-IV inoiswa mumutsinga yako. Mushonga unofanirwa kuiswa zvishoma nezvishoma, saka IV yako ichafanirwa kugara kwenguva yemaminitsi makumi matanhatu kusvika ku120. Kazhinji inopiwa svondo rimwe nerimwe. Chiremba wako anogona kukupa mimwe mishonga usati watanga kurapwa (semuenzaniso, mushonga wehosha, steroid) kuti ubatsire kudzivirira zvinokonzeresa zvisingadiwi.