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October 10, 2025
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I-atrioventricular canal defect iyinkinga yenhliziyo evela ngokuzalwa lapho izindonga ezihlukanisa amakamelo enhliziyo zingakhiwa kahle khona. Lokhu kudala ukuvulwa phakathi kwamakamelo aphezulu naphansi enhliziyweni, okuvumela igazi lixubeke lapho lingafanele lixubeke khona.
Le nkinga ithonya ukugeleza okujwayelekile kwegazi enhliziyweni yengane yakho, okungenza inhliziyo isebenze nzima kunokujwayelekile. Nakuba kuzwakala kukhulu, abantwana abaningi abane le nkinga baphila impilo egcwele, esebenzayo ngokunakekelwa komtholampilo okufanele nokwelashwa.
I-atrioventricular canal defect kwenzeka lapho ithusi elihlukanisa ngokujwayelekile amakamelo amane enhliziyo yakho lingathuthuki ngokuphelele phakathi kokukhulelwa. Esikhundleni sokuba nezindonga eziqinile phakathi kwamakamelo, kukhona izikhala ezivumela igazi ligeleze lapho lingafanele ligeleze khona.
Inhliziyo yakho inamakamelo amane - amabili aphezulu abizwa ngokuthi yi-atria namabili aphansi abizwa ngokuthi yi-ventricles. Ngokuvamile, igazi elingenayo i-oksijini lihlala ngakwesokudla kanti igazi eline-oksijini lihlala ngakwesobunxele. Nale nkinga, igazi lixuba phakathi kwalezi zicubu, okusho ukuthi umzimba wakho ungase ungatholi igazi elanele eline-oksijini.
Le nkinga ibizwa nangokuthi yi-atrioventricular septal defect noma i-endocardial cushion defect. Ingenye yezinkinga zenhliziyo eziyinkimbinkimbi kakhulu ezingokuzalwa, okusho ukuthi ikhona kusukela ngokuzalwa futhi ithonya izingxenye eziningi zesakhiwo senhliziyo.
Kukhona izinhlobo ezimbili eziyinhloko zale nkinga yenhliziyo, nokuqonda ukuthi yiluphi uhlobo oluthonya ingane yakho kusiza odokotela ukuhlela indlela yokwelapha engcono kakhulu.
I-partial atrioventricular canal defect ihilela ukuvulwa odongeni phakathi kwamakamelo amabili aphezulu enhliziyo. Ama-valve enhliziyo alawula ukugeleza kwegazi angase abe nesimo esingajwayelekile, kodwa ahlala ehlukene komunye nomunye. Lo mbono ngokuvamile ubangela izimpawu ezimbalwa futhi ungase ungabonakali kuze kube kamuva ebuntwaneni.
I-complete atrioventricular canal defect inkimbinkimbi kakhulu, ngokuvulwa kokubili odongeni lwamakamelo aphezulu naphansi. Ama-valve enhliziyo axhunyiwe, akha i-valve enkulu kunokuba kube amabili ahlukene. Lo mbono ngokuvamile ubangela izimpawu ekuqaleni ebuntwaneni ngoba kukhona ukuxuba kwegazi okuningi.
Abanye abantwana bane lokho odokotela abakubiza ngokuthi uhlobo oluphakathi noma oluguqukayo, oluwela phakathi kwe-partial ne-complete. I-pediatric cardiologist yakho izonquma ukuthi yiluphi uhlobo ingane yakho elinayo ngokusebenzisa ukuhlolwa okukhethekile kwenhliziyo ne-imaging.
Izimpawu ingane yakho ezibonisa zincike ekuthini inkinga inkulu kangakanani nokuthi kukhona ukuxuba kwegazi okungakanani enhliziyweni yayo. Abanye abantwana babonisa izimpawu ekuqaleni, kanti abanye bangase bangabi nazimpawu ezicacile izinyanga noma iminyaka.
Nazi izimpawu ezivamile abazali abazibonayo kubantwana abasebancane nabakhulu:
Njengoba abantwana bekhula, ungase uqaphele ukuthi abakwazi ukulandela abangani babo ngesikhathi semisebenzi yomzimba. Bangase badinge ukuphumula kaningi noma bagweme imisebenzi ebabangela ukuphefumula okunzima.
Abanye abantwana abanezinhlobo ezilula zale nkinga bangase bangabonisi izimpawu ezicacile kuze kube yilapho beyizinsana noma ngisho nasebangeni lesikole. Kungakho ukuhlolwa okujwayelekile kwabantwana kubaluleke kangaka - udokotela wakho angathola i-heart murmurs noma ezinye izimpawu ezincane ngesikhathi sokuhlolwa okujwayelekile.
Le nkinga yenhliziyo ithuthuka phakathi kwamasonto ayisishiyagalombili okuqala kokukhulelwa lapho inhliziyo yengane yakho ikha khona. Imbangela eqondile ayicaci ngaso sonke isikhathi, kodwa kwenzeka lapho ithusi okufanele lihlukanise amakamelo enhliziyo lingakhula kahle ngaleso sikhathi esibalulekile.
Eziningi zezi meko zenzeka ngokungahleliwe ngaphandle kwanoma yisiphi isizathu esithile noma isenzo sabazali esibangela zona. Kubalulekile ukuqonda ukuthi akukho lutho owalwenza noma awungenzanga ngesikhathi sokukhulelwa okubangele le nkinga - kuyindlela nje inhliziyo yengane yakho eyenziwe ngayo.
Kodwa-ke, kunezinto ezithile ezingandisa amathuba ale nkinga yokwenzeka:
Ngisho nalapho lezi zinto ezingozi zikhona, izingane eziningi zizalwa zinezinhliziyo ezijwayelekile. Iningi le-atrioventricular canal defects kwenzeka emindenini engenamlando wangaphambili wezinkinga zenhliziyo.
Uma uqaphela noma yiziphi izimpawu ezikukhathazayo ngokuphefumula, ukudla, noma amazinga kwamandla engane yakho, kuhlale kungcono ukuthi ihlolwe ngokushesha kunokuba kube sekwephuzile. Themba izinzwa zakho njengomzali - uyayazi kangcono ingane yakho.
Xhumana nodokotela wakho wezingane ngokushesha uma ingane yakho ibonisa noma yiziphi izimpawu ezilandelayo:
Shaya izinsizakalo eziphuthumayo ngokushesha uma ingane yakho inenkinga enkulu yokuphefumula, iba mhlophe noma iluhlaza okwesibhakabhaka kakhulu, noma ibonakala ikhathele kakhulu futhi ingaphenduli. Lokhu kungaba izimpawu zokuthi inhliziyo yayo ayipompi kahle ngokwanele ukuhlangabezana nezidingo zomzimba wayo.
Khumbula ukuthi ukutholakala kwangaphambi kwesikhathi nokwelashwa kuholela emiphumeleni emihle kakhulu. Abantwana abaningi abane le nkinga benza kahle kakhulu lapho ukunakekelwa kwabo kuphathwa ochwepheshe abanolwazi bezingane zenhliziyo.
Nakuba eziningi zezi meko zenzeka ngokungahleliwe, izinto ezithile zingandisa amathuba okuba ingane izalwe nale nkinga yenhliziyo. Ukuqonda lezi zinto ezingozi kungakusiza wazi ukuthi yini okufanele uyilindele nokuthi nini ukubhekwa okuqonde kakhulu kungase kudingeke.
Into enkulu engumngcipheko yi-Down syndrome, njengoba cishe ingxenye yabantwana abane le nkinga ye-genetic nabo bane-atrioventricular canal defects. Uma ingane yakho ine-Down syndrome, iqembu lakho lezokwelapha cishe lizoyilandela inhliziyo yayo eduze kakhulu kusukela ngokuzalwa.
Ezinye izinto ezingase zikhulise ingozi zifaka:
Kubalulekile ukukhumbula ukuthi ukuba nezinto ezingozi akusho ukuthi ingane yakho izoba nale nkinga ngokuqinisekile. Izingane eziningi ezelwe kubomama abanezinto ezingozi eziningi zinezinhliziyo ezijwayelekile ngokuphelele, kanti ezinye ezingenazo izinto ezingozi zingase zithuthukise izinkinga zenhliziyo.
Ngaphandle kokwelashwa okufanele, le nkinga yenhliziyo ingabangela izinkinga ezinkulu ngokuhamba kwesikhathi. Kodwa-ke, ngokunakekelwa komtholampilo okufanele nokuhlinzwa uma kudingeka, eziningi zalezi zinkinga zingavikeleka noma ziphathwe kahle.
Izinkinga ezivamile kakhulu ezingase zithuthuke zifaka:
Izinkinga ezinkulu kodwa ezingavamile zingafaka i-stroke, ikakhulukazi kubantwana abane uhlobo oluphelele lwenkinga. Abanye abantwana bangase bathuthukise isimo esibizwa nge-Eisenmenger syndrome, lapho imithambo yegazi emaphashini yonakale unomphela ngenxa yokucindezela okuphezulu.
Izindaba ezinhle ukuthi ukulungiswa kokuhlamba kwangaphambi kwesikhathi kunciphisa kakhulu ingozi yalezi zinkinga. Abantwana abaningi abenza ukuhlinzwa ngesikhathi esifanele bayaqhubeka bephila impilo evamile, enempilo ngengozi encane kakhulu yezinkinga zenhliziyo ezinkulu.
Ukutholakala ngokuvamile kuqala lapho udokotela wakho wezingane ezwa umsindo ongajwayelekile wenhliziyo obizwa nge-murmur ngesikhathi sokuhlolwa okujwayelekile. Akuwona wonke ama-murmurs enhliziyo abonisa izinkinga, kodwa udokotela wakho uzofuna ukuhlola ukuze aqinisekise ukuthi inhliziyo yengane yakho isebenza kahle.
Isinyathelo sokuqala ngokuvamile yi-echocardiogram, efana ne-ultrasound yenhliziyo. Lo mviwo usebenzisa amaza omsindo ukwenza izithombe eziningiliziwe zesakhiwo senhliziyo yengane yakho futhi ubonise ukuthi igazi ligeleza kanjani ngamakamelo. Awubuhlungu nhlobo futhi awudingi izinsimbi noma imithi.
Udokotela wakho angase futhi a-ode le miviwo eyengeziwe:
Ngezinye izikhathi le nkinga itholakala ngaphambi kokuzalwa ngesikhathi sokuhlolwa okujwayelekile kokukhulelwa. Uma odokotela bethola ukuthi kukhona inkinga yenhliziyo ngesikhathi sokukhulelwa, ungase ube ne-fetal echocardiogram ekhethekile ukuthola isithombe esicacile sokuthuthuka kwenhliziyo yengane yakho.
Ukuthola ukutholakala okuchane kwenza iqembu lakho lezokwelapha lihlele indlela yokwelapha engcono kakhulu nesikhathi esifanele sesimo sengane yakho.
Ukuphathwa kuxhomeke kuhlobo nobunzima benkinga ethile yengane yakho. Umgomo oyinhloko ukubuyisela ukugeleza kwegazi okujwayelekile enhliziyweni nokuvimbela izinkinga ezingase zithuthuke ngokuhamba kwesikhathi.
Ngezinkinga ezilula ezinempawu ezilula, odokotela bangase baqale ngokulandela ingane yakho eduze ngenkathi beqondisa izimpawu ngemithi. Le mithi ingasiza inhliziyo iphompe kahle futhi inciphisa ukwakheka kwamanzi emaphashini.
Ukuhlinzwa yilona kuphathwa okuqinisekile kubantwana abaningi abane le nkinga. Isikhathi sixhomeke ezimpawu zengane yakho nokuthi inhliziyo yayo isebenza kahle kangakanani:
Ngesikhathi sokuhlinzwa, udokotela ohlinzayo uvala ukuvulwa okungajwayelekile ngama-patches futhi alungisa noma ashintshe ama-valve enhliziyo angajwayelekile. Abantwana abaningi badinga ukuhlinzwa okukodwa kuphela, nakuba abanye bangase badinge izinqubo ezengeziwe njengoba bekhula.
Izinga lokuphumelela kokuhlamba liphezulu kakhulu, ikakhulukazi lapho kwenziwa ezikhungweni zezingane zenhliziyo ezikhethekile. Abantwana abaningi bayaphila futhi bangabamba iqhaza emisebenzini evamile yobunye phakathi nezinyanga ezimbalwa ngemuva kokuhlamba.
Ukukhathalela ingane enale nkinga yenhliziyo ekhaya kuhilela ukulandela izimpawu zayo, ukulandela izikhathi zemithi, nokudala indawo esekela impilo yayo nokuthuthuka.
Ngaphambi kokuhlamba, gxila ekusizeni ingane yakho ukulondoloza amandla nokukhula kahle ngangokunokwenzeka. Lokhu kungase kusho ukunikeza ukudla okuncane, okuvamile uma ukudla kunzima, noma ukuvumela isikhathi esengeziwe sokuphumula ngosuku.
Nazi izici ezibalulekile zokunakekelwa kwasekhaya:
Ngemuva kokuhlamba, ingane yakho izodinga isikhathi sokuphulukisa, kodwa izingane eziningi zibuyela ngokushesha ngokumangalisayo. Landela imiyalo yodokotela wakho mayelana nokuvinjelwa kwemisebenzi, ukunakekelwa kwezindawo ezilimele, nokuthi nini kufanele ubuyele emisebenzini evamile.
Khumbula ukuthi ingane ngayinye iphulukisa ngesivinini sayo siqu. Abanye abantwana bazizwa bephilile phakathi kwamasonto ambalwa, kanti abanye bangase bathathe izinyanga ezimbalwa ukuze babuyisele amandla abo aphelele namandla.
Ukuba ulungile emihlanganweni yezokwelapha kusiza uqinisekise ukuthi uthola ulwazi oluwusizo kakhulu futhi uzizwe ukhululekile ngecebo lokukhathalela ingane yakho. Bhala phansi imibuzo yakho ngaphambi kwesikhathi ukuze ungakhohlwa ukukhathazeka okubalulekile ngesikhathi sokuvakasha.
Letha uhlu oluphelele lwanoma iyiphi imithi noma izongezo ingane yakho ezithathayo, kufaka phakathi izilinganiso nesikhathi. Buye uqoqe noma yimiphi imiphumela yokuhlola yangaphambili, amarekhodi ezokwelapha, noma ulwazi lokuqondisa emadokotela abanye.
Cabanga ukulungiselela le mibuzo yeqembu lakho lezokwelapha:
Unganqikazi ukucela incazelo uma amagama ezokwelapha noma amacebo okwelapha ebonakala ekhathaza. Iqembu lakho lezokunakekelwa kwezempilo lifuna ukuqinisekisa ukuthi uyiqonda ngokuphelele isimo sengane yakho futhi uzizwe ukhululekile ngecebo lokukhathalela.
Letha incwadi noma ubuze uma ungarekhoda izingxenye ezibalulekile yengxoxo. Ulwazi lwezokwelapha lungase lukhathaze, futhi ukuba nezinqolobane zokubhekisela kamuva kungaba usizo kakhulu.
Nakuba ukufunda ukuthi ingane yakho inenkinga yenhliziyo kungase kuzwakale kukhulu, kubalulekile ukwazi ukuthi i-atrioventricular canal defects izimo eziqondwa kahle ezineziphumo ezinhle zokwelashwa. Abantwana abaningi abamukela ukunakekelwa okufanele bayaqhubeka bephila impilo evamile ngokuphelele.
Ukuphumelela kuyisihluthulelo ukusebenza nochwepheshe abanolwazi bezingane zenhliziyo abangakusiza ngenqubo yokwelashwa. Izindlela zokuhlamba zamanje zenzile ukulungisa lezi zinkinga kuphephile futhi kusebenza kahle, ngezinga lokuphumelela eliphezulu kunama-95% ezindaweni ezinkulu zezingane zenhliziyo.
Iqembu lezokwelapha lengane yakho lizodala icebo lokukhathalela eliqondene nesimo sayo esithile senkinga nempilo yayo yonke. Ngokwelashwa okufanele, abantwana abaningi abane le nkinga bangabamba iqhaza kuzo zonke imisebenzi evamile yobunye, kufaka phakathi imidlalo kanye nezinye imisebenzi yomzimba.
Khumbula ukuthi awuwedwa kule ndlela. Imindeni eminingi ihambe kule ndlela ngaphambi kwakho, futhi kukhona izinsiza ezinhle zokusekela ezitholakala ukuze zikusize uhambe ngezici zezokwelapha nezingokomzwelo zokunakekelwa kwengane yakho.
Izingane eziningi zingabamba iqhaza emisebenzini yomzimba evamile nemidlalo ngemuva kokuhlamba okuphumelelayo. I-pediatric cardiologist yakho izohlola umsebenzi wenhliziyo yengane yakho futhi inikeze imiyalo ethile mayelana namazinga wemisebenzi. Izingane eziningi ezine-atrioventricular canal defects ezilungisiwe zihlanganyela emidlalweni yokuncintisana ngaphandle kwemikhawulo, kanti ezinye zingase zibe nemikhawulo emincane emisebenzini eqinile kakhulu.
Izidingo zemithi ziyahluka kuye ngesimo esithile sengane yakho nokuthi inhliziyo yayo isebenza kahle kangakanani ngemuva kokuhlamba. Abanye abantwana badinga imithi okwesikhashana kuphela ngaphambi nangemuva kokuhlamba, kanti abanye bangase bayidinga isikhathi eside ukuze basize inhliziyo yabo isebenze kahle. I-cardiologist yakho izohlola njalo ukuthi imithi isadingeka yini futhi ilinganisise icebo lokwelapha njengoba ingane yakho ikhula.
Ingozi yokuba ne-baby enye enenkinga yenhliziyo ezingokuzalwa iphezulu kancane kunokujwayelekile, kodwa isalula. Imindeni eminingi ayina-baby enye enenkinga efanayo. Udokotela wakho angase akukhuthaze ukubonisana nge-genetic ukuze uxoxe ngezinto ezingozi zomndeni wakho nezinketho zokuhlola ezitholakalayo ngesikhathi sokukhulelwa kwesikhathi esizayo.
Izingane eziningi zidinga ukuhlinzwa okukodwa kuphela ukulungisa i-atrioventricular canal defect yazo. Kodwa-ke, abanye abantwana bangase badinge izinqubo ezengeziwe njengoba bekhula, ikakhulukazi uma ama-valve enhliziyo angasebenzi kahle ngemuva kokulungiswa kokuqala. I-cardiologist yengane yakho izolandela umsebenzi wenhliziyo yayo ngokuhamba kwesikhathi futhi ikhuthaze ukwelashwa okwengeziwe uma kudingeka.
Isikhathi sokuphulukisa siyahluka, kodwa izingane eziningi zingabuya kancane kancane emisebenzini evamile phakathi kwamasonto angu-6-8 ngemuva kokuhlamba. Udokotela wakho ohlinzayo uzonikeza imiyalo ethile mayelana nokuvinjelwa kokuphakamisa, ukuthi ingane yakho ingabuya nini esikoleni, nokuthi ingabuya nini emisebenzini yomzimba. Izingane eziningi zizizwa zilungile kakhulu phakathi kwamasonto ambalwa okuqala futhi ziyaqhubeka ziphulukisa ezinyangeni ezilandelayo.
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