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Ukuthi yini i-Brugada Syndrome? Izimpawu, Izimbangela, Nokwelashwa

Created at:1/16/2025

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I-Brugada syndrome yisifo esingavamile sokubetha kwenhliziyo esithinta indlela ama-elekthrikhi asabela ngayo enhliziyweni yakho. Lesi simo se-genetic singabangela inhliziyo yakho ukuba ibetha ngokushesha noma ngokungajwayelekile, okungase kubeka engozini yokuphelelwa yikhanda noma, ezimweni ezinzima, ukuqhekeka kwenhliziyo ngokuzumayo.

Lesi simo saqala ukubikwa ngo-1992 ngabachwepheshe bezempilo baseSpain, uPedro noJosep Brugada. Kuthinta ikakhulu ingxenye yasekunene yesistimu yama-elekthrikhi yenhliziyo yakho. Nakuba kuzwakala kukhulu, ukuqonda i-Brugada syndrome kuzokusiza ukusebenzisana neqembu lakho lezokunakekelwa kwezempilo ukuze lilawulwe kahle.

Zithini izimpawu ze-Brugada syndrome?

Abantu abaningi abane-Brugada syndrome abanawo noma yimiphi impawu. Uma izimpawu zivele, zivame ukuxhumene nokubetha kwenhliziyo okungajwayelekile okungaba yingozi kakhulu.

Nawa amanye wempawu evamile ongaqaphela:

  • Ukuphulukana nokuqonda noma ukuphelelwa yikhanda okuphuthumayo, ikakhulukazi ngesikhathi sokuphumula noma ubuthongo
  • Ukubetha kwenhliziyo okungajwayelekile noma ukuzwa sengathi inhliziyo yakho ibetha ngokushesha noma iyeka ukubetha
  • Ukuphefumula okunzima noma ukuphefumula okufushane
  • Ubuhlungu noma ukungakhululeki esifubeni
  • Ukukhungatheka noma ukuphelelwa amandla
  • Izehlakalo ezifana nezehlakalo zokubamba ngesikhathi sokuphelelwa yikhanda

Ingxenye enzima mayelana ne-Brugada syndrome iwukuthi izimpawu zivame ukwenzeka ngesikhathi sobuthongo noma izikhathi zokuphumula, kunokuba ngesikhathi sokuzivocavoca. Lokhu kuhlukile kwezinye izimo zenhliziyo eziningi. Abanye abantu bahlangabezana nalokho okuthiwa "ukuphefumula okufa ngesikhathi sobuthongo," okuzwakala njengokuphefumula okukhulu noma okunzima ngesikhathi sobuthongo.

Ezimweni ezingavamile, uphawu lokuqala lwe-Brugada syndrome lungaba ukuqhekeka kwenhliziyo ngokuzumayo. Kungakho ukuhlolwa komndeni kubaluleke kakhulu uma othile emndenini wakho ekwazile lesi simo.

Ziyini izinhlobo ze-Brugada syndrome?

I-Brugada syndrome ihlelwe ngezinhlobo ezahlukene ngokususelwa ekuguqukeni kwe-genetic okuhilelekile. Uhlobo oluvamile yi-Type 1, olumelela cishe ama-20-25% ezimo.

I-Type 1 Brugada syndrome ihilela ukuguqulwa kwe-SCN5A gene, elawula ama-sodium channels ezicellini zenhliziyo yakho. Lolu hlobo luvamise ukuba nezimpawu zokudluliselwa ezibikezelwayo futhi kuvame ukuba lula ukuqonda ngokuhlolwa kwe-genetic.

Izinhlobo ezi-2 kuya kwezi-12 zihilela ukuguqulwa kwezinye i-genes ezithinta ama-ion channels ahlukene enhliziyweni yakho. Lezi zinhlobo zingevamile kakhulu futhi ngezinye izikhathi kunzima ukuzithola ngokuhlolwa kwe-genetic okuvamile. Uhlobo ngalunye lungaba nezimpawu nezinga lokutholakala ezihlukene kancane.

Kodwa-ke, kubalulekile ukwazi ukuthi abantu abafika ku-70% abane-Brugada syndrome abanalo ukuguqulwa kwe-genetic oluqondakaliyo ngezindlela zokuhlola ezimanje. Lokhu akusho ukuthi lesi simo asiyona into yangempela noma asibi - kusho nje ukuthi ososayensi basafunda ngazo zonke izici ze-genetic ezihilelekile.

Yini ebangela i-Brugada syndrome?

I-Brugada syndrome ibangelwa ikakhulu ukuguqulwa kwe-genetic okuthinta indlela ama-elekthrikhi asabela ngayo emithanjeni yenhliziyo yakho. Le miqulu iphazamisa ukugeleza okuvamile kwama-sodium, calcium, noma ama-potassium ions ezicellini zenhliziyo yakho.

Cabanga ngesistimu yama-elekthrikhi yenhliziyo yakho njengentambo yendlu yakho. Uma kunenkinga "neentambo" ngenxa yokuguqulwa kwe-genetic, kungabangela ukuphazamiseka kwama-elekthrikhi okubangela ukubetha kwenhliziyo okungozi.

Lesi simo siwusifa oluvela kubazali. Lokhu kusho ukuthi uma omunye wabazali bakho enesifo se-Brugada syndrome, unethuba lama-50% lokudluliselwa ukuguqulwa kwe-genetic. Kodwa-ke, ukuba nokuguqulwa akusho ukuthi uzophumelela izimpawu.

Izici ezithile zingabangela izimpawu kubantu abane-genetic predisposition:

  • Ukuqunjelwa, ikakhulukazi ukuqunjelwa okuphezulu ngaphezu kuka-102°F (39°C)
  • Imithi ethile, ikakhulukazi imithi ethile yokulwa nokubetha kwenhliziyo okungajwayelekile, imithi yokucindezeleka, kanye ne-anesthetics
  • Ukungahlangani kahle kwama-electrolyte, ikakhulukazi i-potassium ephansi noma i-calcium ephezulu
  • Ukusebenzisa utshwala ngokweqile
  • Ukusebenzisa i-cocaine
  • Ukudla okukhulu noma ukuphelelwa amanzi ezimweni ezithile

Ngokuthakazelisayo, ngokungafani nezinye izimo zenhliziyo, ukuzivocavoca ngokomzimba ngokuvamile akubangeli izimpawu ze-Brugada syndrome. Eqinisweni, izimpawu zivame ukwenzeka ngesikhathi sokuphumula noma ubuthongo lapho izinga lenhliziyo yakho liphansi ngokwemvelo.

Nini kufanele ubona udokotela nge-Brugada syndrome?

Kufanele ufuna ukunakekelwa kwezokwelapha ngokushesha uma uhlangabezana nezehlakalo zokuphelelwa yikhanda, ikakhulukazi uma zenzeka ngesikhathi sokuphumula noma ubuthongo. Noma yisiphi isigameko sokulahlekelwa ukuqonda ngokuzumayo kufanele sihlolwe ngokushesha.

Shaya u-911 noma uhambe e-emergency room ngokushesha uma uhlangabezana nobuhlungu besifuba, ukuphefumula okunzima kakhulu, noma uma othile ekufumana ungazi.

Hlela i-aphoyintimenti nodokotela wakho uma uqaphela ukubetha kwenhliziyo okungajwayelekile okuphindaphindayo, ukukhungatheka okuvamile, noma uma unemlando womndeni wokufa kwenhliziyo ngokuzumayo, ikakhulukazi kubantu abangaphansi kweminyaka engama-50. Ngisho noma izimpawu zakho zibonakala zingenangozi, kungcono ukuzihlola.

Kufanele futhi ubona udokotela uma usebenzisa imithi futhi uqaphela izimpawu zenhliziyo ezintsha. Imithi ethile ingenza i-Brugada syndrome ibe yimbi, futhi udokotela wakho angase adinge ukulungisa uhlelo lwakho lokwelashwa.

Ziyini izici ezingaholela ekutholeni i-Brugada syndrome?

Izici eziningi zingandisa amathuba akho okuthola i-Brugada syndrome noma ukuhlangabezana nezimpawu uma unesimo. Ukuqonda lezi zici ezingaholela ekutholeni lesi simo kuzokusiza wena nodokotela wakho ukuthi niqonde kahle isimo sakho.

Izici eziyinhloko ezingaholela ekutholeni lesi simo zifaka:

  • Umlando womndeni we-Brugada syndrome noma ukufa kwenhliziyo ngokuzumayo okungachazeki
  • Ukuba owesilisa (abesilisa banethuba elingaphezulu kwama-8-10 lokuthola izimpawu kunabesifazane)
  • Ubuzwe base-Asia, ikakhulukazi isizwe saseNingizimu-mpumalanga Asia noma isizwe saseJapan
  • Iminyaka phakathi kweminyaka engama-30-50 (lapho izimpawu zivame ukubonakala khona)
  • Ukuba nezinye izimo zokubetha kwenhliziyo okungajwayelekile
  • Ukusebenzisa imithi ethile ethinta ukubetha kwenhliziyo

Ngokuthakazelisayo, ngenkathi abesifazane bengadlulisela futhi baphathe ukuguqulwa kwe-Brugada gene, banethuba elincane kakhulu lokuthola izimpawu. Ososayensi bacabanga ukuthi ama-hormone, ikakhulukazi i-estrogen, angase avikele ekuthonyweni kwalesi simo.

Izici zezwe nazo zidlal'indima. I-Brugada syndrome ivame kakhulu ezingxenyeni ezithile zezwe, ikakhulukazi eNingizimu-mpumalanga Asia. Kweminye imiphakathi yaseThailand naseLaos, kubizwa ngokuthi "i-Sudden Unexplained Nocturnal Death Syndrome" futhi iyona imbangela eholela ekufuleni kwabesilisa abasebancane.

Ziyini izinhlanganisela ezingaba khona ze-Brugada syndrome?

Inhlanganisela enzima kakhulu ye-Brugada syndrome ukuqhekeka kwenhliziyo ngokuzumayo, okungaba yingozi uma kungelashwa ngokushesha. Lokhu kwenzeka lapho inhliziyo yakho ithola ukubetha okusheshayo, okungajwayelekile okumvimba ukupompa igazi ngokuphumelelayo.

Abantu abane-Brugada syndrome bahlangabezana nezinhlanganisela eziningi ezingaba khona:

  • I-Ventricular fibrillation (ukubetha kwenhliziyo okungajwayelekile, okungajwayelekile)
  • Ukufa kwenhliziyo ngokuzumayo, ikakhulukazi ngesikhathi sobuthongo noma ukuphumula
  • Ukuphindaphinda kwezehlakalo zokuphelelwa yikhanda okungabangela ukulimala ngokuwa
  • I-Atrial fibrillation (ukubetha okungajwayelekile emakhameni aphezulu enhliziyo)
  • Ukungasebenzi kahle kwenhliziyo ezimweni ezingavamile ngezigameko eziphindaphindayo
  • Ukuthonywa ngokwengqondo okuvela ekuphilini nesimo esingaba yingozi ekuphileni

Ingozi yalezi zinhlobo ezihlanganisiwe ihluka kakhulu kumuntu ngamunye. Abanye abantu abane-Brugada syndrome abanawo noma yimiphi impawu, ngenkathi abanye bengaba nezehlakalo ezingaba yingozi ekuphileni. Udokotela wakho angakusiza ukuthi uhlole ingozi yakho ngokususelwa esimweni sakho esithile nemiphumela yokuhlola.

Kubalulekile ukwazi ukuthi ngokuphathwa kahle kwezokwelapha, abantu abaningi abane-Brugada syndrome baphila impilo evamile, esebenzayo. Okubalulekile ukusebenzisana eduze nochwepheshe wokubetha kwenhliziyo ukuze uqaphe isimo sakho futhi uthathe izinyathelo ezifanele.

I-Brugada syndrome ihlonishwa kanjani?

Ukuhlonishwa kwe-Brugada syndrome kudinga ukuhlanganiswa kokuhlola nokuhlolwa okucophelelayo ngochwepheshe wenhliziyo. Ukuhlonishwa akuhlali kulula ngoba isimo singaba sesikhathini esithile futhi izimpawu zingase ziye ziye.

Udokotela wakho uzoqala ngomlando wezokwelapha onemininingwane kanye nokuhlolwa komzimba. Uzokubuza ngezimpawu zakho, umlando womndeni, kanye nanoma iyiphi imithi oyisebenzisayo. Lolu lwazi luzosiza ukuthi aqonde izici ezingaholela ekutholeni lesi simo futhi anqume ukuthi yiziphi izivivinyo ezidingekayo.

Izivivinyo eziyinhloko zokuhlola zifaka:

  • I-Electrocardiogram (ECG) ukubuka izimpawu zokubetha kwenhliziyo
  • Ukuhlolwa kokusebenzisa imithi njenge-flecainide noma i-procainamide
  • I-Holter monitor noma i-event recorder ukuqopha ukubetha kwenhliziyo ngokuhamba kwesikhathi
  • Isifundo se-Electrophysiology ukuhlola isistimu yama-elekthrikhi yenhliziyo yakho
  • Ukuhlolwa kwe-genetic ukubuka ukuguqulwa okwaziwayo
  • Ukuhlolwa komndeni uma unezihlobo ezinesimo

I-ECG ibaluleke kakhulu ngoba ingabonisa iphethini ethile ebizwa nge- "Brugada pattern." Kodwa-ke, leli phethini alibonakali njalo kuwo wonke amavivinyo, kungakho udokotela wakho angase akukhuthaze ukuthi wenze ama-ECG amaningi noma ukuqapha okuqhubekayo.

Ngezinye izikhathi, odokotela basebenzisa ukuhlolwa kokusebenzisa imithi lapho bakunika khona imithi engase iveze i-Brugada pattern uma unesimo. Lolu hlobo lokuhlola lwenziwa esibhedlela ngokuqapha okucophelelayo ngoba lungase lubangele ukubetha okungozi kubantu abanesifo.

Yini ukwelashwa kwe-Brugada syndrome?

Ukwelashwa kwe-Brugada syndrome kugxile ekuvimbeni ukubetha kwenhliziyo okungozi nokuphatha izimpawu. Uhlelo oluthile lokwelashwa luxhomeke ezingeni lakho lokutholakala, izimpawu, nemiphumela yokuhlola.

Kubantu abasezingeni elikhulu lokutholakala kokungasebenzi kahle kwenhliziyo ngokuzumayo, ukwelashwa okuyinhloko yi-implantable cardioverter defibrillator (ICD). Le divayisi encane iyalandelela ukubetha kwenhliziyo yakho futhi inikeza umsindo wama-elekthrikhi uma ithola ukubetha okungozi. Nakuba umsindo ungase ube buhlungu, ungasindisa impilo.

Izinketho zokwelashwa zifaka:

  • Ukuhlinzwa kwe-ICD kubantu abasezingeni elikhulu lokutholakala
  • Imithi njenge-quinidine ukusiza ukuqina ukubetha kwenhliziyo
  • Ukuqapha izinto ezingabangela lesi simo njengemithi ethile nokuqunjelwa okuphezulu
  • Ukuqapha okuvamile nokunakekelwa okulandelayo
  • Ukushintsha indlela yokuphila ukuze kunciphise ingozi
  • Ukuqondisa komndeni nokuhlolwa kwe-genetic

Akuwona wonke umuntu one-Brugada syndrome odinga i-ICD. Udokotela wakho uzohlola ingozi yakho ngokususelwa ezintweni ezifana nokuthi uke waba nezimpawu, imiphumela yokuhlola yakho, nomlando womndeni wakho. Abanye abantu bangaphathwa ngokuqapha okucophelelayo nokugwema izinto ezingabangela lesi simo.

Ukuphathwa kwemithi kubalulekile. Iqembu lakho lezokunakekelwa kwezempilo lizohlola yonke imithi yakho ukuqinisekisa ukuthi ayikho enye engenza isimo sakho sibe sibi. Bazokunika uhlu lwemithi okumele uyigweme futhi baqinisekise ukuthi bonke abahlinzeki bakho bezempilo bayazi ngesimo sakho.

Indlela yokulawula i-Brugada syndrome ekhaya?

Ukuphatha i-Brugada syndrome ekhaya kuhilela ukuthatha izinyathelo zokugwema izinto ezingabangela lesi simo nokulungela izimo eziphuthumayo. Nakuba lokhu kungase kuzwakale kukhulu, abantu abaningi baphatha kahle isimo sabo ngokwenza izinguquko ezithile ekuphileni kwabo.

Ukuphathwa kokunqunjelwa kubalulekile ngoba ukuqunjelwa okuphezulu kungabangela ukubetha okungozi. Gcina imithi yokunciphisa ukuqunjelwa njenge-acetaminophen noma i-ibuprofen ekhaya, futhi uxhumane nodokotela wakho uma ukuqunjelwa kwakho kuphezulu kuka-101°F (38.3°C). Ungazami "ukuhlala uqine" uma une-Brugada syndrome.

Nawa amasu ayinhloko okuphatha ekhaya:

  • Qapha ubushushu bakho uma uzizwa ugula futhi welaphe ukuqunjelwa ngokushesha
  • Phatha ikhadi le-wallet noma ugqoke ubucwebe bokunakekelwa kwezokwelapha ngokuhlolwa kwakho
  • Gcina uhlu oluvuselelwe lwemithi okumele uyigweme
  • Hlala unamanzi futhi ugcine ukudla okuhle
  • Thola ubuthongo obunempilo futhi ulawule ukucindezeleka
  • Gwema utshwala ngokweqile neziyobisi zokuzilibazisa

Uma une-ICD, funda indlela yokuhlola umsebenzi wayo futhi wazi ukuthi yini okumele uyenzile uma ishaya. Iqembu lakho ledivayisi lizokuqeqesha ukuthi uyilandele futhi nini kufanele ufuna usizo. Abantu abaningi bazivumelanisa kahle nokuthola i-ICD futhi bangabuyela emisebenzini yabo evamile.

Cabanga ngokufunda i-CPR nokuqinisekisa ukuthi amalungu omndeni wakho ayazi ukuthi angayenza kanjani. Nakuba uyathemba ukuthi ngeke uyidingi, ukuba nabantu abakuzungezile abazi i-CPR kungase kube okuqinisekisayo futhi kusindise impilo.

Kufanele ulungiselele kanjani i-aphoyintimenti yakho nodokotela?

Ukulungiselela i-aphoyintimenti yakho kuzokusiza uthole okuningi ekuhambeleni kwakho futhi kunikeze udokotela wakho ulwazi olulodwa olukusizayo. Qala ngokuqoqa ulwazi mayelana nezimpawu zakho nomlando womndeni wakho ngaphambi kokuya kwakho.

Bhala zonke izimpawu zakho, ngisho noma zibonakala zingaxhunyanisiwe nenhliziyo yakho. Qaphela ukuthi zenzeka nini, isikhathi esingakanani zihlala, nokuthi wawenzani lapho zenzeka khona. Lolu lwazi luzosiza udokotela wakho ukuthi aqonde kahle isimo sakho.

Ngaphambi kwe-aphoyintimenti yakho, lungiselela:

  • Uhlu oluphelele lwemithi yakho yamanje, kufaka phakathi izithasiselo
  • Umlando wezokwelapha womndeni wakho, ikakhulukazi noma yiziphi izinkinga zenhliziyo noma ukufa ngokuzumayo
  • Inkulumo enemininingwane yezimpawu zakho nokuthi zenzeka nini
  • Imibuzo ofuna ukuyibuza udokotela wakho
  • Noma yimiphi imiphumela yokuhlola yangaphambili noma amarekhodi ezokwelapha
  • Ulwazi mayelana nendlela yakho yokuphila, kufaka phakathi imikhuba yokuzivocavoca nezinga lokucindezeleka

Cabanga ngokuletha ilungu lomndeni noma umngani e-aphoyintimenti yakho. Bangakusiza ukuba ukhumbule ukuthi udokotela uthini futhi banikeze ukwesekwa ngesikhathi sokuvakasha okungase kube yingozi. Ukuba nomuntu lapho kungase futhi kusize uma udinga ukuxoxa ngokuhlonzwa komndeni.

Unganqikazi ukubuza imibuzo ngesikhathi sokuvakasha kwakho. Lena ithuba lakho lokuqonda isimo sakho nezinketho zokwelashwa. Buza nganoma yini ekukhathazayo, kufaka phakathi ukuthi yiziphi imisebenzi ephephile nezimpawu ezifanele zibangele ukunakekelwa kwezokwelapha ngokushesha.

Yini okufanele uyikhumbule mayelana ne-Brugada syndrome?

I-Brugada syndrome yisimo esinzima kodwa esilawuleka sokubetha kwenhliziyo okungajwayelekile okubandakanya ikakhulu isistimu yama-elekthrikhi yenhliziyo yakho. Nakuba ingaba yingozi ekuphileni, abantu abaningi abanesimo baphila impilo egcwele, esebenzayo ngokunakekelwa kwezokwelapha okufanele nokuphathwa kwendlela yokuphila.

Into ebaluleke kakhulu okumele uyikhumbule iwukuthi ukuhlonishwa kwangaphambi kwesikhathi nokwelashwa okufanele kunganciphisa kakhulu ingozi yezinhlanganisela. Uma unezimpawu noma umlando womndeni wesimo, ungalindi ukufuna ukuhlolwa kwezokwelapha.

Ukusebenzisana nochwepheshe wokubetha kwenhliziyo kubalulekile ekulawuleni i-Brugada syndrome ngokuphumelelayo. Bangakusiza ukuthi unqume izinga lakho lokutholakala futhi bakhe uhlelo lokwelashwa olufanele kuwe. Ukunakekelwa okulandelayo okuvamile nokuhlala unolwazi ngesimo sakho kuyisihluthulelo sokuphathwa okuphumelelayo.

Khumbula ukuthi ukuba ne-Brugada syndrome akusho ukuthi awukwazi ukuphila impilo evamile. Ngokuqapha okufanele nokunakekelwa kwezokwelapha, abantu abaningi abanesimo bangasebenza, bazivocavoce, futhi bajabulele imisebenzi yabo evamile. Okubalulekile ukuhlala unolwazi, ulandele uhlelo lwakho lokwelashwa, futhi ugcine ukuxhumana okuvulekile neqembu lakho lezokunakekelwa kwezempilo.

Imibuzo evamile mayelana ne-Brugada syndrome

Ingabe abantu abane-Brugada syndrome bangazivocavoca ngokuphephile?

Yebo, abantu abaningi abane-Brugada syndrome bangazivocavoca ngokuphephile. Ngokungafani nezinye izimo zenhliziyo eziningi, izimpawu ze-Brugada syndrome ngokuvamile aziveli ngesikhathi sokuzivocavoca. Kodwa-ke, kufanele uxoxe ngezinhlelo zakho zokuzivocavoca nodokotela wakho ukuqinisekisa ukuthi zifanele isimo sakho esithile.

Udokotela wakho angase akukhuthaze ukugwema imisebenzi enzima kakhulu noma imidlalo engozi enkulu yokulimaza uma une-ICD. Bazokusiza ukwakha uhlelo lokuzivocavoca olukubekela impilo ngenkathi kunciphisa izingozi.

Ingabe i-Brugada syndrome iwusifa?

Yebo, i-Brugada syndrome yisimo se-genetic esingadluliselwa kubantwana. Umuntu ngamunye ongumntwana womuntu one-Brugada syndrome unethuba lama-50% lokudluliselwa ukuguqulwa kwe-genetic. Kodwa-ke, ukuba nokuguqulwa akusho ukuthi izimpawu zizophumelela.

Ukuhlolwa komndeni kuvame ukukhuthazwa lapho othile etholakala enesifo se-Brugada syndrome. Lokhu kusiza ukuthola amanye amalungu omndeni angase abe nesimo futhi adinge ukuqapha noma ukwelashwa.

Ingabe imithi ingabangela izimpawu ze-Brugada syndrome?

Yebo, imithi ethile ingabangela ukubetha kwenhliziyo okungozi kubantu abane-Brugada syndrome. Lokhu kufaka imithi ethile yokulwa nokubetha kwenhliziyo okungajwayelekile, imithi yokucindezeleka, kanye ne-anesthetics ethile. Udokotela wakho uzokunika uhlu oluphelele lwemithi okumele uyigweme.

Ngalokhu, qiniseka ukuthi ubonisa noma yimuphi umhlinzeki wezokunakekelwa kwezempilo ngesimo sakho se-Brugada syndrome ngaphambi kokuba bakunike imithi entsha. Lokhu kufaka odokotela bezinyo, ochwepheshe bokuhlinzwa, nabanye ochwepheshe abangase bangajwayele isimo sakho.

Kufanele ngenzeni uma i-ICD yami ishaya?

Uma i-ICD yakho ishaya, zama ukuhlala uzolile bese uhlala phansi noma ulele phansi ngokushesha. Umsindo usho ukuthi idivayisi yakho itholile futhi iwelaphile ukubetha kwenhliziyo okungozi. Xhumana nodokotela wakho noma ikliniki yedivayisi ngokushesha ukuze ubike umsindo futhi uhlele i-aphoyintimenti yokulandelela.

Uma uthola imisindo eminingi noma uzizwa ungaphili kahle ngemuva komsindo, funa ukunakekelwa kwezokwelapha ngokushesha. Iqembu lakho ledivayisi lizohlola idatha evela kwi-ICD yakho ukuze liqonde ukuthi kwenzekeni futhi liqonde ukuthi yiziphi izinguquko ezidingekayo.

Ingabe abesifazane abane-Brugada syndrome bangaba nabantwana ngokuphephile?

Yebo, abesifazane abaningi abane-Brugada syndrome bangaba nabantwana ngokuphephile, kodwa ukukhulelwa kudinga ukuqapha okucophelelayo yedokotela wakho wenhliziyo nodokotela wakho wokubeletha. Ukuguqulwa kwama-hormone ngesikhathi sokukhulelwa kungase kuvikele ekutholeni izimpawu ze-Brugada syndrome.

Iqembu lakho lezokwelapha lizokuqapha eduze ngesikhathi sokukhulelwa nokubeletha. Bazoxoxa futhi ngokunakekelwa kwe-genetic ukukusiza ukuthi uqonde izingozi zokudlulisela isimo kubantwana bakho nezinketho zokuhlola ezitholakalayo.

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