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Granulomatosis Enemiphunga Eminingi

Uhlolojikelele

I-Granulomatosis enemi-polyangiitis yisifo esingavamile esibangela ukuvuvukala kwezitho eziphatha igazi ekhathini lakho, e-sinuses, ehlombe, emaphashini nasezinkingeni.

Sasibizwa ngokuthi i-Wegener's granulomatosis, lesi simo singenye yezinhlangano zezifo zezitho eziphatha igazi ezibizwa ngokuthi i-vasculitis. Siphazamisa ukugeleza kwegazi kwizitho zakho ezithile. Izicubu ezihlaselekayo zingathuthukisa izindawo zokuvuvukala ezibizwa ngama-granulomas, angathinta indlela lezi zitho ezisebenza ngayo.

Ukuxilongwa kwasekuqaleni nokuphathwa kwe-granulomatosis enemi-polyangiitis kungase kube yimbangela yokubuyela esimweni esiphelele. Ngaphandle kokwelashwa, lesi simo singabulala.

Izimpawu

Izimpawu nezimpawu ze-granulomatosis nge-polyangiitis zingase zivele ngokuzumayo noma ezinyangeni eziningana. Izimpawu zokuqala zivame ukubandakanya amasayinasi akho, umlomo noma amaphaphu. Isimo sivame ukuba sibi ngokushesha, sithinta imithambo yegazi namalungu abonelela ngayo, njengezinso. Izimpawu nezimpawu ze-granulomatosis nge-polyangiitis zingafaka: Ukuqothuka okufana noboya oluvela ekhaleni lakho, ukuqina, ukutheleleka kwama-sinus nokuphuma igazi ekhaleni Ukukhokha, ngezinye izikhathi nge-phlegm egaziwe Ukuphefumula kancane noma ukuthimula Ukuvuvukala Ukuqeda amandla Ubuhlungu bezingxenye zomzimba Ukuqina kwezinye izingxenye zomzimba, izinzwane noma iminwe Ukulahlekelwa isisindo Igazi emathisini Amacwebe esikhini, ukweluka noma isihlungu Amehlo abomvu, ukushisa noma ubuhlungu, nezinkinga zobono Ukuvuvukala kwezindlebe nezinkinga zokuzwa Kwabanye abantu, isifo sithinta kuphela amaphaphu. Uma izinso zithinteka, ukuhlolwa kwegazi nokwemithi kungabonisa inkinga. Ngaphandle kokwelashwa, ukuhluleka kwezinso noma kwamaphaphu kungenzeka. Bheka udokotela wakho uma unekhala eliqothuka elingaphenduli emithi yokuqothula i-cold medicines, ikakhulukazi uma lihambisana nokuphuma igazi ekhaleni nezinto ezifana noboya, ukukhokha igazi, noma ezinye izimpawu ze-granulomatosis nge-polyangiitis. Ngenxa yokuthi lesi sifo singaba sibi ngokushesha, ukuxilongwa kwasekuqaleni kuyisihluthulelo sokuthola ukwelashwa okuphumelelayo.

Isikhathi sokubona udokotela

Bona udokotela uma unekhala elingapheli ngisho noma usebenzisa imithi yekhanda ethengekayo, ikakhulu uma lihambisana nokuphuma igazi emakhaleni, nokuphuma okuthakazelayo okufana nophuphu, ukukhokha igazi, noma ezinye izimpawu zoxwayiso ze granulomatosis with polyangiitis. Ngenxa yokuthi lesi sifo singaba sibi ngokushesha, ukutholakala kwesifo kungumqondo wokuthola ukwelashwa okuphumelelayo.

Izimbangela

Imbangela ye granulomatosis nge polyangiitis ayaziwa. Ayikhuthazi, futhi awekho ubufakazi bokuthi iyefa. Isimo singabangela imithambo yegazi efinyelelwe, ecindezelekile kanye nemfucuza yethishu ebuhlungu (granulomas). Ama granulomas angabhubhisa ithishu evamile, futhi imithambo yegazi ecindezelekile inquma inani legazi no-oksijini olufinyelela kuma-tissue namalungu omzimba wakho.

Izici eziyingozi

I-Granulomatosis with polyangiitis ingaba khona kunoma iyiphi iminyaka. Ngokuvamile ithinta abantu abaneminyaka ephakathi kwengu-40 no-65.

Izingqinamba

Ngaphandle kokuthinta iphunga lakho, amasinya, umlomo, amaphaphu kanye nezinkalazi, i granulomatosis enezifo eziningi ze polyangiitis ingathinta nokwakho, amehlo, izindlebe, inhliziyo namanye amalungu. Izingcindezi zingafaka:

  • Ukuba buthuntu kwezindlebe
  • Ukwenzakala kwesikhumba
  • Ukonakala kwezinkalazi
  • Ukwehla kokuphakama kwesiphambano sekhala (ukugoba) okubangelwa yigagasi elibuthakathaka
  • Iqhwa legazi eliqala kwenye noma ngaphezulu kwezinsimbi ezijulile, ngokuvamile ohlangothini lwakho
Ukuxilongwa

Udokotela wakho uzokubuza ngezimpawu zakho nezibonakaliso, enze ukuhlolwa komzimba, bese uthatha umlando wakho wezokwelapha.

Izivivinyo zegazi zingahlola oku:

  • Izimpawu zokuvuvukala, njengamanani aphezulu e-C-reactive protein noma izinga eliphezulu le-erythrocyte sedimentation rate — okuvame ukubizwa ngokuthi yi-sed rate.
  • Ama-anti-neutrophil cytoplasmic antibodies, abonakala egazini labantu abaningi abanogranulomatosis enemi-polyangiitis esebenzayo.
  • Ukugula kwegazi, okuvamile kubantu abanesifo.
  • Izimpawu zokuthi amandla akho okungcola awasebenzi kahle ekususeni imikhiqizo yokuwohloka egazini lakho.

Izivivinyo zomchamo zingaveza ukuthi umchamo wakho unawo amaseli egazi ebomvu noma uneprotheni eningi kakhulu, okungase kubonise ukuthi isifo siyaphazamisa amandla akho okungcola.

I-X-rays yesifuba, i-CT noma i-MRI zingasiza ekuqondeni ukuthi yiziphi izithelo zegazi namalungu omzimba aziwa. Zingasiza nodokotela wakho ukuba aqaphe ukuthi uyaphendula kahle yini ekwelapheni.

Lona yindlela yokwelapha ngokuhlinzwa lapho udokotela wakho ekhipha khona isampula encane yethishu endaweni ethintekile yomzimba wakho. I-biopsy ingaqinisekisa ukuxilongwa kwe-granulomatosis enemi-polyangiitis.

Ukwelashwa

Uma ngaqala ukuthola ukwelashwa ngokushesha futhi ngendlela efanele, ungase uphulukiswe yi granulomatosis nge polyangiitis phakathi nezinyanga ezimbalwa. Ukwelashwa kungase kuhilele ukusebenzisa imithi yokwelapha isikhathi eside ukuvimbela ukubuyela kwesifo. Ngisho noma ukhona ukwephuza ukwelashwa, kuzodingeka ubone udokotela wakho njalo - futhi mhlawumbe odokotela abaningi, kuye ngokuthi yiziphi izitho ezibuthintekile - ukuqapha isimo sakho.

Uma isimo sakho siqondiswe, ungase uqhubeke usebenzisa imithi ethile isikhathi eside ukuvimbela ukubuyela kwesifo. Lezi zihlanganisa i-rituximab, i-methotrexate, i-azathioprine ne-mycophenolate.

Okwaziwa nangokuthi i-plasmapheresis, leli thina liqeda ingxenye eyi-liquid yegazi lakho (i-plasma) enezihlanganisi ezibangela izifo. Uthola i-plasma entsha noma i-protein eyenziwa yi-liver (i-albumin), okuvumela umzimba wakho ukuba wenze i-plasma entsha. Kubantu abane granulomatosis enkulu kakhulu nge polyangiitis, i-plasmapheresis ingasiza izinso ziphulukiswe.

Ngokwelashwa cishe uzophulukiswa yi granulomatosis nge polyangiitis. Ngisho noma kunjalo ungase uzizwe ucindezelekile ngokubuyela kwesifo noma umonakalo esingawubangela. Nansi eminye imibono yokubhekana nalesi simo:

  • Qonda isimo sakho. Ukufunda nge granulomatosis nge polyangiitis kungakusiza ukubhekana nezinkinga, imiphumela emibi yemithi kanye nokubuyela kwesifo. Ngaphandle kokukhuluma nodokotela wakho, ungase ufune ukubonisana nomeluleki noma umsebenzi wokuxhumana kwezokwelapha.
  • Gcina isisekelo esiqinile sokusekela. Umuzi nabangane bangakusiza ukubhekana nalesi simo. Futhi ungase uthole ukuthi kubalulekile futhi kududuza ukukhuluma nabanye abantu abaphila nalesi simo. Buza ilungu leqembu lakho lokunakekelwa kwezempilo mayelana nokuthola iqembu lokusekela.

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Yenziwe eNdiya, yomhlaba