Health Library Logo

Health Library

Neurofibroma

Uhlolojikelele

I-neurofibroma uhlobo lwezimpukane zezinzwa ezingaphandle ezakha ibhumpu elithambile phezu noma ngaphansi kwesikhumba. I-tumor ingakhula ngaphakathi kwesinye sezitho ezinkulu noma ezincane zezinzwa noma kuphi emzimbeni. Lolu hlobo oluvamile lwezimpukane zezinzwa luqala ukukhula phakathi kwesinye sezitho zezinzwa. I-neurofibroma ikhula ekuvikelweni kwesinye sezitho zezinzwa, okuyaziwa ngokuthi yi-nerve sheath. Ngezinye izikhathi ikhula ezinhlotsheni eziningi zezinzwa. Uma lokhu kwenzeka, kubizwa ngokuthi yi-plexiform neurofibroma. I-neurofibroma ingabangela izimpawu ezilula noma kungabikho zimpawu nhlobo. Uma i-tumor icindezela ezinzwini noma ikhula ngaphakathi kwazo, ingabangela ubuhlungu noma ukungabi namqondo. Ngokuvamile i-neurofibroma ayisiye umdlavuza. Ngokungavamile, ingaba umdlavuza.

Izimpawu

I-neurofibroma lingase lingabangeli zimpawu. Uma kunezimpango, ngokuvamile ziyamila. Uma i-neurofibroma ikhula phezu noma ngaphansi kwesikhumba, izimpawu zingafaka: I-bump esikhumbeni. I-bump ingaba umbala wesikhumba sakho noma pinki noma tan. Ubuhlungu. Ukopha. Uma i-neurofibroma ikhula kakhulu noma icindezela noma ikhula phezu komthambo, izimpawu zingafaka: Ubuhlungu. Ukukhahlela. Ukungabi namandla noma ubuthakathaka. Ushintsho lokuqala uma i-neurofibroma enkulu isebusweni. Abanye abantu abane-neurofibromas banemethi yofuzo eyaziwa ngokuthi yi-neurofibromatosis uhlobo 1 (NF1). Umuntu onen NF1 angaba ne-neurofibromas eminingi. Inani le-neurofibromas likhula ngokwanda kweminyaka. Ukuqhuma okuhilela imithambo eminingi, okuqondwa ngokuthi yi-plexiform neurofibroma, kungaqala kumuntu onen NF1. Lolu hlobo lwe-neurofibroma lungakhula lube lukhulu futhi lubangele ubuhlungu. Futhi lingaba umdlavuza.

Izimbangela

I-neurofibroma lingase liqale ngaphandle kwesizathu esaziwayo, noma lingase libonakale kubantu abanemethi yofuzo ebizwa ngokuthi i-neurofibromatosis uhlobo 1. I-Neurofibromas ivame kakhulu kubantu abaneminyaka engama-20 ukuya kwangama-30 ubudala.

Izici eziyingozi

Isifaki esaziwayo kuphela sokungozakala kwe-neurofibromas ukuba nesimo se-genetic esaziwa ngokuthi yi-neurofibromatosis uhlobo 1 (NF1). Abantu abane-NF1 bane-neurofibromas eziningi, kanye nezinye izimpawu. Cishe kwesigamu sabantu abane-NF1, leli gciwane ladluliselwa kubazali. Noma kunjalo, abantu abaningi abane-neurofibromas abana-NF1.

Ukuxilongwa

Ukuthola i-neurofibroma, ochwepheshe bakho bezempilo bayakuhlola ngokomzimba futhi bahlole umlando wakho wezokwelapha.

Ungase udinga ukuhlolwa kwezithombe njenge-CT noma i-MRI scan. Izithombe zingasiza ukuthola indawo yomdlavuza. I-CT ne-MRI zingatholwa imidlavuza emincane kakhulu futhi zibonise ukuthi yiziphi izicubu ezibuthintekile. I-PET scan ingabonisa ukuthi umdlavuza ungumdlavuza. Umdlavuza ongenamdlavuza ubizwa ngokuthi ungumdlavuza oluhle.

Isibonelo se-neurofibroma singathengwa futhi sihlolwe ukuze kutholakale ukuxilongwa. Lokhu kubizwa ngokuthi yi-biopsy. I-biopsy ingase idingeke uma ukuhlinzwa kucabangwa njengokwelapha.

Ukwelashwa

Ukwelashwa kwe-neurofibroma akudingeki uma kune-tumor eyodwa engenazo izimpawu. Abachwepheshe bezempilo bavame ukulandelela i-neurofibroma. Ukuhlinzwa kungase kudingeke uma i-tumor ibangela izimpawu noma ngezizathu zokuhlobisa. Ukwelashwa kungafaka:

  • Ukulandelela. Uchwepheshe wakho wezempilo angase akukhuthaze ukubuka i-neurofibroma encane engabangeli zimpawu. Ukulandelela kungase futhi kunconywe uma i-neurofibroma ibangela izimpawu kodwa itholakala endaweni okwenza kube nzima ukuyisusa. Ukubuka kufaka ukuhlolwa okuvamile kanye nezivivinyo ze-imaging ukubona ukuthi i-tumor ikhula yini.
  • Imithi yokwelapha i-plexiform neurofibroma. I-Selumetinib (Koselugo) igunyazwe ukwelapha i-plexiform neurofibroma kubantwana abane-neurofibromatosis uhlobo 1. I-plexiform neurofibroma ikhula emithanjeni eminingi. Imithi inganciphisa i-tumor.
  • Izivivinyo zeklinikhi. Ungase ufanelekele ukuhlolwa kweklinikhi okuhlola ukwelashwa okuhlangenwe nakho.

Ikheli: 506/507, 1st Main Rd, Murugeshpalya, K R Garden, Bengaluru, Karnataka 560075

Umshwana wokuzihlangula: I-August iyinkundla yolwazi lwezempilo futhi izimpendulo zayo azihlanganisi iseluleko sezokwelapha. Njalo thintana nochwepheshe bezokwelapha onelayisensi eduze nawe ngaphambi kokwenza noma yiluphi ushintsho.

Yenziwe eNdiya, yomhlaba