Health Library Logo

Health Library

Pectus Excavatum

Uhlolojikelele

I-pectus excavatum yisimo lapho ithambo losifuba lomuntu lihlwithwe khona esifubeni sakhe. Izimo ezinzima ze-pectus excavatum ekugcineni zingaphazanyiswa ukusebenza kwenhliziyo nemiphunga.

Pectus excavatum yisimo lapho ithambo losifuba lomuntu lihlwithwe khona esifubeni. Kumacala anzima, i-pectus excavatum ingabonakala sengathi ukuphakathi kwesifuba kuqothulwe, kushiya umgodi ojulile.

Nakuba ithambo losifuba elihlwithwe liqapheleka ngokushesha ngemva kokuzalwa, ubukhulu be-pectus excavatum buvame ukuba sibi ngesikhathi sokuqhuma kokukhula kwentsha.

Okubizwa nangokuthi isifuba esinjengefunnel, i-pectus excavatum ivame kakhulu kubafana kunabentombazane. Izimo ezinzima ze-pectus excavatum zingaphazanyiswa ukusebenza kwenhliziyo nemiphunga. Kodwa ngisho namacala amancane e-pectus excavatum angenza abantwana bazizwe benesithukutheki ngokubonakala kwabo. Ukuhlinzwa kungalungisa ukungapheleli kwesimo.

Izimpawu

Kubantu abaningi abane-pectus excavatum, uphawu olulodwa kuphela noma isimo yindlebe encane esifubeni sabo. Kwabanye abantu, ukujula kwendlebe kuya ngokwanda ekuqaleni kwesikhathi sokuthomba futhi kungaqhubeka nokubi ngokwanda ebuhleni. Emacaleni aqatha e-pectus excavatum, ithambo lesifuba lingacindezela amaphaphu nenhliziyo. Izimpawu nezimpawu zingafaka: Ukunciphisa ukubekezelela komzimba; Ukuphefumula okusheshayo noma ukushaya kwenhliziyo; Ukutheleleka okuphindaphindayo kokuphefumula; Ukukhwehlela noma ukukhokhla; Ubuhlungu besifuba; Ukukhishwa kwenhliziyo; Ukukhathala; Ukukhungatheka.

Izimbangela

Nakuba imbangela eqondile ye-pectus excavatum ingaziwa, kungenzeka ukuthi iyisimo esidluliselwa ezizukulwaneni ngoba ngezinye izikhathi ivela emindenini.

Izici eziyingozi

I-pectus excavatum livame kakhulu kubafana kunamantombazane. Livela njalo kakhulu kubantu abane:

  • Uhlobo lukaMarfan
  • Uhlobo luka-Ehlers-Danlos
  • I-Osteogenesis imperfecta
  • I-Noonan syndrome
  • I-Turner syndrome
Izingqinamba

Abantu abaningi abane-pectus excavatum bazobe futhi bekhombisa isimo sokuma sikhonkco, ngama-ribs asele ahlukanile nama-shoulder blades. Abaningi bayazithoba kakhulu ngokubonakala kwabo kangangokuba bagwema imisebenzi lapho isifuba sabo singabonakala khona, njengokubhukuda. Bangagwema futhi izingubo ezenza kube nzima ukufihla ukucindezeleka esihlathini sabo.

Ukuxilongwa

I-Pectus excavatum ivame ukuxilongwa ngokuhlola nje isifuba. Udokotela wakho angakuncoma izinhlobo eziningana zezivivinyo ukuhlola izinkinga ezihambisana nayo zenhliziyo nemiphunga. Lezi zihloko zingafaka:

  • Umthunzi we-X-ray wesifuba. Lo mvivinyo ungabonisa ukucwilisa ngaphakathi kwesifuba futhi uvame ukubonisa inhliziyo ihambile ohlangothini lwesobunxele sesifuba. I-X-ray ayinazinkinga futhi ithatha imizuzu embalwa kuphela ukuyiqeda.
  • I-Electrocardiogram. I-electrocardiogram ingabonisa ukuthi izinga lenhliziyo liqondile noma aliqondile, futhi uma izibonakaliso zamandla ezilawula ukushaya kwenhliziyo zilinganiselwe kahle. Lo mvivinyo awuna ubuhlungu futhi uhilela ukufakwa kwezinkomba zamandla ezingaphezu kweshumi nambili, ezinamathele emzimbeni ngokunamathela okunamathisela.
  • Ukuhlolwa kokusebenza kwemiphunga. Lezi zinhlobo zezivivinyo zilinganisa inani lomoya omiphunga yakho ongawugcina nokuthi ungawukhulula ngokushesha kangakanani imiphunga yakho.
  • Uvivinyo lokusebenza komzimba. Lo mvivinyo uqapha ukuthi inhliziyo nemiphunga yakho isebenza kahle kangakanani ngenkathi uzivocavoca, ngokuvamile ebhayisikili noma etreadmill.
Ukwelashwa

I-Pectus excavatum lingalungiswa ngokuhlinzwa, kodwa ukuhlinzwa kuvame ukugcinelwa abantu abanemiboniso nezimpawu ezinzima noma eziphakathi. Abantu abanemiboniso nezimpawu ezincane bangasizakala ngokuqeqeshwa komzimba. Izikhali ezithile zingathuthukisa isimo somzimba futhi zande amazinga okuqhakazeka kwesifuba.

Izindlela ezimbili ezivame kakhulu zokulungisa i-pectus excavatum ziyaziwa ngamagama ochwepheshe abaqale bazihlakulela:

  • Ubuchwepheshe bukaRavitch. Le ndlela endala ihilela isiqeshana esikhulu kakhulu phansi kwesifuba. Uchwepheshe ukhulula uthango olukhubazekile oluhlanganisa ama-ribs ku-breastbone engezansi bese ulungisa i-breastbone esimweni esijwayelekile ngezinto zokulungisa, njengoba kuwukusekela okwenziwe ngensimbi noma i-mesh. Lokhu kusekelwa kususwa ngemuva kwezinyanga eziyi-12.

Abantu abaningi abenza ukuhlinzwa kokulungisa i-pectus excavatum bayajabula ngokushintsha indlela izifuba zabo ezibukeka ngayo, kungakhathaliseki ukuthi iyiphi inqubo esetshenziswayo. Nakuba ukuhlinzwa okuningi kwe-pectus excavatum kwenziwa ngesikhathi sokuqhakazeka kweminyaka yobudala, abantu abadala abaningi nabo baye bazuza ekulungisweni kwe-pectus excavatum.

Kunezindlela eziningi zokulawula ubuhlungu ngemuva kokuhlinzwa ukuze kusize ukuthuthukisa impilo. I-Cryoablation i-freeze i-nerves okwesikhashana ukuvimba ubuhlungu ngemuva kokuhlinzwa futhi ingasiza ngokutakula nokunciphisa ubuhlungu ngemuva kokuhlinzwa amasonto angu-4 kuya kwangu-6.

Senza ukulungiswa kokukhubazeka kodonga lwesifuba, okuthiwa yi-pectus excavatum.

UDkt. Dawn Jaroszewski unguchwepheshe we-thoracic, oqeqeshwe ekulungiseni i-pectus.

Kwakukholelwa ukuthi lezi zinkinga zokukhubazeka zazingokuhlobisa futhi azinawo umthelela kusigulane. Manje, sifumanisa ukuthi abantu bangaba nezinkinga ezinzima kakhulu zenhliziyo nemiphunga.

Eminyakeni embalwa edlule, ngithuthukise ukukhokha okuncane okukhulu.

UMichelle Kroeger wayenecala elithambile le-pectus elenza kwaba sibi ngokuhamba kwesikhathi.

Uma ngigijima, kwaba nzima kakhulu. Ngangingena moya. Khona-ke ngangiqala ukuba nokubetha okuningi enhliziyweni yami, ubuhlungu besifuba.

Ungabona lapha isikhala esincane phakathi komgogodla wakhe lapha nesifuba sakhe.

Okokuqala, uDkt. Jaroszewski wenza izinsiza ezincane ngakwesokunxele nangesokudla kwesiguli. Bese, eqondiswa yikhamera encane, ufake amabha aphakamisa udonga lwesifuba esimweni esijwayelekile.

Lena yi-x-ray, ebonisa umuntu omdala amabha amabili nokulungiswa okuhle.

Amabha afana ne-braces. UMichelle uzowagcina cishe iminyaka emibili. Uma ephuma, isifu sakhe sizogcina ukuma kwaso okusha. Manje, angaqhubeka nokuphila kwakhe okumatasa engenazo izimpawu.

Intsha eningi ifuna nje ukufana futhi ibukeke njengabangane bayo. Lokhu kungaba nzima kakhulu kubantwana abanepectus excavatum. Ezimweni ezithile, ukwelulekwa kungadingeka ukuze kusize ekuqeqeshweni amakhono okuqondana. Amaqembu wokusekela online namaforamu nawo ayafika, lapho ungakhuluma nabantu ababhekene nezinhlobo ezifanayo zezinkinga.

Ikheli: 506/507, 1st Main Rd, Murugeshpalya, K R Garden, Bengaluru, Karnataka 560075

Umshwana wokuzihlangula: I-August iyinkundla yolwazi lwezempilo futhi izimpendulo zayo azihlanganisi iseluleko sezokwelapha. Njalo thintana nochwepheshe bezokwelapha onelayisensi eduze nawe ngaphambi kokwenza noma yiluphi ushintsho.

Yenziwe eNdiya, yomhlaba