Ukuthini i-Progressive Supranuclear Palsy? Izimpawu, Izimbangela, kanye Nokwelashwa

I-Progressive supranuclear palsy (PSP) iyisifo esingavamile sobuchopho esithinta ukunyakaza, ibhalansi, inkulumo, kanye nokulawula amehlo. Kwenzeka lapho amaseli athile ebuchopho ewohloka ngokuhamba kwesikhathi, ikakhulukazi ezindaweni eziqondisa lezi zisebenzi ezibalulekile.

Cabanga ngebuchopho bakho njengoba unezindawo ezahlukene zokulawula imisebenzi ehlukahlukene. I-PSP yonakalisa ngokukhethekile izindawo ezibhekene nokuhlanganisa ukunyakaza kwakho nokulondoloza ibhalansi yakho. Nakuba ihlanganyela izinto ezithile ne-Parkinson's disease, i-PSP inephethini yayo ehlukile yezimpawu nokuqhubeka kwayo.

Zithini izimpawu ze-Progressive Supranuclear Palsy?

Izimpawu ze-PSP zivame ukuqala kancane kancane futhi zingabahlukahlukene kakhulu. Izimpawu zokuqala ezibonakala kakhulu zivame ukubandakanya izinkinga ngebhalansi nokuhamba kwamehlo, nakuba okuhlangenwe nakho kwabantu bonke kungabahlukile.

Nawa izimpawu eziyinhloko ongaziqaphela:

• Izinkinga zebhalansi nokuwa okuvamile - Ukuwa ngemuva okuvela ngokungazelelwe
• Ubunzima bokuhamba kwamehlo - Ubunzima bokubuka phezulu noma phansi, ukubona okungacace, noma izinkinga zokugxila
• Ukuqina nokuhamba okuhamba kancane - Ikakhulukazi endaweni yentamo nomzimba
• Ukushintsha kwenkulumo - Inkulumo ephazamisekile, ubunzima bokuqamba amagama, noma ukushintsha komthamo wezwi
• Izinkinga zokugwinya - Ubunzima ngamanzi noma ukudla okuqinile
• Ukushintsha kokucinga - Izinkinga zokugxila, ukwenza izinqumo, noma ukukhumbula
• Ukuphazamiseka kokulala - Ukungalali ubuthongo noma ukushintsha kwemizamo yokulala
• Ukushintsha kwesimo sengqondo - Usizi, intukuthelo, noma ukuqhuma komzwelo

Izinkinga zokunyakaza kwamehlo zivame ukuba yilokho okuhlukanisa i-PSP kwezinye izimo. Ungase uthole kunzima ukubuka phansi uma uhamba phansi noma ube nobunzima bokuhambisa ukubuka kwakho ngokushesha phakathi kwezinto.

Ezimweni ezingavamile, abanye abantu bahlangabezana nezimpawu ezingavamile njengokuhleka noma ukukhala okungenakulawuleka, ukukhanya okukhulu, noma ukushintsha okukhulu komuntu okubonakala kungekho emvelweni.

Zithini izinhlobo ze-Progressive Supranuclear Palsy?

I-PSP iza ngezindlela eziningi ezahlukene, ngayinye inephethini yayo yezimpawu. Uhlobo oluvamile kakhulu, kodwa ukuqonda ukwahluka kungakusiza uqonde ukuthi yini ongahlangabezana nayo.

I-Classic PSP (Richardson's syndrome) uhlobo oluvamile kakhulu. Ngokuvamile iqala ngezinkinga zebhalansi nokuwa ngemuva, kulandele ubunzima bokuhamba kwamehlo nokuqina entanyeni nomzimba.

I-PSP-Parkinsonism ibukeka ifana ne-Parkinson's disease emazingeni okuqala. Ungase uqaphele ukuzamazama, ukunyakaza okuhamba kancane, nokuqina okuphendula ngandlela-thile emithi ye-Parkinson's.

I-PSP enezimpawu eziphambili ze-frontal ithinta ikakhulukazi ukucabanga nokuziphatha kuqala. Ukushintsha komuntu, ukwenza izinqumo, noma ulimi kungaba izimpawu zokuqala kunokunyakaza okunzima.

Izinhlobo ezingavamile zihlanganisa i-PSP enezinkinga zokukhuluma nolimi njengophawu oluyinhloko, noma izinhlobo ezithinta ikakhulukazi izindlela zokunyakaza ezithile. Udokotela wakho angakusiza aqonde ukuthi yiluphi uhlobo oluchaza kangcono izimpawu zakho.

Yini ebangela i-Progressive Supranuclear Palsy?

I-PSP kwenzeka lapho iprotheni ebizwa nge-tau iqala ukwakheka ngokungavamile kumaseli athile ebuchopho. Le protheni ngokuvamile iyasiza ukulondoloza ubukhulu bamaseli ebuchopho, kodwa ku-PSP, ihlanganisana ndawonye futhi yonakalise amaseli ngokuhamba kwesikhathi.

Isizathu esiqondile sokuthi kungani i-tau iqala ukuqoqwa asiqondwa ngokugcwele. Izimo eziningi zibonakala zingenangqondo, okusho ukuthi zenzeka ngokungahleliwe ngaphandle komlando womndeni ocacile noma isithintelo sendawo.

Ezimweni ezingavamile kakhulu, i-PSP ingadluliselwa emindenini ngenxa ye-genetic mutations. Noma kunjalo, lokhu kubalwa ngaphansi kuka-1% lazo zonke izimo ze-PSP. Ukuba nelungu lomndeni elithola i-PSP akukhuphuli kakhulu ingozi yakho yokuthola lesi simo.

Ucwaningo oluthile luphakamisa ukuthi ukwahluka okukhethekile kwe-genetic kungenza umuntu abe semngciphekweni omncane we-PSP, kodwa lokhu kuyizinguquko ezivamile abantu abaningi abazithwala ngaphandle kokuthola isifo.

Izici zendawo ezifana nokulimala kwekhanda noma ukukhishwa ezintweni ezithile ezinobuthi kuye kwafundwa, kodwa azikho izixhumanisi ezicacile eziye zakhiwa. Iqiniso liwukuthi i-PSP ibonakala ithuthukiswa ngokuhlanganiswa okuyinkimbinkimbi kwezici ezaziqondwa yizazi zezesayensi.

Nini okufanele ubheke udokotela nge-Progressive Supranuclear Palsy?

Kufanele ucabange ukuya kudokotela uma uhlangabezana nezinkinga zebhalansi ezingachazwanga, ikakhulukazi uma uqale ukuwa ngemuva. Lezi zimpawu zokuqala zidinga ukunakekelwa, ngisho noma zibonakala zingenamandla.

Ezinye izimpawu ezinkulu ezidinga ukuhlolwa yi-medical zihlanganisa izinkinga eziqhubekayo ngokunyakaza kwamehlo, njengobunzima bokubuka phezulu noma phansi, noma ubunzima bokuqondisa ukubona kwakho. Ukushintsha kwesitayela sakho senkulumo noma ukwanda kobunzima bokugwinya kubalulekile ukukuxoxa.

Uma uqaphela ukuqina okukhulu entanyeni yakho noma emzimbeni wakho okuthinta imisebenzi yakho yansuku zonke, noma uma uhlangabezana nokushintsha komuntu okubonakala kungekho emvelweni, lokhu kungaba izimpawu zokuqala ezifanele ukuhlolwa.

Ungalindi uma uhlangabezana nezimpawu eziningi ndawonye. Ukuhlanganiswa kwezinkinga zebhalansi, ubunzima bokuhamba kwamehlo, nokushintsha kwenkulumo kubalulekile ukukuhlola ngokushesha.

Khumbula, izimpawu eziningi zingaba nezinye izincazelo, futhi ukubona udokotela ngokushesha kungasiza ukukhipha izimo ezilawuleka noma ukunikeza ukunakekelwa okusekela okuthuthukisa ikhwalithi yempilo yakho.

Zithini izici ezingozi ze-Progressive Supranuclear Palsy?

I-PSP ikakhulukazi ithinta abantu abaseminyakeni yabo engama-60 nama-70, nakuba ingase ibonakale kubantu abancane. Ubudala yiyona nto ebaluleke kakhulu yengozi esiyaziyo.

Nawa ama-risk factors ayinhloko aqunyiwe ucwaningo:

• Ubudala - Abantu abaningi baqalwa phakathi kweminyaka engama-60-70
• Ubulili - Amadoda avame kakhulu ukuthola i-PSP kunabesifazane
• Ukwahluka okukhethekile kwe-genetic - Ezinye izinguquko ze-gene ezivamile zingase zikhulise kancane ingozi
• I-Geography - Ezinye izindawo zibonisa amazinga aphezulu, nakuba izizathu zingacaci

Ngokungafani nezinye izimo ze-neurological, i-PSP ayibonakali ihlotshaniswa kakhulu nezici zokuphila ezifana nokudla, ukuzivocavoca, noma ukubhema. Umlando womndeni awuvamile, njengoba izimo eziningi zenzeka ngokungahleliwe.

Ucwaningo oluthile luye lwabuka ukuthi ukulimala kwekhanda kungase kukhulise ingozi, kodwa ubufakazi abunamandla ngokwanele ukudweba iziphetho ezicacile. Okufanayo kuya kulokho okuvezwe ezintweni ezithile ezinobuthi.

Kubalulekile ukuqonda ukuthi ukuba nama-risk factors akusho ukuthi uzothola i-PSP. Abantu abaningi abanamazinga aphansi abakutholi lesi simo, kanti abanye abangenazo izici ezingozi ezicacile bayakuthola.

Zithini izinhlanganisela ezingaba khona ze-Progressive Supranuclear Palsy?

Njengoba i-PSP iqhubeka, izinhlanganisela eziningi zingathuthuka ezithinta izici ezahlukene zokuphila kwansuku zonke. Ukuqonda lezi zinto ezingaba khona kungakusiza wena nomndeni wakho ukulungiselela nokufuna ukwesekwa okufanele.

Ukukhathazeka okukhulu kuvame ukuphathelene nokulondeka nokuhamba:

• Ukuwanda kengozi yokuwa - Izinkinga zebhalansi ziyaqhubeka ngokuhamba kwesikhathi, okuholela ekuweni okuvamile nokubi kakhulu
• Ubunzima bokugwinya - Kungabangela ukuminyana, ukungondliwe kahle, noma i-pneumonia ngokudla okungena emaphashini
• Izinkinga zokukhuluma - Kungathuthuka ubunzima bokuhlanganisa izidingo nemizwa
• Izinkinga zobono - Izinkinga zokunyakaza kwamehlo zingenza ukufunda, ukuqhuba, noma ukuhamba ngezitebhisi kube yingozi

Njengoba isimo siqhubeka, izinhlanganisela eziyinkimbinkimbi kakhulu zingavela. Lokhu kungase kuhlanganise ukulinganiselwa okukhulu kokunyakaza okudinga amadivayisi okusiza noma izitulo zezithuthuthu, nokukhulu kobunzima ngemisebenzi yokunakekela uqobo njengokuhlanza noma ukugqoka.

Ukushintsha kokucinga kungase kube khulu ngokuhamba kwesikhathi, okuthinta ukukhumbula, ukuxazulula izinkinga, namandla okwenza izinqumo. Ukuphazamiseka kokulala kungase kube kubi kakhulu, okuthinta impilo yonke kanye nekhalithi yempilo.

Ezimweni ezingavamile, abanye abantu bathuthukisa izinhlanganisela ezinkulu ezifana nobunzima obukhulu bokuqeda umoya noma ukulahlekelwa ngokuphelele kokunyakaza kwamehlo okuzithandelayo. Noma kunjalo, abantu abaningi abane-PSP baqhubeka belondoloza ubuhlobo obukhulu futhi bathola izindlela zokuzivumelanisa namandla abo ashintshayo.

I-Progressive Supranuclear Palsy ihlonishwa kanjani?

Ukuhlonishwa kwe-PSP kungaba inselele ngoba izimpawu zayo zihlangana nezinye izimo ezifana ne-Parkinson's disease. Udokotela wakho ngokuvamile uzoqala ngomlando wezokwelapha onemininingwane kanye nokuhlolwa komzimba okuqondene nokuhamba kwakho, ibhalansi, kanye nomsebenzi wamehlo.

Alukho uvivinyo olulodwa olungabonisa i-PSP ngokuqinisekile. Esikhundleni salokho, odokotela basebenzisa izindinganiso zezokwelapha eziqondene nezimpawu zakho nokuthi zithuthukile kanjani ngokuhamba kwesikhathi. Ukuhlonishwa kuvame ukubizwa ngokuthi "i-PSP enokwenzeka" kunokuba kuqinisekile.

Udokotela wakho angase ayalele izifundo zokubonisa ubuchopho ezifana ne-MRI ukubuka izinguquko ezithile esakhiweni sobuchopho. Ku-PSP, ezinye izindawo ze-brainstem zingase zibonise ukunciphisa okukhethekile noma ukushintsha okusekela ukuhlonishwa.

Ngezinye izikhathi kuyadingeka ukuhlolwa okuengeziwe ukukhipha ezinye izimo. Lokhu kungase kuhlanganise ukuhlolwa kwegazi ukuhlola ezinye izimbangela zezinkinga zokunyakaza, noma ukuskena okukhethekile okubuka umsebenzi wobuchopho kunokuba nje isakhiwo.

Inqubo yokuhlola ingathatha isikhathi, futhi ungase udinge ukubona ochwepheshe abanjengo-neurologists abanokuhlangenwe nakho ngezifo zokunyakaza. Ungadangali uma ukuhlonishwa kungekho ngokushesha - ukubuka ngokucophelela ukuthi izimpawu zishintsha kanjani ngokuhamba kwesikhathi kuvame ukunikeza isithombe esicacile.

Yini ukwelashwa kwe-Progressive Supranuclear Palsy?

Okwamanje, asikho isiphilisi se-PSP, kodwa ukwelashwa okuhlukahlukene kungasiza ukuphatha izimpawu nokuthuthukisa ikhwalithi yempilo. Indlela igxile ekunakekeleni izinkinga ezithile njengoba zivele futhi kulondolozwe umsebenzi isikhathi eside ngangokunokwenzeka.

Imithi esetshenziswa ye-Parkinson's disease ngezinye izikhathi inikeza izinzuzo ezincane, ikakhulukazi kubantu abane-PSP-Parkinsonism type. Noma kunjalo, impendulo ivame ukulinganiselwa futhi ibe yisikhashana uma iqhathaniswa ne-Parkinson's disease evamile.

I-Physical therapy idlala indima ebalulekile ekugcineni ukuhamba nokuvimbela ukuwa. Umqeqeshi wakho angakufundisa imizamo ekhethekile yokuthuthukisa ibhalansi, uqinise imisipha, futhi ulondoloze ukuguquguquka. Bayakusiza futhi ufunde amasu okuhamba ngokuphepha.

I-Speech therapy iba yibalulekile lapho izinkinga zokukhuluma noma ukugwinya zithuthuka. Umqeqeshi wezwi angakufundisa amasu okukhuluma ngokucacile nangokuphepha, okungenzeka ukuvimbela izinhlanganisela ezifana ne-pneumonia.

I-Occupational therapy ikusiza ukulungisa imisebenzi yansuku zonke kanye nendawo yakho yokuhlala ukuze uvumelane namandla ashintshayo. Lokhu kungase kuhlanganise ukuncoma amadivayisi okusiza noma ukulungisa ikhaya lakho ngokuphepha.

Ngezimpawu ezithile, ukwelashwa okuqondiswe kutholakala. Izinkinga zokunyakaza kwamehlo zingase zisizwe ngamagalasi akhethekile noma imizamo yamehlo. Ukuphazamiseka kokulala kuvame ukuthuthukiswa ngamathani wokulala noma imithi.

Ungayiphatha kanjani i-Progressive Supranuclear Palsy ekhaya?

Ukudala indawo yekhaya ephephile futhi esekelayo kungenza umehluko omkhulu ekuphatheni izimpawu ze-PSP. Qala ngokususa izingozi zokuwa ezifana nama-rugs ahlangene, uthuthukise ukukhanya, futhi ufake ama-grab bars ezihlanzini nasezitebhisi.

Yakha izindlela zansuku zonke ezisebenza ngezimpawu zakho kunokuba zimelane nazo. Abantu abaningi bathola ukuthi bane-balance engcono namandla ngezikhathi ezithile zosuku, ngakho hlela imisebenzi ebalulekile ngalezi zikhathi eziphezulu.

Ngezinhlungu zokugwinya, gxila ekudleni kancane futhi ukhethe ukudla okunezakhiwo ezifanele. Amanzi ahlanganisiwe noma ukudla okumnene kungase kube lula ukulawula ngokuphepha. Yidla uhlale uqonde futhi ugweme ukuhlubuka ngesikhathi sokudla.

Hlala usebenza ngokomzimba ngangokunokwenzeka isimo sakho siyakuvumela. Ngisho nemizamo emnene njengokuhamba, ukuqina, noma imizamo yesitulo ingasiza ukulondoloza amandla nokuqina. Hlala uqaphela ukuphepha futhi ucabange ngokusebenzisa amadivayisi okusiza uma kudingeka.

Londoloza uxhumano lwentlalo futhi uhlanganyele emisebenzini oyithandayo, uyilungise njengoba kudingeka. Lokhu kungase kusho ukusebenzisa ama-audiobooks esikhundleni sokufunda, noma ukuthola imisebenzi emisha esebenza namandla akho wamanje.

Ungangabazi ukucela usizo ngemisebenzi yansuku zonke. Ukwamukela usizo akusona ukuyeka - ukuba uhlakaniphile ngokulondoloza amandla ezintweni ezibaluleke kakhulu kuwe.

Kufanele ulungiselele kanjani i-appointment yakho yedokotela?

Ngaphambi kwe-appointment yakho, bhala zonke izimpawu zakho, kufaka phakathi ukuthi zaqala nini nokuthi zishintshile kanjani ngokuhamba kwesikhathi. Yiba uchwepheshe ngalokho oqaphele - ngisho nezindaba ezincane zingabalulekile ekuhlonishweni.

Letha uhlu oluphelele lwemithi yonke oyithathayo, kufaka phakathi imithi yokuthengwa ngaphandle komthetho kanye nezinhlanganisela. Lungiselela futhi uhlu lwezinye izimo zezokwelapha onazo nomlando wezokwelapha womndeni wakho.

Cabanga ukuletha ilungu lomndeni noma umngani obeqaphele izimpawu zakho. Bangase baqaphele izinto oziphuthelwe noma bakusize ukukhumbula imininingwane ebalulekile ngesikhathi se-appointment.

Lungiselela imibuzo kusengaphambili. Ungase ufune ukubuza ngenqubo yokuhlola, izinketho zokwelapha, lokho okufanele ukulindele njengoba isimo siqhubeka, noma izinsiza zokusekela nolwazi.

Uma kungenzeka, letha noma yimaphi amarekhodi ezokwelapha adlule noma imiphumela yokuhlola ehlobene nezimpawu zakho. Lokhu kungasiza udokotela wakho ukuqonda umlando wakho wezokwelapha futhi ugweme ukuphinda ukuhlolwa okungadingekile.

Yini okuyinhloko nge-Progressive Supranuclear Palsy?

I-PSP iyisimo esiyinselele, kodwa ukuyiqonda kukusiza wenze izinqumo ezilwemi ngokunakekelwa kwakho. Nakuba kungenakho isiphilisi okwamanje, ukwelashwa okuningi namasu angasiza ukuphatha izimpawu nokugcina ikhwalithi yempilo.

Into ebaluleke kakhulu okumele uyikhumbule iwukuthi i-PSP ithinta wonke umuntu ngokuhlukile. Okuhlangenwe nakho kwakho kungase kungafani nalokho okufundayo noma lokho abanye abakuchazayo. Gxila ezimpawu zakho futhi usebenze neqembu lakho lokunakekelwa kwezempilo ukunakekela izidingo zakho ezithile.

Ukuhlonishwa kokuqala nokungenelela kungenza umehluko wangempela ekuphatheni lesi simo. Ungalihli ukufuna ukunakekelwa kwezokwelapha uma uhlangabezana nezimpawu ezinkulu, futhi ungangabazi ukufuna imibono yesibili uma kudingeka.

Ukukwakha inethiwekhi eqinile yokusekela yomndeni, abangane, nochwepheshe bezempilo kubalulekile. I-PSP ayisiyo uhambo okufanele uhlangane nalo wedwa, futhi izinsiza eziningi ziyatholakala ukukusiza wena nabathandekayo bakho ukubhekana nezinselele ezizayo.

Imibuzo evamile ebuzwayo nge-Progressive Supranuclear Palsy

Q1: Abantu baphila isikhathi esingakanani bephethe i-Progressive Supranuclear Palsy?

Ukuqhubeka kwe-PSP kuyahlukahluka kakhulu phakathi kwabantu, kodwa abantu abaningi baphila iminyaka engama-6-10 ngemuva kokuba izimpawu ziqale. Abanye abantu bangase babe nokuqhubeka okuhamba kancane futhi baphile isikhathi eside, kanti abanye bangase baqhubeke ngokushesha. Okubalulekile ukugxila ekhwalithi yempilo nokwenza okuningi ngesikhathi sakho ngokunakekelwa kwezokwelapha okufanele nokusekelwa.

Q2: Ingabe i-Progressive Supranuclear Palsy iyefa?

I-PSP ayivamile ukudluliselwa. Ngaphansi kuka-1% yezimo kuyizimo zomndeni, okusho ukuthi zidluliselwa emindenini. Izimo eziningi zenzeka ngokungahleliwe ngaphandle komlando womndeni. Ukuba nomuntu omkhulu one-PSP akukhuphuli kakhulu ingozi yakho yokuthola lesi simo.

Q3: Ingabe i-Progressive Supranuclear Palsy ingaphambukiswa kwezinye izimo?

Yebo, i-PSP ivame ukuqala ukungalahleka njenge-Parkinson's disease, i-Alzheimer's disease, noma ezinye izifo zokunyakaza ngoba izimpawu zingase zihlangane. Izinkinga zokunyakaza kwamehlo ezihlukile nephethini yokuwa ngokuvamile zisiza odokotela ukwahlukanisa i-PSP kulezi zimo ezinye ngokuhamba kwesikhathi.

Q4: Ingabe kukhona ukwelashwa okusha okuhlolwa kwe-PSP?

Ukwelashwa okuningi okuthenjisayo okwamanje kusevivinyweni lezokwelapha, kufaka phakathi imithi ehlose ukwakheka kwe-tau protein kanye nezinqubo ezinhloso zokulinda amaseli ebuchopho. Nakuba kungenakho ukwelashwa okuphumelelayo okwamanje, ucwaningo oluqhubekayo lunikeza ithemba lezinketho ezinhle zokuphatha esikhathini esizayo.

Q5: Ingabe ukushintsha kokuphila kungasiza ngezimpawu ze-PSP?

Nakuba ukushintsha kokuphila kungenakunciphisa ukuqhubeka kwe-PSP, kungathuthukisa kakhulu ikhwalithi yempilo. I-Physical therapy ejwayelekile, ukugcina uxhumano lwentlalo, ukudla ukudla okunomsoco, nokudala indawo yekhaya ephephile konke kusiza ukuphatha izimpawu nokugcina ukuzimela isikhathi eside ngangokunokwenzeka.