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Vasculitis

Uhlolojikelele

I-Vasculitis ihilela ukuvuvukala kwezitho eziphatha igazi. Ukuvuvukala kungabangela ukuba izindonga zezitho eziphatha igazi ziqine, okunciphisa ububanzi bendlela ehamba ngayo igazi esithweni. Uma ukugeleza kwegazi kunqanyuliwe, kungabangela ukonakala kwamalungu nomzimba.

Kunezinhlobo eziningi ze-vasculitis, futhi iningi lazo liyimfihlo. I-Vasculitis ingathinta ilungu elilodwa, noma eziningi. Isimo singaba sesikhathi esifushane noma isikhathi eside.

I-Vasculitis ingathinta noma ubani, yize ezinye izinhlobo zivame kakhulu kubantu bezigaba ezahlukene zokuzalwa. Kuye ngohlobo olukhona, ungase uthuthuke ngaphandle kokwelashwa. Izinhlobo eziningi zidinga imithi yokulawula ukuvuvukala nokuvimbela ukubhebhetheka.

Izimpawu

Izimpawu ezijwayelekile nezinhlungu zezinye izinhlobo ze-vasculitis zifaka: Ukushisa Intloko Ukukhathala Ukulahlekelwa isisindo Ubuhlungu bomzimba jikelele Ezinye izimpawu zihambisana nezingxenye zomzimba ezihilelekile, kufaka phakathi: Isistimu yokugaya. Uma isisu sakho noma amabele akho ehilelekile, ungase ube nobuhlungu ngemva kokudla. I-Ulcers kanye ne-perforations kungenzeka futhi kungabangela igazi emathunjini. Amakhanda. Ukuqina, ukukhala emakhanda nokulahlekelwa ukuzwa okusheshayo kungase kwenzeke. Amehlo. I-Vasculitis ingenza amehlo akho abonakale abomvu futhi akhube noma ashisiwe. I-Giant cell arteritis ingabangela ukubona okukabili nokulahlekelwa ukubona okwesikhashana noma okungapheli elinye noma womabili amehlo. Ngakho-ke ngezinye izikhathi yiyona impawu yokuqala yesifo. Pandla noma izinyawo. Ezinye izinhlobo ze-vasculitis zingabangela ukungabi namandla noma ubuthakathaka esandleni noma enyaweni. Izandla kanye nezinyawo zingase zifuvuke noma ziqine. Amaphaphu. Ungase ube nokuqina kokuphefumula noma ukhwehle igazi uma i-vasculitis ihilela amaphaphu akho. Isikhumba. Ukuphuza igazi phansi kwesikhumba kungabonakala njengemibala ebomvu. I-Vasculitis ingabangela futhi ama-lumps noma ama-sores avulekile esikhumbeni sakho. Yenza i-aphoyintimenti nodokotela wakho uma unezimpawu noma izimpawu ezikukhathazayo. Ezinye izinhlobo ze-vasculitis zingaba sibi ngokushesha, ngakho-ke ukuxilongwa kwasekuqaleni kuyisihluthulelo sokuthola ukwelashwa okuphumelelayo.

Isikhathi sokubona udokotela

Yenza i-aphoyintimenti nodokotela wakho uma unezimpawu noma izimpawu ezikukhathazayo. Ezinye izinhlobo ze-vasculitis zingaba zimbi ngokushesha, ngakho-ke ukuxilongwa kwasekuqaleni kuyisihluthulelo sokuthola ukwelashwa okuphumelelayo.

Izimbangela

Imbangela eqondile ye-vasculitis ayiqondakali ngokuphelele. Amanye ama-type ahlobene nokwakheka kwe-genetic komuntu. Amanye aphuma ohlelo lwe-immune oluhlasele amaseli e-blood vessel ngephutha. Izimbangela ezingase zibangele le nhlangano ye-immune system zifaka:

  • Ukutheleleka, njenge-hepatitis B ne-hepatitis C
  • Ukuhlinzwa kwegazi
  • Izifo ze-immune system, njenge-rheumatoid arthritis, i-lupus ne-scleroderma
  • Ukusebenzisana nezinye izidakamizwa
Izici eziyingozi

I-Vasculitis ingathinta noma ubani. Izici ezingase zikhulise ingozi yezifo ezithile zihlanganisa:

  • Ubudala. I-Giant cell arteritis ayivame ukwenzeka ngaphambi kweminyaka engama-50, kuyilapho i-Kawasaki disease ivame kakhulu kubantwana abaneminyaka engaphansi kwengu-5.
  • Umlando womndeni. I-Behcet's disease, i-granulomatosis ene-polyangiitis ne-Kawasaki disease ngezinye izikhathi zidlulela emindenini.
  • Izinqumo zokuphila. Ukusebenzisa i-cocaine kungakhuphula ingozi yakho yokuthuthukisa i-vasculitis. Ukubhema utshaba, ikakhulu uma ungumuntu wesilisa oneminyaka engaphansi kwengu-45, kungakhuphula ingozi yakho ye-Buerger's disease.
  • Imithi. I-Vasculitis ngezinye izikhathi ingase iqalwe yimithi efana ne-hydralazine, i-allopurinol, i-minocycline ne-propylthiouracil.
  • Ukutheleleka. Ukuba ne-hepatitis B noma i-C kungakhuphula ingozi yakho ye-vasculitis.
  • Izifo ze-immune. Abantu abanazo izifo lapho ama-immune systems abo ehlasela imizimba yabo ngephutha bangase babe sengozini enkulu ye-vasculitis. Isibonelo sihlanganisa i-lupus, i-rheumatoid arthritis ne-scleroderma.
  • Ubulili. I-Giant cell arteritis ivame kakhulu kwabesifazane, kuyilapho i-Buerger's disease ivame kakhulu kumadoda.
Izingqinamba

Izinkinga ze-Vasculitis kuncike ohlotsheni nobunzima besimo sakho. Noma zingase zibe zihlobene nemiphumela emibi yemithi oyisebenzisayo ukwelapha isimo. Izinkinga ze-vasculitis zihlanganisa:

  • Ukuphazamiseka kwamalungu. Ezinye izinhlobo ze-vasculitis zingaba nzima, zibangele ukulimala kwamalungu amakhulu.
  • Iziqu egazini kanye ne-aneurysms. I-clot yegazi ingase ibe khona emithanjeni yegazi, ivinje ukugeleza kwegazi. Ngokungavamile, i-vasculitis izobangela ukuthi umthambo wegazi ubuthakathaka futhi uqale ukukhula, wakhe i-aneurysm (AN-yoo-riz-um).
  • Ukwehluleka kobono noma ubuthakathaka bebona. Lena ingxaki engenzeka ye-giant cell arteritis engaphathwe kahle.
  • Ukutheleleka. Ezinye zezidakamizwa ezisetshenziswa ekwelapheni i-vasculitis zingase zibuthakathaka uhlelo lwakho lokulwa nezifo. Lokhu kungakwenza ube sengozini yokutheleleka.

U-Andy Grundstad wayegula futhi ekhathele ukuzizwa egulisiwe futhi ekhathele. "Ngazizwa sengathi ngineminyaka engama-80," kusho u-Andy, oneminyaka engama-35 ubudala, umcwaningi wezolimo ohlala ngaphandle kweCrosby, eNorth Dakota. Wayekwaziswe nge-vasculitis esemncane futhi wahlala nezinkinga ezahlukahlukene zempilo ngenkathi amaqembu okunakekelwa elwa ukunikeza ukuxilongwa okubanzi nokuphathwa okuphumelelayo. Izimpawu zika-Andy zaba zimbi ngemuva kokushaya kwengqondo ngo-2017. Amaphaphu angama-daily kanye nobuhlungu bezingxenye zomzimba bahambisana nokushaya kwengqondo okwesibili ngo-2020…

Ukuxilongwa

Udokotela wakho cishe uzoqala ngokuthatha umlando wakho wezokwelapha nokwenza ukuhlolwa komzimba. Ungase akucingele ukuthi wenze izivivinyo nezinqubo zokuxilonga eziyodwa noma ngaphezulu ukuze ukhanyise ezinye izimo ezifanayo ne-vasculitis noma ukuxilonga i-vasculitis. Izivivinyo nezinqubo zingafaka:

  • Izivivinyo zegazi. Lezi zivivinyo zibheka izimpawu zokuvuvukala, njengamanqanaba aphezulu e-C-reactive protein. Ukubalwa kwamaseli egazi okuphelele kungabonisa ukuthi unezakhiwo ezinemininingwane ebomvu eyanele. Izivivinyo zegazi ezibheka ama-antibodies athile - njengovavanyo lwe-anti-neutrophil cytoplasmic antibody (ANCA) - zingasiza ekuxilongeni i-vasculitis.
  • Izivivinyo zobumfanekiso. Amathuluzi okubona angenawo ubuhlungu angasiza ekuqondeni ukuthi yiziphi izithelo zegazi namalungu omzimba athintekile. Angasiza futhi udokotela ukuba aqaphele ukuthi uyaphendula yini ekwelapheni. Izivivinyo zobumfanekiso ze-vasculitis zifaka i-X-rays, i-ultrasound, i-computerized tomography (CT), i-magnetic resonance imaging (MRI) ne-positron emission tomography (PET).
  • I-X-rays yezithelo zakho zegazi (angiography). Ngesikhathi senqubo, i-catheter eguquguqukayo, efana nesitayela esincinyane, ifakwa esitheleni esikhulu noma esithanjeni. Umenzi okhethekile ube usufakwe ku-catheter, futhi i-X-rays ithathwa njengoba umenzi ugcwalisa isithelo noma isithelo. Imigqa yezithelo zakho zegazi ibonakala ku-X-rays eziphumelelayo.
  • I-Biopsy. Lena inqubo yokucathulwa lapho udokotela wakho ekhipha khona isampula encane yethishu endaweni ethintekile yomzimba wakho. Udokotela wakho ube esehlola le tissu ukuze abone izimpawu ze-vasculitis.
Ukwelashwa

Ukuphathwa kugxile ekulawuleni ukuvuvukala nokuphatha noma yiziphi izimo ezingaphansi ezingase ziqalise i-vasculitis.

I-corticosteroid drug, efana ne-prednisone, uhlobo oluvamile kakhulu lwezidakamizwa ezirehwa ukulawula ukuvuvukala okuhlotshaniswa ne-vasculitis.

Imiphumela emibi ye-corticosteroids ingaba nzima, ikakhulukazi uma uyithatha isikhathi eside. Imiphumela emibi engenzeka ifaka ukwanda kwesisindo, isifo sikashukela namathambo abuthakathaka. Uma i-corticosteroid idingeka ekwelapheni isikhathi eside, cishe uzothola umthamo omncane ngangokunokwenzeka.

Eminye imithi ingabhalwa nge-corticosteroids ukulawula ukuvuvukala ukuze umthamo we-corticosteroids uqiniswe ngokushesha. Imithi esetshenziswayo ixhomeke ohlotsheni lwe-vasculitis ekhona. Le mithi ingafaka i-methotrexate (Trexall), i-azathioprine (Imuran, Azasan), i-mycophenolate (CellCept), i-cyclophosphamide, i-tocilizumab (Actemra) noma i-rituximab (Rituxan).

Imithi ethile ozoyidinga ixhomeke ohlotsheni nobunzima be-vasculitis onayo, izitho ezihilelekile, nanoma yiziphi ezinye izinkinga zezokwelapha onazo.

Esinye sezinkinga zakho ezinkulu zokuphila ne-vasculitis kungaba ukubhekana nemiphumela emibi yemithi yakho. Iziphakamiso ezilandelayo zingasiza:

  • Qonda isimo sakho. Funda konke ongakwazi nge-vasculitis nokuphathwa kwayo. Yazi imiphumela emibi engenzeka yemithi oyithatha, utshele udokotela wakho nganoma yiziphi izinguquko empilweni yakho.
  • Thola ukugoma okuvamile. Ukugcina usesikhathini ngokugoma, njengokwelapheka isifo sikagciwane ne-pneumonia, kungasiza ukuvimbela izinkinga ezingase ziphumelele emithini yakho, njengokuqanduseka. Xoxa nodokotela wakho ngokugoma.
  • Gcina isisekelo esiqinile sokusekela. Umuzi nabangane bangakusiza njengoba ubhekene naleli simo. Uma ucabanga ukuthi kuzoba usizo ukukhuluma nabanye abantu abaphila ne-vasculitis, cela ilungu leqembu lakho lokunakekelwa kwezempilo mayelana nokuthola iqembu lokusekela.

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