Ubuthakathaka beVon Willebrand yini? Izimpawu, Izimbangela, Nokwelashwa

Ubuthakathaka beVon Willebrand yisifo esivamile sokugabha igazi elitholakala ngokudluliselwa, elithinta abantu abacishe babe yi-1% yabantu. Kwenzeka uma igazi lakho lingabambeki kahle ngenxa yezinkinga eprotheni ebizwa ngokuthi yi-von Willebrand factor. Nakuba lokhu kungase kuzwakale kukhathazayo, abantu abaningi abanesimo esinjalo baphila impilo evamile ngokuphelele ngokuphathwa kahle nokunakekelwa.

Le prothini isebenza njengolukanda oluqinile olusiza amaseli egazi akho ukuba ahlangane ndawonye ukuyeka ukopha uma uthola isiqongo noma ukulimala. Uma ungenayo le prothini ngokwanele, noma ayisebenzi kahle, ungase uqhumbe kalula noma ugahe isikhathi eside kunokujwayelekile ngemuva kokulimalala noma izinqubo zezokwelapha.

Ziyini izimpawu zobuthakathaka beVon Willebrand?

Isilwane esivamile ongasibona ukopha okuhlala isikhathi eside kunokufanele noma kwenzeka kalula kunokulindelekile. Abantu abaningi abanezimpawu ezilula zalesi simo abaziqapheli nokuthi banaso kuze kube yilapho bedinga ukuhlinzwa noma belimala kakhulu.

Nazi izimpawu ongazihlangabezana nazo, ukhumbula ukuthi zingaba zithambile kakhulu kuya ezibonakalayo kakhulu:

• Ukuqhuma okulula okuvela ngamabump amancane noma ngezinye izikhathi ngaphandle kwesizathu esicacile
• Ukuqhuma kwempumulo okuvamile okuhlala isikhathi esingaphezu kwemizuzu eyi-10 noma kwenzeka izikhathi eziningi ngenyanga
• Isikhathi esinzima sezinyanga eziningi esiphela izinsuku ezingaphezu kwe-7 noma sidinga ukushintsha ama-pad/ama-tampon njalo ngehora
• Amagciwane egazi, ikakhulukazi ngesikhathi sokuhlanza amazinyo noma ukubhula
• Ukugaha okuqhubekayo ngemuva kokusiqongo, umsebenzi wamazinyo, noma ukuhlinzwa
• Igazi emanzini akho noma emathunjini (akuvamile kodwa kungenzeka)

Kwabesifazane, ukugaha okunzima kwesikhathi senyanga kuvame ukuba yisibonakaliso sokuqala esiqaphelekayo. Ungase udinga ukusebenzisa ama-pad amaningi noma ama-tampon ngesikhathi esisodwa, uhlangabezane nokugeleza okukhulu, noma ube nezinyanga ezithinta kakhulu imisebenzi yakho yansuku zonke.

Ezimweni ezingavamile, ezinzima kakhulu, ungase uhlangabezane nokugaha kwangaphakathi noma ukugaha ezinhlanganweni nasemisipha, okungabangela ubuhlungu nokuvuvukala. Noma kunjalo, leli zinga lobunzima lithinta kuphela ingxenye encane yabantu abanesimo.

Ziyini izinhlobo zobuthakathaka beVon Willebrand?

Kunezinhlobo ezintathu eziyinhloko zobuthakathaka beVon Willebrand, ngayinye inezilinganiso ezahlukene zobunzima nezimpawu. Ukuqonda ukuthi yiluphi uhlobo olukhona kusiza udokotela wakho ukuba enze uhlelo lokwelapha oluhle kakhulu olufanele isimo sakho.

Uhlobo 1 yilona elithambile futhi elivamile kakhulu, elithinta abantu abacishe babe yi-75% abanesimo. Unezinga eliphansi kunokujwayelekile le-von Willebrand factor, kodwa iprotheni isasebenza kahle. Abantu abaningi abaneUhlobo 1 banezimpawu ezilula kangangokuthi abadingi ukwelashwa.

Uhlobo 2 luza ngezinhlobo eziningi (2A, 2B, 2M, no-2N) futhi luthinta abantu abacishe babe yi-20% abanesifo. Kulolu hlobo, ungase ube namazinga ajwayelekile eprotheni, kodwa ayisebenzi kahle. Izimpawu zivame ukuba zibonakale kakhulu kunohlobo 1 kodwa zisaphatheka ngokunakekelwa okuhle.

Uhlobo 3 yilona eliyigugu futhi elibi kakhulu, elithinta abantu abangaphansi kuka-5% abanebuthakathaka beVon Willebrand. Abantu abaneUhlobo 3 bane-von Willebrand factor encane kakhulu noma ayikho nhlobo. Lolu hlobo ludinga ukuphathwa okunzima kwezokwelapha nokugadwa.

Yini ebangela ubuthakathaka beVon Willebrand?

Ubuthakathaka beVon Willebrand bubangelwa izinguquko e-gene elizisa umzimba wakho ukuthi wenze kanjani i-von Willebrand factor protein. Lezi zinguquko ze-genetic zidluliselwa, okusho ukuthi zidluliselwa kubazali bakho nge-DNA yakho.

Izimo eziningi zilandela lokho odokotela abakubiza ngokuthi "iphethini ye-autosomal dominant." Lokhu kusho ukuthi udinga kuphela ukudlulisela i-gene eguqukile komunye umzali ukuze ube nesimo. Uma omunye wabazali bakho enebubuthakathaka beVon Willebrand, unethuba eliyi-50% lokudlulisela.

Noma kunjalo, ubuthakathaka beVon Willebrand Uhlobo 3 bulandela iphethini ehlukile ebizwa ngokuthi "i-autosomal recessive." Lokhu kusho ukuthi udinga ukudlulisela ama-gene aguqukile kubazali bobabili ukuze uthuthukise leli fomu elibi. Bobabili abazali bavame ukuba ngabaqhubi abangenazo izimpawu.

Ezimweni ezingavamile, abanye abantu bathuthukisa lokho okuthiwa "i-acquired Von Willebrand syndrome" kamuva ekuphileni. Lokhu akutholakali ngokudluliselwa kodwa kungenzeka ngenxa yezimo ezithile zezokwelapha njengezifo ze-autoimmune, izinkinga zenhliziyo, noma ezinye izifo zomdlavuza ezithinta indlela i-von Willebrand factor yakho esebenza ngayo.

Nini kufanele ubheke udokotela ngenxa yobuthakathaka beVon Willebrand?

Kufanele ucabange ukuya kudokotela uma uqaphela iphethini yokopha okungavamile noma ukuqhuma okuhluke kulokho okujwayelekile kuwe. Qaphela ukugaha okuhlala isikhathi eside kunokulindelekile noma kwenzeka njalo kunokufanele.

Hlela i-aphoyintimenti uma uhlangabezana nokuqhuma kwempumulo okuvamile okunzima ukuyeka, ikakhulukazi uma kwenzeka izikhathi eziningi ngenyanga noma kuhlala isikhathi esingaphezu kwemizuzu eyi-10. Isikhathi esinzima sezinyanga eziningi esithinta impilo yakho yansuku zonke noma esidinga ukushintsha isivikelo njalo ngehora futhi siyakufaneleka ukuxoxa nodokotela wakho.

Funani ukunakekelwa kwezokwelapha ngokushesha uma unegazi eliqhubekayo ngemuva komsebenzi wamazinyo, ukuhlinzwa, noma ukulimala okungeke kuyeke ngezindlela ezijwayelekile zokuqala zokusiza. Igazi emanzini akho noma emathunjini, noma noma yiluphi ukugaha okukwenza uzizwe ubuthakathaka noma ukhwehle, kufanele kuhlolwe ngokushesha.

Uma uhlela ukuhlinzwa, izinqubo zamazinyo, noma ukhulelwe, kubalulekile ukuxoxa nganoma yimuphi umlando wokopha okungavamile neqembu lakho lezokunakekelwa kwezempilo. Bangathatha izinyathelo zokuvimbela izinkinga nokuqinisekisa ukuphepha kwakho ngesikhathi salezi zinqubo.

Ziyini izici ezingozi zobuthakathaka beVon Willebrand?

Isici esiyinhloko esingozi sobuthakathaka beVon Willebrand ukuba nomlando womndeni wesimo noma izinkinga zokopha ezingachazwanga. Njengoba lokhu kuyisimo esidluliselwa, ingozi yakho ixhomeke kakhulu ekwakheni kwakho kwe-genetic.

Ukuba nomzali onebubuthakathaka beVon Willebrand kukunika amathuba angu-50% okudlulisela isimo, yize ubunzima bungase buhluke kokuhlangenwe nakho komzali wakho. Ngezinye izikhathi, izimpawu zingaba zithambile kakhulu ezinhlwini zomndeni kangangokuthi isimo asiqaphelwa izizukulwane.

Izinhlobo ezithile zegazi zingathinta futhi ingozi yakho nobunzima besimpawu. Abantu abanegazi lohlobo lwe-O ngokwemvelo banezinga eliphansi le-von Willebrand factor, okungenza izimpawu zibonakale kakhulu uma unesimo. Lokhu akubangeli isifo, kodwa kungathinta indlela esivele ngayo.

Abesifazane bangase baqaphele izimpawu kalula kunamadoda ngenxa yezinyanga, okungaveza izinkinga zokopha ezingase zingaphawulwa. Ukukhulelwa, ukubeletha, nokuhluka kwe-hormonal kungathinta futhi amazinga e-von Willebrand factor nezinqubo zokopha.

Ziyini izinkinga ezingenzeka zobuthakathaka beVon Willebrand?

Abantu abaningi abanebuthakathaka beVon Willebrand baphila impilo evamile, enempilo ngaphandle kwezinkinga ezinzima. Noma kunjalo, kuwusizo ukuqonda ukuthi yiziphi izinkinga ezingavela ukuze ukwazi ukusebenza neqembu lakho lezokunakekelwa kwezempilo ukuze uzivimbele.

Inkinga evamile kakhulu ukushoda kwa-iron anemia, okungathuthukiswa ukopha okungapheli isikhathi eside. Lokhu kungenzeka ngenxa yezinyanga eziningi, ukuqhuma kwempumulo okuvamile, noma ukopha okuqhubekayo. Ungase uzizwe ukhathele, ubuthakathaka, noma ukhwehle uma lokhu kwenzeka.

Nazi izinkinga ezingenzeka okufanele uzazi, yize eziningi zingavikeleka ngokunakekelwa okuhle:

• Ukugaha okukhulu ngesikhathi sokuhlinzwa, izinqubo zamazinyo, noma ukubeletha
• Ukushoda kwa-iron anemia ngenxa yokopha okungapheli isikhathi eside
• Izinkinga zokopha ngesikhathi sokukhulelwa nokubeletha
• Ngokungavamile, ukugaha okubulalayo okuvela ekulimaleni okukhulu noma ekugahaneni kwangaphakathi
• Ukugaha kwezinhlanganwe nokwenzakala (ikakhulukazi ezigabeni ezinzima zeUhlobo 3)

Ngesikhathi sokukhulelwa, ukuhluka kwe-hormone kungathuthukisa izimpawu zokopha kwabesifazane abaningi abanebuthakathaka beVon Willebrand. Noma kunjalo, izinkinga zokopha zingase zenzeke ngesikhathi sokubeletha noma emasontweni alandela ukubeletha, ngakho ukuphathwa okuhle kwezokwelapha kubalulekile.

Ngobuthakathaka beVon Willebrand Uhlobo 3, izinkinga ezinzima kakhulu njengokugaha kwangaphakathi noma ukugaha ezinhlanganweni kungenzeka, kufana nalokho okwenzeka e-hemophilia. Noma kunjalo, ngokunakekelwa okuhle kwezokwelapha nokwelashwa, ngisho nabantu abanezimpawu ezinzima bangaphila impilo egcwele, esebenzayo.

Ubuthakathaka beVon Willebrand bungavikeleka kanjani?

Njengoba ubuthakathaka beVon Willebrand kuyisimo se-genetic esidluliselwa, awukwazi ukuvimbela ukuba kwenzeke. Noma kunjalo, ungathatha izinyathelo zokuvimbela izinkinga zokopha nokuphatha izimpawu zakho ngokuphumelelayo uma usuke wazi ukuthi unesimo.

Uma unomlando womndeni wezifo zokopha, ukwelulekwa kwe-genetic kungakusiza ukuqonda ingozi yakho nokwenza izinqumo ezinolwazi ngokuhlela umndeni. Umluleki we-genetic angachaza ama-phethini okudluliselwa nokuqala ukuxoxa ngezinketho zokuhlola uma ukhathazekile ngokudlulisela isimo kubantwana bakho.

Iqhinga elibaluleke kakhulu lokuvimbela ukufunda ukuphatha isimo sakho kahle. Lokhu kuhlanganisa ukugwema imithi engase ikhulise ingozi yokopha, njenge-aspirin nezinye izilengisi zobuhlungu, ngaphandle uma kuvunyelwe ngokuqondile udokotela wakho.

Ukusebenzisana eduze neqembu lakho lezokunakekelwa kwezempilo ngaphambi kwanoma yiluphi ukuhlinzwa, umsebenzi wamazinyo, noma izinqubo zezokwelapha kungavimbela izinkinga zokopha. Bangakunika imithi noma bathathe ezinye izinyathelo zokwenza ube nokuphepha ngesikhathi salezi zimo.

Ubuthakathaka beVon Willebrand butholakala kanjani?

Ukuthola ubuthakathaka beVon Willebrand kuhilela ukuhlolwa kwegazi okuningi okuqapha ukuthi igazi lakho liyambeka kahle kangakanani nokuthi une-von Willebrand factor engakanani. Udokotela wakho uzoqala ngokubuza ngomlando wakho siqu nomlando womndeni wezinkinga zokopha.

Ukuhlolwa kokuqala kuvame ukubandakanya ukubalwa kwegazi okugcwele ukuhlola i-anemia nokuhlolwa okuyisisekelo kokwambeka. Uma lokhu kuphakamisa isifo sokopha, udokotela wakho uzoyala ukuhlolwa okukhethekile ukuqapha amazinga e-von Willebrand factor nokusebenza.

Ukuhlolwa okubalulekile kokuxilonga kuhlanganisa ukuqapha i-von Willebrand factor antigen (inani leprotheni), i-von Willebrand factor activity (indlela esebenza ngayo), namazinga e-Factor VIII (enye iprotheni yokwambeka esebenza ne-von Willebrand factor). Ngezinye izikhathi, ukuhlolwa okukhethekile okwengeziwe kudingeka ukuze kunqunywe uhlobo oluqondile.

Ukuthola ukuxilongwa okuqondile ngezinye izikhathi kungathatha isikhathi ngoba amazinga e-von Willebrand factor angase ahluke ngokusekelwe egazini lakho, amazinga engcindezi, ama-hormone, nezinye izici. Udokotela wakho angase adinge ukuphakamisa ukuhlolwa noma enze ukuhlolwa okukhethekile okwengeziwe ukuze athole isithombe esicacile.

Yini ukwelashwa kobuthakathaka beVon Willebrand?

Ukwelashwa kobuthakathaka beVon Willebrand kugxile ekuthuthukiseni amazinga e-von Willebrand factor noma ekuthuthukiseni ukwambeka kwegazi uma ukudinga kakhulu. Izindaba ezinhle ukuthi abantu abaningi abanezimpawu ezilula abadingi ukwelashwa okuvamile futhi badinga kuphela imithi ngaphambi kokuhlinzwa noma ngesikhathi seziqephu zokopha okunzima.

Imithi evamile kakhulu yi-desmopressin (DDAVP), ephethe isikhashana ukukhululwa komzimba wakho kwe-von Willebrand factor egcinwe. Lokhu kungenziwa njengesi-spray sesifuba noma i-injection futhi kusebenza kahle kwabantu abaningi abaneUhlobo 1 nezinye izimo zeUhlobo 2.

Kwabantu abangaphenduli kahle ku-desmopressin noma abanezinye izinhlobo ezinzima, ukwelashwa kokufaka i-factor kungase kudingeke. Lezi yimikhiqizo egxile ebandakanya i-von Willebrand factor ne-Factor VIII engase inikezwe nge-IV uma ukopha kwenzeka noma ngaphambi kwezinqubo.

Izinketho zokwelapha ezengeziwe zihlanganisa:

• Imithi ye-antifibrinolytic njenge-tranexamic acid ukusiza ukuvimbela ukwehla kwe-clot
• Ukwelashwa kwe-hormonal kwabesifazane abanegazi elinzima lenyanga
• I-iron supplements ukwelapha noma ukuvimbela i-anemia evela ekuphucweni kwegazi
• Ukwelashwa okusebenza ngqo ekuqhumeni kwempumulo noma ekuqhumeni komlomo

Uhlelo lokwelapha lwakho luzokwenziwa ngokwezifiso ngokusekelwe egazini lakho eliqondile lobuthakathaka beVon Willebrand, ubunzima besimpawu, nokuphendula komuntu ngamunye emithi ehlukene. Abantu abaningi bathola ukuthi ngokwelashwa okuhle, bangabamba iqhaza emisebenzini evamile ngaphandle kokuncika okukhulu.

Indlela yokuphatha ubuthakathaka beVon Willebrand ekhaya?

Ukuphatha ubuthakathaka beVon Willebrand ekhaya kuhilela ukufunda amasu asebenzayo okuthambisa izingozi zokopha nokuphatha iziqephu ezincane zokopha ngokuphumelelayo. Ngezinye izinguquko ezilula nokulungiselela, ungagcina impilo esebenzayo, evamile.

Okokuqala, kubalulekile ukugwema imithi engase ikhulise ingozi yokopha. Gwema i-aspirin, i-ibuprofen, nezinye i-NSAIDs ngaphandle uma kuvunyelwe ngokuqondile udokotela wakho. Esikhundleni salokho, sebenzisa i-acetaminophen ukunciphisa ubuhlungu, futhi njalo hlola nodokotela wakho ngaphambi kokuthi uqale noma iyiphi imithi emisha noma izithasiselo.

Ngokuqhuma kwempumulo, gcina izinto ezisebenzayo zilungile futhi wazi indlela efanele. Cindezela ingxenye ethambile yempumulo yakho ngokuqinile imizuzu engu-10-15 ngenkathi ukhwehlela phambili kancane. Faka u-ice ebhulwini lempumulo, futhi cabanga ngokusebenzisa i-humidifier ekhaya lakho ukuvimbela ukumomotheka kwempumulo.

Nazi izindlela ezisiza zokuphatha ekhaya:

• Sebenzisa ibrashi yamahloni ebuthambile nokunakekelwa kwamazinyo okuthambile ukuvimbela ukugaha kwamagciwane
• Faka ucindezelelo oluqondile nokuphakamisa izigqongo neziqongo
• Gcina ikiti lokusiza elihlelile eliqukethe i-gauze, ama-bandages, nama-ice packs
• Gqoka izingubo zokuphepha ngesikhathi sezemidlalo noma imisebenzi engozi yokulimalala
• Gcina ukudla okuhle kwe-iron ukuvimbela i-anemia

Kwabesifazane abanegazi elinzima lenyanga, ukulandelela izinyanga zakho kungasiza ekuqondeni ama-phethini nokuhlela kusengaphambili. Sebenzisa ama-pad obusi, cabanga ngama-menstrual cups, futhi ungangabazi ukuxoxa ngezinketho ze-hormonal nodokotela wakho uma izinyanga zithinta kakhulu ikhwalithi yempilo yakho.

Kufanele ulungiselele kanjani i-aphoyintimenti yakho yodokotela?

Ukulungiselela kahle i-aphoyintimenti yakho yodokotela kungasiza ekuqinisekiseni ukuthi uthola ukuxilongwa okuqondile kakhulu nohlelo lokwelapha oluphumelelayo. Qala ngokugcina irekhodi lemininingwane yokugaha kwakho, kuhlanganise nokuthi kwenzeka nini, isikhathi eside kangakanani, nokuthi yini eyibangela.

Bula umlando wezokwelapha womndeni wakho, ikakhulukazi uqaphele noma yibaphi abantu abasemncane abake baba nokugaha okungavamile, izinyanga eziningi, noma izinkinga zokuhlinzwa noma umsebenzi wamazinyo. Ngezinye izikhathi izifo zokopha zihamba emindenini kodwa azikaxilongwa ngokusemthethweni, ngakho-ke lolu lwazi lungaba lubalulekile kakhulu.

Yenza uhlu lwemithi yayo yonke nezithasiselo ozithathayo njengamanje, kuhlanganise nezilengisi zobuhlungu ezingaphezu kokuthengiswa, amavithamini, nezithasiselo zezitshalo. Ezinye zalezi zingathinta ukugaha, futhi udokotela wakho udinga ukwazi konke okukuthathayo.

Bhala imibuzo ethile ofuna ukuyibuza, njengalezi:

• Yiluphi uhlobo lobuthakathaka beVon Willebrand enami?
• Yiziphi imisebenzi engingayigwema noma ngiyishintshe?
• Kufanele ngenze njani uma nginephuthuma lokopha?
• Lokhu kuzothinta kanjani ukukhulelwa noma ukuhlinzwa esikhathini esizayo?
• Ingabe amalungu omndeni wami kufanele ahlolwe?

Letha umuntu osekela uma kungenzeka, ikakhulukazi ngezikhathi zokuqala zokuxilongwa. Ukuba nomuntu lapho kungakusiza ukukhumbula ulwazi olubalulekile nokunikeza ukwesekwa ngokomzwelo ngesikhathi esingase sizwakale sengathi yingxoxo ebiwe.

Yini okufanele uyikhumbule ngebuthakathaka beVon Willebrand?

Ubuthakathaka beVon Willebrand yisimo esiphatheka esithinta izigidi zabantu emhlabeni wonke, abaningi babo baphila impilo evamile ngokuphelele. Nakuba kuyisifo esivamile kakhulu sokopha esidluliselwa, kuvame ukuba buthambile futhi kungase kungadingi ukwelashwa okuvamile.

Into ebaluleke kakhulu okumele uyikhumbule ukuthi ukuba nobuthakathaka beVon Willebrand akudingeki ukulinganiselwe impilo yakho kakhulu. Ngokunakekelwa okuhle kwezokwelapha, abantu abaningi bangabamba iqhaza emisebenzini evamile, babe nemisebenzi ephumelelayo, futhi bakhulise imindeni enempilo.

Ukuxilongwa kwasekuqaleni nokusebenza neqembu lezokunakekelwa kwezempilo eliqondayo kwenza umehluko omkhulu ekulawuleni isimo sakho ngokuphumelelayo. Abantu abaningi bathola ukuthi uma sebeqonda isimo sabo futhi bafunde amasu afanele okuphatha, bazizwa bethemba kakhulu futhi beqondisa impilo yabo.

Uma ucindezela ukuthi ungase ube nobuthakathaka beVon Willebrand ngokusekelwe ezimpawu zakho noma emlandweni womndeni, ungangabazi ukuxoxa ngakho nodokotela wakho. Ukuthola izimpendulo nokunakekelwa okufanele kungathuthukisa kakhulu ikhwalithi yempilo yakho futhi kuvimbele izinkinga ngokuhamba kwesikhathi.

Imibuzo evamile ebuzwa ngebuthakathaka beVon Willebrand

Ingabe abantu abanebuthakathaka beVon Willebrand bangadlala imidlalo?

Yebo, abantu abaningi abanebuthakathaka beVon Willebrand bangabamba iqhaza ezemidlalo nasemisebenzini yomzimba. Ungase udinge ukugwema imidlalo ehlangene kakhulu noma imisebenzi engozi enkulu yokulimalala, kuye ngobunzima besimpawu sakho. Sebenza nodokotela wakho ukuze unqume ukuthi yiziphi imisebenzi ephephile kuwe futhi ucabange ngokusebenzisa izingubo zokuphepha uma kufaneleka.

Ingabe ubuthakathaka beVon Willebrand buzothinta ikhono lami lokuba nabantwana?

Abesifazane abaningi abanebuthakathaka beVon Willebrand banezinto eziphumelelayo zokukhulelwa nokubeletha. Ukuhluka kwe-hormone ngesikhathi sokukhulelwa kuvame ukuthuthukisa izimpawu zokopha isikhashana. Noma kunjalo, uzodinga ukunakekelwa okukhethekile ngesikhathi sokukhulelwa nokubeletha ukuze ulawule izinkinga ezingenzeka zokopha. Xoxa ngokuhlela umndeni neqembu lakho lezokunakekelwa kwezempilo ukuze uthole isiqondiso esifanele.

Ingabe ubuthakathaka beVon Willebrand bufana ne-hemophilia?

Cha, nakuba kokubili kuyizifo zokopha, kubangelwa izinkinga ezihlukene zeprotheni yokwambeka. Ubuthakathaka beVon Willebrand buthinta i-von Willebrand factor, kuyilapho i-hemophilia ihilela ukushoda kwe-Factor VIII noma IX. Ubuthakathaka beVon Willebrand buvamile buthambile futhi buthinta amadoda nabesifazane ngokulinganayo, kuyilapho i-hemophilia enzima ikakhulukazi ithinta amadoda.

Ingabe ngidinga ukugqoka i-bracelet yokuxwayisa kwezokwelapha?

Ukugqoka i-bracelet yokuxwayisa kwezokwelapha noma ukuphatha ikhadi le-ID lezokwelapha kuyinto enhle, ikakhulukazi uma unebuthakathaka beVon Willebrand obuphakathi nendawo kuya ebunzimeni. Lolu lwazi lungabaluleka kakhulu kubasebenzi bezokwelapha bephuthumayo uma ungenamandla noma ungakwazi ukukhulumisana ngesikhathi sephuthuma lezokwelapha noma ingozi.

Ingabe ubuthakathaka beVon Willebrand bungaba sibi ngokuhamba kwesikhathi?

Ubuthakathaka beVon Willebrand ngokwabo abuvami ukuba sibi ngokuhamba kwesikhathi, kodwa izici ezihlukahlukene zingathinta izimpawu zakho ngokuhamba kwesikhathi. Ukuhluka kwe-hormone, imithi ethile, nezinye izimo zezempilo zingathinta ubunzima bokupha. Ukulandelela njalo neqembu lakho lezokunakekelwa kwezempilo kusiza ekuqinisekiseni ukuthi uhlelo lokwelapha lwakho luhlala luphumelela njengoba izidingo zakho zishintsha.