

Health Library
October 10, 2025
Question on this topic? Get an instant answer from August.
Amathonsi eso e-Cysteamine ayimithi ekhethekile eyenzelwe ukwelapha i-cystinosis, isimo esingavamile sezakhi zofuzo esibangela ukwakheka kwamakristalu ayingozi emehlweni. Lokhu kwelashwa okunobumnene kodwa okuphumelelayo kusiza ekuncibilikiseni lawa makristalu futhi kuvikele umbono wakho ekulimaleni kwesikhathi eside.
Uma wena noma othandekayo wakho unikezwe amathonsi eso e-cysteamine, cishe ubhekene nohambo oluyinkimbinkimbi lwezokwelapha. Ukuqonda ukuthi le mithi isebenza kanjani nokuthi yini ongayilindela kungakusiza uzizwe uqiniseka kakhulu ngohlelo lwakho lokwelashwa.
Isixazululo se-ophthalmic se-Cysteamine yithonsi leso elinikezwa ngudokotela elenzelwe ngqo ukwelapha amadiphozi e-crystal ye-cystine ye-corneal. Lawa makristalu akheka lapho umzimba wakho ungenakukwazi ukucubungula kahle i-amino acid ebizwa nge-cystine, okuholela ekwakhekeni okubuhlungu ezingxenyeni ezihlukahlukene zomzimba okuhlanganisa namehlo akho.
Umuthi usebenza ngokwephula lawa madiphozi e-crystal aqongelela e-cornea, ungqimba olucacile olungaphambili lweso lakho. Ngaphandle kokwelashwa, lawa makristalu angabangela ukungakhululeki okukhulu futhi angaholela ezinkingeni zombono ngokuhamba kwesikhathi.
Lena akuyona imithi ozoyithola ekhemisi lakho langakini. Amathonsi eso e-Cysteamine ngokuvamile alungiswa ngamakhemisi akhethekile okuhlanganisa ngoba izidingo zesiguli ngasinye zingahluka kancane ngokuya ngesimo sabo esithile nokuphendula ekwelashweni.
Amathonsi eso e-Cysteamine asetshenziswa ikakhulukazi ukwelapha amadiphozi e-crystal ye-cystine ye-corneal kubantu abane-cystinosis. I-Cystinosis yisifo esingavamile esizuzwe ngofuzo esithinta indlela umzimba wakho ocubungula ngayo i-cystine, i-amino acid evame ukwephulwa futhi iqedwe emangqamuzaneni.
Uma une-cystinosis, i-cystine yakha futhi yakhe amakristalu emzimbeni wakho wonke, okuhlanganisa nasemehlweni akho. Lawa makristalu e-cornea angabangela ubuhlungu obukhulu emehlweni, ukuzwela ukukhanya, nomuzwa wokuthi unenhlabathi emehlweni akho. Ngokuhamba kwesikhathi, angathinta nekhwalithi yakho yokubona.
Amathonsi esamehlo asiza ukuncibilikisa lawa makristalu akhona futhi avimbele ukwakheka kwamasha. Lokhu kwelashwa kubaluleke kakhulu ngoba ngenkathi ezinye izinhlobo ze-cysteamine zingelapha i-cystinosis kwezinye izingxenye zomzimba wakho, yifomu lamathonsi esamehlo kuphela elingafinyelela ngempumelelo kumakristalu e-corneal.
I-Cysteamine isebenza ngokweqisa ngamakhemikhali amakristalu e-cystine akheke e-cornea yakho. Cabanga ngayo njenge-ejenti encibilikayo ngobumnene eqondise ngqo lezi zinto ezifakwe amakristalu ngaphandle kokulimaza izicubu zamehlo ezinempilo.
Umuthi uguqula i-cystine ibe yinhlanganisela ehlukile umzimba wakho ongayiqeda kalula. Le nqubo yenzeka kancane kancane ngokuhamba kwesikhathi, yingakho uzodinga ukusebenzisa amathonsi njalo izinyanga eziningana ukuze ubone imiphumela ephelele.
Lokhu kuthathwa njengomuthi oqinile ngokulinganisela mayelana nesenzo sawo esiqondile ngokumelene namakristalu e-cystine. Ngenkathi isebenza kahle kakhulu ngenjongo yayo, futhi ikhethekile kakhulu futhi isebenza kuphela kulolu hlobo oluthile lokwakheka kwamakristalu.
Udokotela wakho uzohlinzeka ngemiyalelo ethile yokusebenzisa amathonsi esamehlo e-cysteamine, kodwa indlela ejwayelekile ihlanganisa ukufaka ithonsi elilodwa esweni ngalinye elithintekile izikhathi eziningana ngosuku. Imvamisa eqondile incike ekuqineni kwezinto zakho ezifakwe amakristalu nokuthi usabela kahle kangakanani ekwelashweni.
Ngaphambi kokusebenzisa amaconsi, geza izandla zakho kahle ngensipho namanzi. Thambisa ikhanda lakho kancane futhi udonse kancane isihlathi sakho esingezansi ukuze wakhe iphokhe elincane. Cindezela ithonsi elilodwa kuleli phokhe, bese uvala iso lakho kancane futhi ucindezele kancane ekhoneni elingaphakathi eduze kwekhala lakho cishe iminithi elilodwa.
Ungawasebenzisa lawa maconsi nokuthi ngaphandle kokudla, njengoba esetshenziswa ngqo emehlweni akho kunokuba athathwe ngomlomo. Kodwa-ke, zama ukuwasebenzisa ngezikhathi ezifanayo nsuku zonke ukuze ugcine amazinga aqhubekayo emithi ezicutshini zamehlo akho.
Uma usebenzisa eminye imithi yamehlo, linda okungenani imizuzu emi-5 phakathi kwamaconsi amehlo ahlukene ukuwavimbela ukuthi angagezani. Hlala usebenzisa amaconsi e-cysteamine ekugcineni uma usebenzisa imithi yamehlo eminingi.
Abantu abaningi badinga ukusebenzisa amaconsi e-cysteamine amehlo izinyanga eziningana ukuze babone ukuthuthuka okukhulu emakristalini abo. Udokotela wakho ngokuvamile uzoncoma ukuwasebenzisa okungenani izinyanga eziyi-6 ekuqaleni, nakuba abanye abantu bengase badinge izikhathi zokwelashwa ezinde.
Isikhathi esithathayo sincike ekutheni unamakristali amangaki nokuthi ancibilika ngokushesha kangakanani. Abanye abantu baqaphela ukuncipha kobuhlungu bamehlo nokuzwela ukukhanya emasontweni ambalwa, kuyilapho ukuthuthuka kokubona kungase kuthathe izinyanga ezi-3-6 ukuba kubonakale.
Udokotela wakho wamehlo uzoqapha inqubekela phambili yakho ngezivivinyo zamehlo ezivamile ukuze abone ukuthi amakristali ancibilika kahle kangakanani. Bangase balungise isimiso sakho sokwelashwa ngokusekelwe kulokho abakubonayo ngesikhathi sokuhlolwa kwabo.
Ngemva kwesikhathi sokwelashwa sokuqala, abantu abaningi abanesifo se-cystinosis badinga ukuqhubeka nokusebenzisa amaconsi isikhathi eside ukuze bavimbele ukwakheka kwamanye amakristali. Lokhu kuba yingxenye yokuphatha isimo sakho sonke kunokumane welaphe izimpawu ezikhona.
Njengemithi eminingi yamehlo, amaconsi e-cysteamine angabangela imiphumela emibi ethile, nakuba abantu abaningi beyibekezelela kahle. Imiphumela emibi evame kakhulu ivamise ukuba mncane futhi ithambekele ekuthuthukiseni njengoba amehlo akho ejwayela umuthi.
Nansi imiphumela emibi ongase uyithole, futhi kujwayelekile ngokuphelele ukuzwa ukhathazekile ngalezi zinto ezingenzeka:
Le miphumela emibi ejwayelekile ivamise ukunyamalala ngemizuzu embalwa ngemva kokufaka amaconsi. Uma ziqhubeka noma ziba yinkinga, yazisa udokotela wakho ukuze akwazi ukulungisa ukwelashwa kwakho uma kudingeka.
Abanye abantu bangase babe nemiphumela emibi engavamile kodwa ebonakalayo edinga ukunakwa:
Imiphumela emibi engavamile kodwa ebucayi ingenzeka, nakuba ingavamile. Lokhu kuhlanganisa ukusabela okukhulu komzimba, izinguquko ezinkulu ekucindezelweni kwamehlo, noma izimpawu zokutheleleka kwamehlo. Uma uba nobuhlungu obukhulu obuzumayo emehlweni, izinguquko ezinkulu ekuboneni, noma izimpawu zokusabela komzimba njengokuvuvukala kobuso, funa ukwelashwa ngokushesha.
Abantu abaningi abane-cystinosis bangawasebenzisa ngokuphepha amaconsi e-cysteamine emehlweni, kodwa zikhona izimo lapho kudingeka khona ukuqapha okwengeziwe. Udokotela wakho uzobuyekeza ngokucophelela umlando wakho wezokwelapha ngaphambi kokukuyalela lo muthi.
Kufanele wazise udokotela wakho uma unokungezwani komzimba ne-cysteamine noma imithi efanayo. Nakuba ukusabela komzimba kulo muthi kungavamile, kungaba kubi uma kwenzeka.
Abantu abanezimo ezithile zamehlo bangase badinge ukuqashwa okukhethekile ngenkathi besebenzisa amaconsi e-cysteamine. Lokhu kufaka phakathi labo abanezifo zamehlo ezisebenzayo, i-dry eye syndrome eqinile, noma ukuhlinzwa kwamehlo kwakamuva. Udokotela wakho usengakwazi ukukuyala lo muthi kulezi zimo, kodwa bazofuna ukukubhekisisa.
Uma ukhulelwe noma uncelisa, xoxa ngobungozi nezinzuzo nodokotela wakho. Ngenkathi umuthi ufakwa ngqo emehlweni futhi okuncane kakhulu kungena egazini lakho, udokotela wakho uzofuna ukulinganisa izinzuzo ngokumelene nanoma yiziphi izingozi ezingaba khona.
Izingane ngokuvamile zingasebenzisa amaconsi e-cysteamine emehlweni ngokuphepha, kodwa zingase zidinge usizo lokuwafaka ngendlela efanele. Udokotela wakho uzohlinzeka ngesiqondiso esiqondile sokusetshenziswa kwezingane uma ingane yakho idinga lokhu kwelashwa.
Amaconsi e-cysteamine emehlweni atholakala kakhulu njenge-Cystadrops, okuyigama eliyinhloko lomkhiqizo walo muthi. Le fomula yenzelwe ngokuqondile ukwelapha izindawana zekristalu ye-cystine ye-corneal futhi iza ngokugxila okujwayelekile.
Kwezinye izimo, udokotela wakho angase ayalele inguqulo ehlanganisiwe yamaconsi e-cysteamine emehlweni enziwe yikhemisi ekhethekile. Le yimithi eyenziwe ngokwezifiso engase ibe nokugxila okuhlukile kuye ngezidingo zakho ezithile.
Izinhlobo ezihlanganisiwe zivame ukudingeka ngoba akuzona zonke izitolo zamakhemisi eziphethe inguqulo yegama lomkhiqizo, futhi ngezinye izikhathi odokotela bakhetha ukulungisa ukugxila ezigulini ngazinye. Zombili izinhlobo zisebenza ngokulinganayo uma zilungiswe kahle.
Njengamanje, amaconsi e-cysteamine emehlweni yiwona kuphela umuthi ovunyelwe ngokuqondile ukwelapha izindawana zekristalu ye-cystine ye-corneal. Akukho ezinye izindlela eziqondile ezisebenza ngendlela efanayo kulesi simo esithile.
Kodwa-ke, udokotela wakho angase ancome ukwelashwa okusekelayo ukusiza ukuphatha izimpawu zakho ngenkathi i-cysteamine isebenza. Lokhu kungabandakanya izinyembezi ezingokwenziwa ukusiza ngomswakama, izibuko zelanga ukunciphisa ukuzwela ekukhanyeni, noma amasu okuphatha ubuhlungu bokungakhululeki kwamehlo.
Ngokwesimo esingaphansi se-cystinosis, i-cysteamine yomlomo (i-Cystagon noma i-Procysbi) isetshenziselwa ukwelapha amakristalu atholakala kwezinye izingxenye zomzimba. Kodwa-ke, le mithi yomlomo ayifinyeleli ngempumelelo kumakristalu e-corneal, yingakho amaconsi amehlo adingeka ngokuqondile.
Abanye abantu bazuza futhi ekugqokeni izinto zokuzivikela kanye nokulungiswa kwendlela yokuphila ukunciphisa ukucindezeleka kwamehlo ngenkathi amakristalu abo encibilika. Udokotela wakho wamehlo angase ancome amasu athile ngokuya ngesimo sakho somuntu ngamunye.
Amaconsi amehlo e-Cysteamine awanakho ukufaniswa neminye imithi yamehlo ngoba aphatha isimo esithile kakhulu futhi esingavamile. Yiwona kuphela umuthi oklanyelwe ukuncibilikisa amakristalu e-cystine e-cornea, okwenza asebenze ngendlela eyingqayizivele ngenjongo yalo.
Uma uziqhathanisa namaconsi amehlo ajwayelekile wamehlo omile noma ukucasuka, amaconsi e-cysteamine asebenza ngenjongo ehlukile ngokuphelele. Zenzelwe ngokuqondile ukwelapha isimo sezakhi zofuzo kunokuba izinkinga ezivamile zamehlo.
Ukusebenza kahle kwamaconsi e-cysteamine kulinganiswa ngokuthi ancibilikisa kahle kangakanani amakristalu futhi athuthukise izimpawu zakho ngokuhamba kwesikhathi. Abantu abaningi abane-cystinosis babona ukuthuthuka okukhulu ekunethezekeni kwamehlo abo nasekhwalithi yombono lapho besebenzisa lawa maconsi ngokuqhubekayo.
Udokotela wakho wakhetha i-cysteamine ngokuqondile ngoba iyona yokwelapha esebenza kahle kakhulu etholakalayo ngesimo sakho. Ngenkathi okunye ukwelashwa okusekelayo kungasiza ngezimpawu, i-cysteamine yiwona kuphela umuthi okhuluma ngempela ngamakristalu angaphansi.
Yebo, amathonsi eso e-cysteamine ngokuvamile aphephile ukusetshenziswa isikhathi eside uma eqashwe kahle udokotela wakho wamehlo. Abantu abaningi abane-cystinosis basebenzisa lawa mathonsi iminyaka ngaphandle kwezinkinga ezinkulu.
Udokotela wakho uzohlela ukuhlolwa kwamehlo njalo ukuze aqaphele ukuthi ukwelashwa kusebenza kahle kangakanani futhi aqaphele noma yimaphi imiphumela emibi. Bangashintsha isimiso sakho sokulinganisa noma ukugxilisa uma kudingeka ukuze kugcinwe kokubili ukusebenza kahle nokuphepha.
Ukusetshenziswa isikhathi eside kuvame ukudingeka ngoba i-cystinosis yisimo esingamahlalakhona. Amathonsi asiza ekuvikeleni ukwakheka kwamakhristali amasha ngenkathi eqhubeka nokuncibilikisa izinto ezikhona, okwenza ukwelashwa okuqhubekayo kube yingxenye ebalulekile yokuphatha impilo yakho yamehlo.
Uma ngengozi usebenzisa amathonsi amaningi kunalawo abekiwe, ungapheli amandla. Ukusebenzisa ithonsi elilodwa noma amabili engeziwe akunakwenzeka ukuthi kubangele ingozi enkulu, yize ungase uzwe ukucasuka kwamehlo okwandayo noma ukushaya.
Geza amehlo akho ngamanzi ahlanzekile uma uzwa ukungakhululeki okukhulu. Umuthi owedlulele ngokwemvelo uzosuka emehlweni akho ngokuhamba kwesikhathi.
Uma usebenzise ngaphezu kwalokho okubekiwe noma uma uzwa ubuhlungu obukhulu emehlweni, izinguquko zombono, noma izimpawu zokusabela komzimba, xhumana nodokotela wakho noma funa ukwelashwa. Kuhlale kungcono ukuxhumana nomhlinzeki wokunakekelwa kwezempilo uma ungaqiniseki ngokuphepha komuthi.
Uma uphuthelwa umthamo, uwusebenzise ngokushesha lapho ukhumbula, ngaphandle uma sekuyisikhathi somthamo wakho olandelayo ohleliwe. Kulokho, weqa umthamo ophuthelwe futhi uqhubeke nesimiso sakho esijwayelekile.
Ungasebenzisi amathonsi engeziwe ukuze ulungise umthamo ophuthelwe, ngoba lokhu kungandisa ingozi yakho yemiphumela emibi ngaphandle kokuhlinzeka ngezinzuzo ezengeziwe. Ukuqina kubalulekile, kodwa ngezikhathi ezithile ukuphuthelwa umthamo ngeke kulithinte kakhulu ukuqhubeka kokwelashwa kwakho.
Uma ukhohlwa njalo imithamo, cabangela ukusetha izikhumbuzi zocingo noma ukugcina amaconsi akho endaweni ebonakalayo lapho uzokhumbula ukuwasebenzisa. Udokotela wakho angase futhi asikisele amasu okukusiza ukuthi ugcine isimiso esiqhubekayo.
Kufanele uyeke kuphela ukusebenzisa amaconsi e-cysteamine uma udokotela wakho ekweluleka ukuthi wenze njalo. Noma ngabe izimpawu zakho zithuthuka kakhulu, ukuyeka ngaphambi kwesikhathi kungavumela ukuthi amakristalu akheke kabusha.
Udokotela wakho uzoqapha intuthuko yakho ngokuhlolwa kwamehlo njalo futhi anganciphisa kancane kancane imvamisa yakho yokulinganisa uma amakristalu akho eseqedwe ngokwanele. Abanye abantu bangagcina besebenzisa amaconsi kaningi, kanti abanye badinga ukuqhubeka nokusebenzisa njalo isikhathi eside.
Isinqumo sokuyeka noma ukunciphisa ukwelashwa sincike ekuphenduleni kwakho ngakunye, ubukhulu be-cystinosis yakho, nokuthi amakristalu akho acacile kangakanani. Udokotela wakho uzokuqondisa kunoma yiziphi izinguquko ukuze aqinisekise ukuthi impilo yamehlo akho ihlala ivikelekile.
Odokotela abaningi batusa ukugwema amalensi okuxhumana ngenkathi besebenzisa amaconsi e-cysteamine eye, ikakhulukazi ngesikhathi sokuqala sokwelashwa. Umuthi ungasebenzisana nezinto ezisetshenziswa kumalensi okuxhumana futhi ungase ubangele ukucasuka okwengeziwe.
Uma ngempela udinga ukugqoka oxhumana nabo, xoxa ngalokhu nodokotela wakho wamehlo kuqala. Bangase batusa izinhlobo ezithile zamalensi noma basikisele ukulinda isikhathi esithile ngemuva kokusebenzisa amaconsi ngaphambi kokufaka oxhumana nabo.
Abantu abaningi bathola ukuthi amehlo abo anethezekile ngaphandle kokuxhumana ngesikhathi sokwelashwa kwe-cysteamine noma kunjalo, njengoba umuthi ungaqala ukubangela ukucasuka okuthile nokuzwela. Izibuko zingase zibe yindlela engcono ngesikhathi sokwelashwa kwakho.
6Mpeople
Get clear medical guidance
on symptoms, medications, and lab reports.