Kanuma
I-Sebelipase alfa injection isebenza ekwelapheni kwabagula abanesifo se-Lysosomal acid lipase (LAL). Lolu dokotela kufanele lunikezwe yidolokoto noma ngaphansi kokunakekelwa kwalo. Lo mkhiqizo utholakala ngezindlela zokulinganisa ezilandelayo:
Ekucatshangeni kokusebenzisa imithi, izingozi zokuthatha imithi kufanele ziqhathaniswe nezinzuzo ezizoletha. Lo ngumqulu ozothatha wena nodokotela wakho. Kulo muthi, okulandelayo kufanele kucabangelwe: Tshela udokotela wakho uma uke waba nanoma iyiphi impendulo engaqondakali noma ehlasimulisayo kulo muthi noma kunoma iyiphi eminye imithi. Tshela futhi ochwepheshe bakho bezempilo uma unezinye izinhlobo zokubeletha, njengokudla, izibhebhe, izigcini, noma izilwane. Ngomkhiqizo ongenayo iresiphi, funda ilebula noma izithako zephakheji ngokucophelela. Izifundo ezifanele ezenziwe kuze kube manje azibonisi izinkinga ezikhethekile zezingane ezizobeka umkhawulo ekusebenziseni ukugxilwa kwe-sebelipase alfa kubantwana abanenyanga ubudala nangaphezulu. Izifundo ezifanele mayelana nobudlelwano bobukhulu nemiphumela yokugxilwa kwe-sebelipase alfa azikwenzelwanga kubantu abadala, azikho izinkinga ezikhethekile zabantu abadala ezibhalwe kuze kube manje. Ayikho izifundo ezifanele kubesifazane zokunquma ingozi yengane uma usebenzisa lo muthi ngesikhathi sokuncelisa. Linganisa izinzuzo ezingaba khona nezingozi ezingaba khona ngaphambi kokuthatha lo muthi ngesikhathi sokuncelisa. Nakuba imithi ethile ingafanele isetshenziswe ndawonye nhlobo, kwezinye izimo imithi emibili ehlukene ingasetshenziswa ndawonye ngisho noma kungenzeka ukuthi kube khona ukusebenzisana. Kulezi zimo, udokotela wakho angase afune ukushintsha umthamo, noma ezinye izinyathelo zokuphepha zingadingeka. Tshela ochwepheshe bakho bezempilo uma uthatha noma iyiphi enye imithi yokuqaphela noma engekho iresiphi (over-the-counter [OTC]). Imithi ethile akufanele isetshenziswe ngesikhathi noma eduze kwesikhathi sokudla ukudla noma ukudla izinhlobo ezithile zokudla njengoba kungenzeka kube khona ukusebenzisana. Ukusebenzisa utshwala noma utshako lwetabha kunye nezinye izidakamizwa kungabangela ukusebenzisana. Xoxa nochwepheshe bakho bezempilo ngokusetshenziswa kwemithi yakho ngokudla, utshwala, noma utshako lwetabha. Ukuba khona kwezinye izinkinga zezokwelapha kungathinta ukusetshenziswa kwalo muthi. Qiniseka ukuthi utshela udokotela wakho uma unezinye izinkinga zezokwelapha, ikakhulukazi:
Umshula wesibeletho noma omunye ochwepheshe bezempilo oqeqeshwe uzo kunika le miyekezo esibhedlela. Le miyekezo inikezwa nge-IV catheter ebekwe kwenye yezinsizi zakho. Imithi kufanele ihlanganiswe kancane, ngakho-ke i-IV izohlala isikhathi esingaphansi kwamahora ama-2. Ngokuvamile inikezwa kanye ngesonto noma kanye ngesonto.
Umshwana wokuzihlangula: I-August iyinkundla yolwazi lwezempilo futhi izimpendulo zayo azihlanganisi iseluleko sezokwelapha. Njalo thintana nochwepheshe bezokwelapha onelayisensi eduze nawe ngaphambi kokwenza noma yiluphi ushintsho.