Lamzede
Isicathulo se-Velmanase alfa-tycv sisetshenziswa ekwelapheni izimpawu ezingaphandle kwesistimu yezinzwa eziyinhloko (CNS) ze-alpha-mannosidosis. I-Alpha-mannosidosis yisifo esingavamile esibangelwa ukushoda kwe-enzyme ebizwa nge-alpha-mannosidase. Lolu lwemi sitholakala kuphela ngaphansi kokunakekelwa komdokotela wakho. Lo mkhiqizo utholakala ngezindlela zokulinganisela ezilandelayo:
Ekucatshangeni kokusebenzisa imithi, kubalulekile ukuqhathanisa izingozi zokusebenzisa imithi nezinzuzo ezingaba khona. Lo ngumqondo ozothatha isinqumo ngawo wena nodokotela wakho. Ngale mithi, kufanele kucabangelwe okulandelayo: Tshela udokotela wakho uma uke waba nokulimala okungavamile noma uketshezi olukhulu kule mithi noma kwezinye izidakamizwa. Tshela odokotela wakho uma unazo ezinye izinhlobo zoketshezi, njengokudla, izidakamizwa, izigcini, noma izilwane. Ngomkhiqizo ongenayo iresiphi, funda ilebula noma izithako zephakheji ngokucophelela. Izifundo ezifanele ezenziwe kuze kube manje azibonisi izinkinga ezikhethekile zezingane ezingalimi ukusetshenziswa kwe-velmanase alfa-tycv injection ezinganeni. Ukuphepha nokuphumelela kuye kwaqiniswa. I-Alpha-mannosidosis yisifo esivame ukuthinta izingane nabantu abadala abasebancane. Azikho izifundo ezifanele eziqhathanisa ubudala nemiphumela ye-velmanase alfa-tycv injection kubantu abadala. Azikho izifundo ezifanele zabesifazane zokunquma ingozi yengane uma usebenzisa le mithi ngesikhathi sokuncelisa. Linganisa izinzuzo ezingaba khona nezingozi ezingaba khona ngaphambi kokuthatha le mithi ngesikhathi sokuncelisa. Nakuba ezinye izidakamizwa kufanele zingasetshenziswa ndawonye, kwezinye izimo, izidakamizwa ezimbili ezahlukene zingasetshenziswa ndawonye ngisho noma kungenzeka ukuthi kube khona ukusebenzisana. Kulezi zimo, udokotela wakho angase afune ukushintsha umthamo, noma ezinye izinyathelo zokuphepha zingadingeka. Tshela udokotela wakho uma uthatha ezinye izidakamizwa eziresiphi noma ezingenasiphiwo (over-the-counter [OTC]). Ezinye izidakamizwa akufanele zisetshenziswe ngesikhathi sokudla noma ngesikhathi sokudla izinhlobo ezithile zokudla ngoba kungenzeka kube khona ukusebenzisana. Ukusebenzisa utshwala noma utshaba nezinye izidakamizwa kungabangela ukusebenzisana. Xoxa nodokotela wakho ngokusebenzisa imithi yakho ngokudla, utshwala, noma utshaba.
Umshula wesibeletho noma omunye ochwepheshe bezempilo oqeqeshwe uzohlinzeka ngale miyekezo esibhedlela. Le miyekezo inikezwa ngenaliti ebekwe kwenye yezinsimbi zakho. Ngokuvamile inikezwa kanye ngesonto. Udokotela wakho uzohlinzeka ngeminye imithi (isib. imithi yokwelapha ukwanda, imithi yokwelapha ubushushu, noma imithi ye-steroid) ngaphambi kokuthola le miyekezo ukuze usize ukuvimbela imiphumela engathandeki. Shaya udokotela wakho noma iqhawe lezokwelapha ukuze uthole imiyalo.
Umshwana wokuzihlangula: I-August iyinkundla yolwazi lwezempilo futhi izimpendulo zayo azihlanganisi iseluleko sezokwelapha. Njalo thintana nochwepheshe bezokwelapha onelayisensi eduze nawe ngaphambi kokwenza noma yiluphi ushintsho.